Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene.
about
Skeletal muscle laminin and MDC1A: pathogenesis and treatment strategies.Characterization and expression of the laminin gamma3 chain: a novel, non-basement membrane-associated, laminin chainForm and function: the laminin family of heterotrimersDefective expression of plectin/HD1 in epidermolysis bullosa simplex with muscular dystrophyMuscle regeneration and myogenic differentiation defects in mice lacking TIS7Laminin expression in adult and developing retinae: evidence of two novel CNS lamininsThe laminin alpha chains: expression, developmental transitions, and chromosomal locations of alpha1-5, identification of heterotrimeric laminins 8-11, and cloning of a novel alpha3 isoformLaminin regulates PDGFRβ(+) cell stemness and muscle development.A splice site mutation in laminin-α2 results in a severe muscular dystrophy and growth abnormalities in zebrafishBortezomib Does Not Reduce Muscular Dystrophy in the dy2J/dy2J Mouse Model of Laminin α2 Chain-Deficient Muscular DystrophyDeterminants of laminin polymerization revealed by the structure of the α5 chain amino-terminal regionCrystal Structures of the Network-Forming Short-Arm Tips of the Laminin β1 and γ1 ChainsA role of dystroglycan in schwannoma cell adhesion to lamininMild congenital muscular dystrophy in two patients with an internally deleted laminin alpha2-chainIntegrins (alpha7beta1) in muscle function and survival. Disrupted expression in merosin-deficient congenital muscular dystrophyThe adhesion GPCR GPR126 has distinct, domain-dependent functions in Schwann cell development mediated by interaction with laminin-211Structure of the human laminin alpha2-chain gene (LAMA2), which is affected in congenital muscular dystrophyPrimary structure and expression of a novel human laminin alpha 4 chainPrimary structure, developmental expression, and immunolocalization of the murine laminin alpha4 chainThe renal glomerulus of mice lacking s-laminin/laminin beta 2: nephrosis despite molecular compensation by laminin beta 1Glycosylation defects: a new mechanism for muscular dystrophy?Deletion of the laminin alpha4 chain leads to impaired microvessel maturationDef-6, a guanine nucleotide exchange factor for Rac1, interacts with the skeletal muscle integrin chain alpha7A and influences myoblast differentiationHigh RhoA activity maintains the undifferentiated mesenchymal cell phenotype, whereas RhoA down-regulation by laminin-2 induces smooth muscle myogenesisDistribution and function of laminins in the neuromuscular system of developing, adult, and mutant miceJab1 regulates Schwann cell proliferation and axonal sorting through p27.Potent pro-inflammatory and pro-fibrotic molecules, osteopontin and galectin-3, are not major disease modulators of laminin α2 chain-deficient muscular dystrophy.Molecular analysis of laminin N-terminal domains mediating self-interactions.Adaptive evolution during an ongoing range expansion: the invasive bank vole (Myodes glareolus) in Ireland.Laminins: structure and genetic regulation.Laminins of the neuromuscular system.Laminins and human disease.A laminin-2, dystroglycan, utrophin axis is required for compartmentalization and elongation of myelin segmentsEx vivo stretch reveals altered mechanical properties of isolated dystrophin-deficient hearts.Differential heparin inhibition of skeletal muscle alpha-dystroglycan binding to laminins.Distinct genetic regions modify specific muscle groups in muscular dystrophy.The Ras antagonist, farnesylthiosalicylic acid (FTS), decreases fibrosis and improves muscle strength in dy/dy mouse model of muscular dystrophy.Adenovirus mediated gene transfer to skeletal muscle.Omigapil treatment decreases fibrosis and improves respiratory rate in dy(2J) mouse model of congenital muscular dystrophySchwann cell-specific ablation of laminin gamma1 causes apoptosis and prevents proliferation.
P2860
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P2860
Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene.
description
1994 nî lūn-bûn
@nan
1994 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
1994 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
1994年の論文
@ja
1994年論文
@yue
1994年論文
@zh-hant
1994年論文
@zh-hk
1994年論文
@zh-mo
1994年論文
@zh-tw
1994年论文
@wuu
name
Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene.
@ast
Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene.
@en
Murine muscular dystrophy caused by a mutation in the laminin alpha 2
@nl
type
label
Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene.
@ast
Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene.
@en
Murine muscular dystrophy caused by a mutation in the laminin alpha 2
@nl
prefLabel
Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene.
@ast
Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene.
@en
Murine muscular dystrophy caused by a mutation in the laminin alpha 2
@nl
P2093
P356
P1433
P1476
Murine muscular dystrophy caused by a mutation in the laminin alpha 2 (Lama2) gene.
@en
P2093
P2888
P304
P356
10.1038/NG1194-297
P407
P577
1994-11-01T00:00:00Z