Intraflagellar transport and cilia-dependent renal disease: the ciliary hypothesis of polycystic kidney disease.
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NEK8 mutations affect ciliary and centrosomal localization and may cause nephronophthisisThe Role of G-Protein-Coupled Receptor Proteolysis Site Cleavage of Polycystin-1 in Renal Physiology and Polycystic Kidney DiseaseThe role of the cilium in normal and abnormal cell cycles: emphasis on renal cystic pathologiesAn essential role for DYF-11/MIP-T3 in assembling functional intraflagellar transport complexesEffects of TORC1 Inhibition during the Early and Established Phases of Polycystic Kidney DiseaseCharacterization of the intraflagellar transport complex B core: direct interaction of the IFT81 and IFT74/72 subunits.A conserved signal and GTPase complex are required for the ciliary transport of polycystin-1.Type 3 adenylyl cyclase: a key enzyme mediating the cAMP signaling in neuronal ciliaVHL inactivation induces HEF1 and Aurora kinase ADisruption of aquaporin-11 produces polycystic kidneys following vacuolization of the proximal tubuleEssential and synergistic roles of RP1 and RP1L1 in rod photoreceptor axoneme and retinitis pigmentosaArf4 is required for Mammalian development but dispensable for ciliary assemblyADP-ribosylation factor-like 3 is involved in kidney and photoreceptor developmentDisruption of IFT complex A causes cystic kidneys without mitotic spindle misorientationDeletion of IFT20 in the mouse kidney causes misorientation of the mitotic spindle and cystic kidney diseaseProteomic analysis of a eukaryotic ciliumThe primary cilium as a complex signaling centerThe WD repeat-containing protein IFTA-1 is required for retrograde intraflagellar transport.Primary cilia mediate mechanosensing in bone cells by a calcium-independent mechanism.The zebrafish fleer gene encodes an essential regulator of cilia tubulin polyglutamylation.The Nek8 protein kinase, mutated in the human cystic kidney disease nephronophthisis, is both activated and degraded during ciliogenesis.Phylogenetic analysis of the Neks reveals early diversification of ciliary-cell cycle kinases.The NIMA-family kinase, Nek1 affects the stability of centrosomes and ciliogenesis.Polycystic kidney disease in the medaka (Oryzias latipes) pc mutant caused by a mutation in the Gli-Similar3 (glis3) gene.Design and Implementation of the Hepatorenal Fibrocystic Disease Core Center Clinical Database: A Centralized Resource for Characterizing Autosomal Recessive Polycystic Kidney Disease and Other Hepatorenal Fibrocystic DiseasesNovel targets for the treatment of autosomal dominant polycystic kidney disease.Loss of primary cilia occurs early in breast cancer development.Primary cilia regulate branching morphogenesis during mammary gland development.Autosomal recessive polycystic kidney disease: a hepatorenal fibrocystic disorder with pleiotropic effectsTransgenic overexpression of Anks6(p.R823W) causes polycystic kidney disease in rats.Hypertension in Autosomal Dominant Polycystic Kidney Disease: A Clinical and Basic Science PerspectiveCiliary membrane proteins traffic through the Golgi via a Rabep1/GGA1/Arl3-dependent mechanismmTOR is out of control in polycystic kidney disease.Effect of statin therapy on disease progression in pediatric ADPKD: design and baseline characteristics of participantsIFT46 plays an essential role in cilia developmentChronic fluid flow is an environmental modifier of renal epithelial function.Mechanical properties of a primary cilium as measured by resonant oscillation.How insights from cardiovascular developmental biology have impacted the care of infants and children with congenital heart disease.Cystic kidney diseases: many ways to form a cyst.Human embryonic stem cells in culture possess primary cilia with hedgehog signaling machinery.
P2860
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P2860
Intraflagellar transport and cilia-dependent renal disease: the ciliary hypothesis of polycystic kidney disease.
description
2004 nî lūn-bûn
@nan
2004 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2004 թվականի հոտեմբերին հրատարակված գիտական հոդված
@hy
2004年の論文
@ja
2004年論文
@yue
2004年論文
@zh-hant
2004年論文
@zh-hk
2004年論文
@zh-mo
2004年論文
@zh-tw
2004年论文
@wuu
name
Intraflagellar transport and c ...... of polycystic kidney disease.
@ast
Intraflagellar transport and c ...... of polycystic kidney disease.
@en
Intraflagellar transport and c ...... of polycystic kidney disease.
@nl
type
label
Intraflagellar transport and c ...... of polycystic kidney disease.
@ast
Intraflagellar transport and c ...... of polycystic kidney disease.
@en
Intraflagellar transport and c ...... of polycystic kidney disease.
@nl
prefLabel
Intraflagellar transport and c ...... of polycystic kidney disease.
@ast
Intraflagellar transport and c ...... of polycystic kidney disease.
@en
Intraflagellar transport and c ...... of polycystic kidney disease.
@nl
P1476
Intraflagellar transport and c ...... s of polycystic kidney disease
@en
P2093
Gregory J Pazour
P304
P356
10.1097/01.ASN.0000141055.57643.E0
P577
2004-10-01T00:00:00Z