HADHA
Trifunctional enzyme subunit alpha, mitochondrial also known as hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit is a protein that in humans is encoded by the HADHA gene. Mutations in HADHA have been associated with trifunctional protein deficiency or long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency.
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C2orf81Chromosome 2Crotonase familyECHA (disambiguation)FASTKD3GBP (disambiguation)HADHA (gene)HADHBHousekeeping geneHydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunitHydroxyacyl-Coenzyme A dehydrogenaseLCEHLCHADList of OMIM disorder codesList of human protein-coding genes 2Long-chain-(S)-3-hydroxyacyl-CoA:NAD+ oxidoreductaseLong-chain 3-hydroxy acyl-coenzyme A dehydrogenaseLong-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiencyMTPAMitochondrial trifunctional proteinMitochondrial trifunctional protein deficiencyMonolysocardiolipin acyltransferaseTP-ALPHATrifunctional enzyme subunit alpha, mitochondrial
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HADHA
Trifunctional enzyme subunit alpha, mitochondrial also known as hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit is a protein that in humans is encoded by the HADHA gene. Mutations in HADHA have been associated with trifunctional protein deficiency or long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency.
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HADHA (англ. Hydroxyacyl-CoA d ...... . Локалізований у мітохондрії.
@uk
HADHA (Hydroxyacyl-CoA dehydr ...... ر بواسطة جين HADHA في الإنسان.
@ar
La 3-idrossiacil-CoA (a lunga ...... nno una catena lunga 8 o 10 C.
@it
Niedobór dehydrogenazy 3-hydro ...... cą diety i unikania głodzenia.
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Subunidade alfa da enzima trif ...... ciadas à ou à deficiência de .
@pt
Trifunctional enzyme subunit a ...... me A dehydrogenase deficiency.
@en
長鎖-3-ヒドロキシアシルCoAデヒドロゲナーゼ(long- ...... l-CoA dehydrogenase, LCHADがある。
@ja
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996,234,914
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HADHA (англ. Hydroxyacyl-CoA d ...... : ВалінW: Триптофан Y: Тирозин
@uk
HADHA (Hydroxyacyl-CoA dehydr ...... ر بواسطة جين HADHA في الإنسان.
@ar
La 3-idrossiacil-CoA (a lunga ...... nno una catena lunga 8 o 10 C.
@it
Niedobór dehydrogenazy 3-hydro ...... ndrial trifunctional protein).
@pl
Subunidade alfa da enzima trif ...... ciadas à ou à deficiência de .
@pt
Trifunctional enzyme subunit a ...... me A dehydrogenase deficiency.
@en
長鎖-3-ヒドロキシアシルCoAデヒドロゲナーゼ(long- ...... l-CoA dehydrogenase, LCHADがある。
@ja
label
3-idrossiacil-CoA (a lunga catena) deidrogenasi
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HADHA
@ar
HADHA
@en
HADHA
@pt
HADHA
@uk
Niedobór dehydrogenazy 3-hydroksyacylo-koenzymu A długołańcuchowych kwasów tłuszczowych
@pl
長鎖-3-ヒドロキシアシルCoAデヒドロゲナーゼ
@ja