RNase P without RNA: identification and functional reconstitution of the human mitochondrial tRNA processing enzyme
about
A novel mutation in the HSD17B10 gene of a 10-year-old boy with refractory epilepsy, choreoathetosis and learning disabilityPNPASE regulates RNA import into mitochondriaLRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAsTRMT10A dysfunction is associated with abnormalities in glucose homeostasis, short stature and microcephalyPentatricopeptide repeat domain protein 3 associates with the mitochondrial small ribosomal subunit and regulates translationPentatricopeptide repeat domain protein 1 lowers the levels of mitochondrial leucine tRNAs in cellsTEFM (c17orf42) is necessary for transcription of human mtDNARNase P: at last, the key finds its lockDiscovery of a minimal form of RNase P in PyrobaculumThe ancient history of the structure of ribonuclease P and the early origins of ArchaeaMechanistic and Structural Studies of Protein-Only RNase P Compared to Ribonucleoproteins Reveal the Two Faces of the Same Enzymatic ActivityThe Diversity of Ribonuclease P: Protein and RNA Catalysts with Analogous Biological FunctionsAntibiotics and RNase PSequence Analysis and Comparative Study of the Protein Subunits of Archaeal RNase PMetabolic Enzymes Enjoying New Partnerships as RNA-Binding ProteinsStructure of transfer RNAs: similarity and variabilityThe human mitochondrial transcriptome and the RNA-binding proteins that regulate its expressionPartitional Classification: A Complement to Phylogeny.Transcriptional control of an essential ribozyme in Drosophila reveals an ancient evolutionary divide in animalsMitochondrial ribonuclease P structure provides insight into the evolution of catalytic strategies for precursor-tRNA 5' processingThermodynamic properties distinguish human mitochondrial aspartyl-tRNA synthetase from bacterial homolog with same 3D architectureCrystal structure of tRNA m1G9 methyltransferase Trm10: insight into the catalytic mechanism and recognition of tRNA substratetRNA biology in mitochondriaIdentification of LACTB2, a metallo-β-lactamase protein, as a human mitochondrial endoribonucleaseNDUFAF7 methylates arginine 85 in the NDUFS2 subunit of human complex ILocalization of human RNase Z isoforms: dual nuclear/mitochondrial targeting of the ELAC2 gene product by alternative translation initiationMitochondrial ribosomal RNA (rRNA) methyltransferase family members are positioned to modify nascent rRNA in foci near the mitochondrial DNA nucleoidRecessive Mutations in TRMT10C Cause Defects in Mitochondrial RNA Processing and Multiple Respiratory Chain Deficiencies.A subcomplex of human mitochondrial RNase P is a bifunctional methyltransferase--extensive moonlighting in mitochondrial tRNA biogenesisStructure of the nuclease subunit of human mitochondrial RNase PMyxococcus CsgA, Drosophila Sniffer, and human HSD10 are cardiolipin phospholipasesInhibition of the mitochondrial enzyme ABAD restores the amyloid-β-mediated deregulation of estradiolPlaying RNase P evolution: swapping the RNA catalyst for a protein reveals functional uniformity of highly divergent enzyme formsN4BP1 is a newly identified nucleolar protein that undergoes SUMO-regulated polyubiquitylation and proteasomal turnover at promyelocytic leukemia nuclear bodiesArchaeal/eukaryal RNase P: subunits, functions and RNA diversificationUse of chemical modification and mass spectrometry to identify substrate-contacting sites in proteinaceous RNase P, a tRNA processing enzymetRNA biology charges to the frontRNase MRP and diseaseRNase P branches out from RNP to protein: organelle-triggered diversification?Human RNase H1 is associated with protein P32 and is involved in mitochondrial pre-rRNA processing
P2860
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P2860
RNase P without RNA: identification and functional reconstitution of the human mitochondrial tRNA processing enzyme
description
2008 nî lūn-bûn
@nan
2008 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի հոտեմբերին հրատարակված գիտական հոդված
@hy
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
name
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@ast
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@en
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@en-gb
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@nl
type
label
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@ast
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@en
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@en-gb
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@nl
prefLabel
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@ast
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@en
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@en-gb
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@nl
P2093
P921
P3181
P1433
P1476
RNase P without RNA: identific ...... ondrial tRNA processing enzyme
@en
P2093
Esther Löffler
Johann Holzmann
Keiryn L Bennett
Peter Frank
P304
P3181
P356
10.1016/J.CELL.2008.09.013
P407
P577
2008-10-01T00:00:00Z