Resetting translational homeostasis restores myelination in Charcot-Marie-Tooth disease type 1B mice - sprookjes - yvandenbroek - TriplyDB

Resetting translational homeostasis restores myelination in Charcot-Marie-Tooth disease type 1B mice

Resetting translational homeostasis restores myelination in Charcot-Marie-Tooth disease type 1B mice

http://www.wikidata.org/entity/Q36750041

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LGI proteins in the nervous system.Functional Role of the Disulfide Isomerase ERp57 in Axonal Regeneration Muscle-specific Drp1 overexpression impairs skeletal muscle growth via translational attenuation.Inhibition of GADD34, the stress-inducible regulatory subunit of the endoplasmic reticulum stress response, does not enhance functional recovery after spinal cord injury SB225002 Induces Cell Death and Cell Cycle Arrest in Acute Lymphoblastic Leukemia Cells through the Activation of GLIPR1 Impaired eukaryotic translation initiation factor 2B activity specifically in oligodendrocytes reproduces the pathology of vanishing white matter disease in mice.Preventing proteostasis diseases by selective inhibition of a phosphatase regulatory subunit Loss of Fig4 in both Schwann cells and motor neurons contributes to CMT4J neuropathy.PERK inhibition prevents tau-mediated neurodegeneration in a mouse model of frontotemporal dementia.Genotype-phenotype characteristics and baseline natural history of heritable neuropathies caused by mutations in the MPZ gene.Altered Trafficking and Processing of GALC Mutants Correlates with Globoid Cell Leukodystrophy Severity Activation of the unfolded protein response promotes axonal regeneration after peripheral nerve injury Perk Ablation Ameliorates Myelination in S63del-Charcot-Marie-Tooth 1B Neuropathy.Overexpression of CHOP in Myelinating Cells Does Not Confer a Significant Phenotype under Normal or Metabolic Stress Conditions.Ablation of Perk in Schwann Cells Improves Myelination in the S63del Charcot-Marie-Tooth 1B Mouse.ER stress inhibitor attenuates hearing loss and hair cell death in Cdh23erl/erl mutant mice.Disturbance of endoplasmic reticulum proteostasis in neurodegenerative diseases.Therapeutic options in Charcot-Marie-Tooth diseases.Schwann cell myelination ER stress and the unfolded protein response in neurodegeneration.TFG-Related Neurologic Disorders: New Insights Into Relationships Between Endoplasmic Reticulum and Neurodegeneration.Endoplasmic reticulum stress and the unfolded protein response in disorders of myelinating glia The unfolded protein response: mechanisms and therapy of neurodegeneration.The integrated stress response.Chaperones as potential therapeutics for Krabbe disease.Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.Fine-tuning PERK signaling for neuroprotection.c-Jun activation in Schwann cells protects against loss of sensory axons in inherited neuropathy.PPP1R15A-mediated dephosphorylation of eIF2α is unaffected by Sephin1 or Guanabenz.Unraveling gene expression profiles in peripheral motor nerve from amyotrophic lateral sclerosis patients: insights into pathogenesis.Rab32 connects ER stress to mitochondrial defects in multiple sclerosis.Sox2 expression in Schwann cells inhibits myelination in vivo and induces influx of macrophages to the nerve.qMotor, a set of rules for sensitive, robust and quantitative measurement of motor performance in mice.Transcription Factor C/EBP Homologous Protein in Health and Diseases.Impairment of protein degradation and proteasome function in hereditary neuropathies.Decoding the selectivity of eIF2α holophosphatases and PPP1R15A inhibitors.Pathogenic inflammation in the CNS of mice carrying human PLP1 mutations.The integrated stress response in hypoxia-induced diffuse white matter injury.Myelin protein zero mutations and the unfolded protein response in Charcot Marie Tooth disease type 1B.A Sephin1-insensitive tripartite holophosphatase dephosphorylates translation initiation factor 2α.

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Resetting translational homeostasis restores myelination in Charcot-Marie-Tooth disease type 1B mice

http://www.wikidata.org/entity/Q36750041

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Resetting translational homeos ...... rie-Tooth disease type 1B mice

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Daniela Ungaro

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Lawrence Wrabetz

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M Laura Feltri

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Maurizio D'Antonio

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Ubaldo Del Carro

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P2860

Caspase-12 mediates endoplasmic-reticulum-specific apoptosis and cytotoxicity by amyloid-beta

TRB3, a novel ER stress-inducible gene, is induced via ATF4-CHOP pathway and is involved in cell death

Derlin-2 and Derlin-3 are regulated by the mammalian unfolded protein response and are required for ER-associated degradation

Deletion of the serine 34 codon from the major peripheral myelin protein P0 gene in Charcot-Marie-Tooth disease type 1B

Sustained translational repression by eIF2α-P mediates prion neurodegeneration

L2L: a simple tool for discovering the hidden significance in microarray expression data

Signal integration in the endoplasmic reticulum unfolded protein response

Identification of genes induced in peripheral nerve after injury. Expression profiling and novel gene discovery

Translational control is required for the unfolded protein response and in vivo glucose homeostasis

A selective inhibitor of eIF2alpha dephosphorylation protects cells from ER stress

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