Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.
about
Skeletal muscle laminin and MDC1A: pathogenesis and treatment strategies.Form and function: the laminin family of heterotrimersIncreasing complexity of the dystrophin-associated protein complexDistinct roles for laminin globular domains in laminin alpha1 chain mediated rescue of murine laminin alpha2 chain deficiencyA role of dystroglycan in schwannoma cell adhesion to lamininDystroglycan is a binding protein of laminin and merosin in peripheral nerveMild congenital muscular dystrophy in two patients with an internally deleted laminin alpha2-chainIntegrins (alpha7beta1) in muscle function and survival. Disrupted expression in merosin-deficient congenital muscular dystrophyThe absence of nidogen 1 does not affect murine basement membrane formationHigh RhoA activity maintains the undifferentiated mesenchymal cell phenotype, whereas RhoA down-regulation by laminin-2 induces smooth muscle myogenesisDistribution and function of laminins in the neuromuscular system of developing, adult, and mutant miceThe super super-healing MRL mouse strainRegulation of radial glial survival by signals from the meninges.Amelioration of laminin-alpha2-deficient congenital muscular dystrophy by somatic gene transfer of miniagrin.Laminins of the neuromuscular system.Laminins and human disease.Differential heparin inhibition of skeletal muscle alpha-dystroglycan binding to laminins.Adenovirus mediated gene transfer to skeletal muscle.Elimination of myostatin does not combat muscular dystrophy in dy mice but increases postnatal lethality.The muscular dystrophies: from genes to therapies.Overexpression of the cytotoxic T cell (CT) carbohydrate inhibits muscular dystrophy in the dyW mouse model of congenital muscular dystrophy 1A.Comparative proteomic profiling of dystroglycan-associated proteins in wild type, mdx, and Galgt2 transgenic mouse skeletal muscle.Distribution of alpha-dystroglycan during embryonic nerve-muscle synaptogenesis.Non-muscle alpha-dystroglycan is involved in epithelial development.Partial laminin alpha2 chain restoration in alpha2 chain-deficient dy/dy mouse by primary muscle cell culture transplantationMerosin and laminin in myogenesis; specific requirement for merosin in myotube stability and survival.Differential expression of mRNAs encoding laminin chain variants during in vitro development of mouse blastocystsalpha-Dystroglycan is a laminin receptor involved in extracellular matrix assembly on myotubes and muscle cell viability.Targeted disruption of the LAMA3 gene in mice reveals abnormalities in survival and late stage differentiation of epithelial cells.Animal models for muscular dystrophy show different patterns of sarcolemmal disruption.Membrane targeting and stabilization of sarcospan is mediated by the sarcoglycan subcomplex.Gamma-sarcoglycan deficiency leads to muscle membrane defects and apoptosis independent of dystrophin.A recombinant tail-less integrin beta 4 subunit disrupts hemidesmosomes, but does not suppress alpha 6 beta 4-mediated cell adhesion to laminins.Laminin-211 in skeletal muscle function.Animal models of muscular dystrophyMuscular dystrophy associated with alpha-dystroglycan deficiency in Sphynx and Devon Rex cats.Overexpression of Galgt2 reduces dystrophic pathology in the skeletal muscles of alpha sarcoglycan-deficient miceMerosin-deficient congenital muscular dystrophy. Partial genetic correction in two mouse modelsSkeletal muscle as a paradigm for regenerative biology and medicine.Congenital muscular dystrophy. Part II: a review of pathogenesis and therapeutic perspectives.
P2860
Q22001192-9155A619-2709-47CF-8320-38D0F5E7BD6FQ22254277-8B8C4EEE-F5A6-4DFC-B146-E5453703AAB9Q24564140-E8BDEE53-B043-4A15-9AD9-8E1FAAD9B4D9Q27323309-CDA9C9D9-93F2-43DE-BACC-A27960E1DB95Q28238357-55BDFA62-F3EA-4E54-BA8B-0A001D298F2AQ28238540-F3CB4D82-14B9-4B2E-B235-3C0FBD90A3A9Q28238601-F1E0A680-575F-43BB-B0C5-F5C85FCEC122Q28249995-0CC0FAE7-E1F0-4907-84D1-B64AAF98831CQ28588236-083142F7-9E87-424C-98D3-89907DA93812Q28592451-5813D136-237B-4DC5-970F-E439400D66A1Q28593330-7448CD58-AC58-4680-8D6D-EE67339801E8Q29542636-3B58765D-2B5F-4DB5-9090-50CE06E8E09AQ30490012-4B3F073B-E9C8-45B6-B3ED-31857214A890Q33922811-2C945B6F-2BE5-41E4-BA56-3F59E0823992Q34071971-1371357F-00CC-4E37-9BCB-F6FB4D2F98D7Q34071975-120F77C8-C75A-4B68-98DB-30E212CD47E5Q34379897-629A5149-2111-4860-86D7-4B7C0C45B0CEQ34733229-3568C2F4-24D3-479B-B896-DFEED027BF27Q35083601-4B58E39C-02D6-448E-BDC2-E0476107EF8BQ35834674-B07DB6AC-38A4-4E57-A053-3000FC988E1EQ35928246-9CF7D3DB-6F32-4807-91B5-1511F1E42D91Q36218358-F47DC901-6E79-4B44-B8BD-D53EE38E5962Q36235647-544F3687-5968-465E-90C6-227D0A4D0FF1Q36235753-6A4C2021-6754-473A-9465-C941127F518EQ36236670-691D7D00-E703-45CD-8CD6-EB4EF523D77EQ36237447-E14EE762-D205-49AF-A711-C01970600223Q36255161-08242DB2-07DA-4580-BE57-775139C3BD87Q36256527-53DAFCB0-F44C-4758-ACC0-E00FCCDA5F3FQ36256553-A9D732D8-0FC5-4527-AE77-74082C4A2C8EQ36273863-C1CF68F9-7512-4AC6-B135-649D24F55151Q36288396-E13E8E34-DA25-4AE6-ABB5-94A11CBA89CBQ36290630-1756004D-8A26-4F69-A1C1-A372F6DE81BEQ36382518-31C377CF-B5DF-4616-A90E-380E2D8CDD72Q36531788-CD992CDF-A33A-447A-92B9-BC98F736FF78Q36915922-F179D7F0-3E27-479C-B38C-E331A82BA589Q37105883-6B0E9C95-5875-4282-BA39-217377E233E4Q37257159-77519CB7-5D17-4264-BCD2-B859204F183CQ37384623-F4976356-D220-4192-964D-5326AF7CA2A8Q37422514-0EBCA579-9E88-48BD-8676-6C1ED4201CBBQ37528083-729D1167-C712-41E7-873B-9F4921D14B77
P2860
Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.
description
1994 nî lūn-bûn
@nan
1994 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
1994 թվականի հունիսին հրատարակված գիտական հոդված
@hy
1994年の論文
@ja
1994年論文
@yue
1994年論文
@zh-hant
1994年論文
@zh-hk
1994年論文
@zh-mo
1994年論文
@zh-tw
1994年论文
@wuu
name
Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.
@ast
Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.
@en
type
label
Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.
@ast
Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.
@en
prefLabel
Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.
@ast
Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.
@en
P2093
P2860
P356
P1476
Defective muscle basement membrane and lack of M-laminin in the dystrophic dy/dy mouse.
@en
P2093
P2860
P304
P356
10.1073/PNAS.91.12.5572
P407
P577
1994-06-01T00:00:00Z