Arrhythmogenic cardiomyopathy
Arrhythmogenic cardiomyopathy (ACM), arrhythmogenic right ventricular dysplasia (ARVD), or arrhythmogenic right ventricular cardiomyopathy (ARVC), is an inherited heart disease. ACM is caused by genetic defects of the parts of heart muscle (also called myocardium or cardiac muscle) known as desmosomes, areas on the surface of heart muscle cells which link the cells together. The desmosomes are composed of several proteins, and many of those proteins can have harmful mutations.
differential diagnosis
disease
ARVCARVDARVD/CArrhythmogenic Right Ventricular CardiomyopathyArrhythmogenic right ventricular cardiomyopathyArrhythmogenic right ventricular dysplasiaArrhythmogenic right ventricular dysplasia/cardiomyopathyArrythmogenic right ventricular dysplasiaArrythmogenic right ventricular dysplasia, familialDiffuse non-epidermolytic PPK with woolly hair and cardiomyopathyEpsilon waveEpsilon wavesFamilial arrhythmogenic right ventricular dysplasiaFamilial arrythmogenic right ventricular dysplasia
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ACRVARVCARVDARVD/CAntonio PuertaArrhythmiaArrhythmogenic Right Ventricular CardiomyopathyArrhythmogenic right ventricular cardiomyopathyArrhythmogenic right ventricular dysplasiaArrhythmogenic right ventricular dysplasia/cardiomyopathyArrythmogenic right ventricular dysplasiaArrythmogenic right ventricular dysplasia, familialAssociation football cultureAssociation for Inherited Cardiac Conditions1,2-dimethoxyethaanBongani MayosiBoxer cardiomyopathyBrugada syndromeCardiac Risk in the YoungCardiac arrestCardiac muscleCardiomyopathyChromosome 3DSC2Deaths in April 2015Deaths in September 2006DesmocollinDesmoglein-2DesmoplakinDesmosomeDiffuse non-epidermolytic PPK with woolly hair and cardiomyopathyEpsilon waveEpsilon wavesFamilial arrhythmogenic right ventricular dysplasiaFamilial arrythmogenic right ventricular dysplasiaFlecainideForamen secundumFrank I. MarcusGap junction modulationHeart
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differential
diseases
types
primaryTopic
Arrhythmogenic cardiomyopathy
Arrhythmogenic cardiomyopathy (ACM), arrhythmogenic right ventricular dysplasia (ARVD), or arrhythmogenic right ventricular cardiomyopathy (ARVC), is an inherited heart disease. ACM is caused by genetic defects of the parts of heart muscle (also called myocardium or cardiac muscle) known as desmosomes, areas on the surface of heart muscle cells which link the cells together. The desmosomes are composed of several proteins, and many of those proteins can have harmful mutations.
has abstract
Arrhythmogenic cardiomyopathy ...... have a familial distribution.
@en
Arytmogenna kardiomiopatia pra ...... dla życia arytmii komorowych.
@pl
La displasia arritmogénica es ...... eta sana y buena forma física.
@es
La displasia ventricolare dest ...... ssuto fibroso o fibro-adiposo.
@it
La dysplasie ventriculaire dro ...... ables d'un individu à l'autre.
@fr
Η αρρυθμιογόνος καρδιομυοπάθει ...... πτώματα στην ηλικία των 40-50.
@el
Аритмоге́нная кардиомиопати́я ...... поражением правого желудочка.
@ru
خلل تنسج البطين الأيمن المحدث ...... عائلي في 30 إلى 50% من حالاته.
@ar
DiseasesDB
MeSH ID
OMIM id
Link from a Wikipage to an external page
Wikipage page ID
page length (characters) of wiki page
Wikipage revision ID
1,023,575,301
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caption
Photomicrograph of an ACM heart.
@en
DiseasesDB
ICD
@en
I42.8
@en
MeshID
D019571
@en
name
Arrhythmogenic cardiomyopathy
@en
OMIM
synonyms
arrhythmogenic right ventricul ...... , right ventricular dysplasia
@en
wikiPageUsesTemplate
subject
comment
Arrhythmogenic cardiomyopathy ...... ns can have harmful mutations.
@en
Arytmogenna kardiomiopatia pra ...... dla życia arytmii komorowych.
@pl
La displasia arritmogénica es ...... afecta al ventrículo derecho.
@es
La displasia ventricolare dest ...... ssuto fibroso o fibro-adiposo.
@it
La dysplasie ventriculaire dro ...... ables d'un individu à l'autre.
@fr
Η αρρυθμιογόνος καρδιομυοπάθει ...... πτώματα στην ηλικία των 40-50.
@el
Аритмоге́нная кардиомиопати́я ...... поражением правого желудочка.
@ru
خلل تنسج البطين الأيمن المحدث ...... بروتينات أن يصاب بطفرات مؤذية.
@ar
label
Arrhythmogene rechtsventrikuläre Kardiomyopathie
@de
Arrhythmogenic cardiomyopathy
@en
Arytmogenna kardiomiopatia prawej komory
@pl
Displasia arritmogénica
@es
Displasia ventricolare destra aritmogena
@it
Dysplasie ventriculaire droite arythmogène
@fr
Αρρυθμιογόνος καρδιομυοπάθεια
@el
Аритмогенная дисплазия правого желудочка
@ru
خلل تنسج البطين الأيمن المحدث لاضطراب النظم
@ar
sameAs
wasDerivedFrom
isPrimaryTopicOf
name
Arrhythmogenic cardiomyopathy
@en