Identification of specific subunits of highly purified bovine liver branched-chain ketoacid dehydrogenase

Identification of specific subunits of highly purified bovine liver branched-chain ketoacid dehydrogenase

Item
http://www.wikidata.org/entity/Q28271535
Maple syrup urine disease. Complete primary structure of the E1 beta subunit of human branched chain alpha-ketoacid dehydrogenase complex deduced from the nucleotide sequence and a gene analysis of patients with this diseasePremature termination of transcription and alternative splicing in the human transacylase (E2) gene of the branched-chain alpha-ketoacid dehydrogenase complexThe 2-oxo acid dehydrogenase complexes: recent advancesAltered kinetic properties of the branched-chain alpha-keto acid dehydrogenase complex due to mutation of the beta-subunit of the branched-chain alpha-keto acid decarboxylase (E1) component in lymphoblastoid cells derived from patients with maple sycDNA cloning of the chicken branched-chain alpha-keto acid dehydrogenase complex. Chicken-specific residues of the acyltransferase affect the overall activity and the interaction with the dehydrogenase.Rare etiology of autosomal recessive disease in a child with noncarrier parents.Mechanism for basal expression of rat mitochondrial branched-chain-2-oxo-acid dehydrogenase kinase [corrected].Molecular genetic basis for inherited human disorders of branched-chain alpha-keto acid dehydrogenase complex.Direct physical evidence for stabilization of branched-chain alpha-ketoacid dehydrogenase by thiamin pyrophosphate.Absence of branched chain acyl-transferase as a cause of maple syrup urine disease.Structural organization of the rat branched-chain 2-oxo-acid dehydrogenase kinase gene and partial characterization of the promoter-regulatory region.Resolution of branched-chain oxo acid dehydrogenase complex of Pseudomonas aeruginosa PAO.Effects of diet and of alloxan-diabetes on the activity of branched-chain 2-oxo acid dehydrogenase complex and of activator protein in rat tissues.Alteration in gene expression of branched-chain keto acid dehydrogenase kinase but not in gene expression of its substrate in the liver of clofibrate-treated ratsStable correction of maple syrup urine disease in cells from a Mennonite patient by retroviral-mediated gene transfer.Down-regulation of rat mitochondrial branched-chain 2-oxoacid dehydrogenase kinase gene expression by glucocorticoids.
P2860

Identification of specific subunits of highly purified bovine liver branched-chain ketoacid dehydrogenase

Item
http://www.wikidata.org/entity/Q28271535
description
1983 nî lūn-bûn
@nan
1983 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
1983 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
1983年の論文
@ja
1983年論文
@yue
1983年論文
@zh-hant
1983年論文
@zh-hk
1983年論文
@zh-mo
1983年論文
@zh-tw
1983年论文
@wuu
name
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@ast
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@en
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@nl
type
label
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@ast
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@en
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@nl
prefLabel
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@ast
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@en
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@nl
P1433
P1476
P2093
P304
P31
P356
P407
P433
P478
P577
P698
P356
P1433
P1476
Identification of specific sub ...... d-chain ketoacid dehydrogenase
@en
P2093
P304
P31
P356
P407
P433
P478
P577
P698