Corticospinal Motor Neurons Are Susceptible to Increased ER Stress and Display Profound Degeneration in the Absence of UCHL1 Function
about
Ubiquitin C-terminal hydrolase L1 (UCH-L1): structure, distribution and roles in brain function and dysfunctionAdeno-associated virus-delivered artificial microRNA extends survival and delays paralysis in an amyotrophic lateral sclerosis mouse model.Recent Insights into the Role of Unfolded Protein Response in ER Stress in Health and Disease.Proposed association between the hexanucleotide repeat of C9orf72 and opposability index of the thumb.In vivo transduction of neurons with TAT-UCH-L1 protects brain against controlled cortical impact injury.The essential and downstream common proteins of amyotrophic lateral sclerosis: A protein-protein interaction network analysis.The point mutation UCH-L1 C152A protects primary neurons against cyclopentenone prostaglandin-induced cytotoxicity: implications for post-ischemic neuronal injury.Spinal Muscular Atrophy Patient iPSC-Derived Motor Neurons Have Reduced Expression of Proteins Important in Neuronal Development.Absence of alsin function leads to corticospinal motor neuron vulnerability via novel disease mechanismsAbsence of UCHL 1 function leads to selective motor neuropathy.Marked changes in dendritic structure and spine density precede significant neuronal death in vulnerable cortical pyramidal neuron populations in the SOD1(G93A) mouse model of amyotrophic lateral sclerosisER stress and the unfolded protein response in neurodegeneration.Life and death in the trash heap: The ubiquitin proteasome pathway and UCHL1 in brain aging, neurodegenerative disease and cerebral Ischemia.Apical dendrite degeneration, a novel cellular pathology for Betz cells in ALSMutant Profilin1 transgenic mice recapitulate cardinal features of motor neuron disease.Protein-protein interactions reveal key canonical pathways, upstream regulators, interactome domains, and novel targets in ALS
P2860
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P2860
Corticospinal Motor Neurons Are Susceptible to Increased ER Stress and Display Profound Degeneration in the Absence of UCHL1 Function
description
2015 nî lūn-bûn
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2015 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2015 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2015年の論文
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2015年論文
@yue
2015年論文
@zh-hant
2015年論文
@zh-hk
2015年論文
@zh-mo
2015年論文
@zh-tw
2015年论文
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name
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@ast
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@en
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@nl
type
label
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@ast
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@en
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@nl
prefLabel
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@ast
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@en
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@nl
P2093
P2860
P3181
P356
P1433
P1476
Corticospinal Motor Neurons Ar ...... the Absence of UCHL1 Function
@en
P2093
Barış Genç
Emel Ulupınar
Gregory A Cox
Jeffrey D Macklis
Martha C Bohn
P Hande Özdinler
Raymond P Roos
P2860
P304
P3181
P356
10.1093/CERCOR/BHU318
P407
P577
2015-01-16T00:00:00Z