Urinary 2-hydroxy-5-oxoproline, the lactam form of α-ketoglutaramate, is markedly increased in urea cycle disorders.
about
Structural insights into the catalytic active site and activity of human Nit2/ω-amidase: kinetic assay and molecular dynamics simulationα-Ketoglutaramate: an overlooked metabolite of glutamine and a biomarker for hepatic encephalopathy and inborn errors of the urea cycleInvolvement of aspartoacylase in tremor expression in rats.Starvation ketoacidosis: a cause of severe anion gap metabolic acidosis in pregnancy.Comparative enzymology of (2S,4R)4-fluoroglutamine and (2S,4R)4-fluoroglutamate.Enzymatic analysis of α-ketoglutaramate--a biomarker for hyperammonemia.Urinary proteomics and metabolomics in the diagnosis of pediatric disorders.ω-Amidase: an underappreciated, but important enzyme in L-glutamine and L-asparagine metabolism; relevance to sulfur and nitrogen metabolism, tumor biology and hyperammonemic diseases.On the role of the mitochondrial 2-oxoglutarate dehydrogenase complex in amino acid metabolism.
P2860
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P2860
Urinary 2-hydroxy-5-oxoproline, the lactam form of α-ketoglutaramate, is markedly increased in urea cycle disorders.
description
2011 nî lūn-bûn
@nan
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
2011年论文
@zh
2011年论文
@zh-cn
name
Urinary 2-hydroxy-5-oxoproline ...... eased in urea cycle disorders.
@ast
Urinary 2-hydroxy-5-oxoproline ...... eased in urea cycle disorders.
@en
type
label
Urinary 2-hydroxy-5-oxoproline ...... eased in urea cycle disorders.
@ast
Urinary 2-hydroxy-5-oxoproline ...... eased in urea cycle disorders.
@en
prefLabel
Urinary 2-hydroxy-5-oxoproline ...... eased in urea cycle disorders.
@ast
Urinary 2-hydroxy-5-oxoproline ...... eased in urea cycle disorders.
@en
P2093
P2860
P1476
Urinary 2-hydroxy-5-oxoproline ...... reased in urea cycle disorders
@en
P2093
Arthur J L Cooper
Morimasa Ohse
Tomiko Kuhara
Yoshito Inoue
P2860
P2888
P304
P356
10.1007/S00216-011-4688-X
P407
P577
2011-02-06T00:00:00Z