Peroxisomes are required for lipid metabolism and muscle function in Drosophila melanogaster
about
Peroxisomal biogenesis is genetically and biochemically linked to carbohydrate metabolism in Drosophila and mouse.Induced pluripotent stem cell models of Zellweger spectrum disorder show impaired peroxisome assembly and cell type-specific lipid abnormalities.Missense variants in the middle domain of DNM1L in cases of infantile encephalopathy alter peroxisomes and mitochondria when assayed in Drosophila.Peroxisomes protect lymphoma cells from HDAC inhibitor-mediated apoptosis.Unbalanced lipolysis results in lipotoxicity and mitochondrial damage in peroxisome-deficient Pex19 mutants.Dietary rescue of lipotoxicity-induced mitochondrial damage in Peroxin19 mutants.
P2860
Peroxisomes are required for lipid metabolism and muscle function in Drosophila melanogaster
description
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2014 թվականին հրատարակված գիտական հոդված
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2014年の論文
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2014年論文
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2014年論文
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2014年論文
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2014年論文
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2014年論文
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2014年论文
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name
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@ast
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@en
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@nl
type
label
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@ast
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@en
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@nl
prefLabel
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@ast
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@en
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@nl
P2093
P2860
P50
P1433
P1476
Peroxisomes are required for l ...... ion in Drosophila melanogaster
@en
P2093
Arvind Manisundaram
H Alex Brown
James B Summerville
Michael Stern
Pavlina T Ivanova
Stephen B Milne
P2860
P304
P356
10.1371/JOURNAL.PONE.0100213
P407
P577
2014-01-01T00:00:00Z