Klippel–Trénaunay syndrome
Klippel–Trénaunay syndrome, formerly Klippel–Trénaunay–Weber syndrome and sometimes angioosteohypertrophy syndrome and hemangiectatic hypertrophy, is a rare congenital medical condition in which blood vessels and/or lymph vessels fail to form properly. The three main features are nevus flammeus (port-wine stain), venous and lymphatic malformations, and soft-tissue hypertrophy of the affected limb. It is similar to, though distinctly separate from, the less common Parkes Weber syndrome. The classical triad of Klippel–Trenaunay syndrome consists of:
known for
Angioosteohypertrophy syndromeHemangiectatic hypertrophyKlippel-Trenaunay-WeberKlippel-Trenaunay-Weber SyndromeKlippel-Trenaunay-Weber syndromeKlippel-Trenaunay SyndromeKlippel-Trenaunay syndromeKlippel-Trénaunay-WeberKlippel-Trénaunay-Weber SyndromeKlippel-Trénaunay-Weber syndromeKlippel-Trénaunay syndromeKlippel-trenaunay-weber syndromeKlippel Trenaunay Weber syndromeKlippel Trenaunay syndromeKlippel–Trenaunay syndromeKlippel–Trenaunay–Weber syndromeKlippel–Trénaunay–Weber syndrome
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AGGF1AngiomatosisAngioosteohypertrophy syndromeArteriovenous malformationCLOVES syndromeCasey MartinCavernous liver hemangiomaCobb syndromeDiffuse capillary malformation with overgrowthExternal iliac veinFrederick Parkes WeberHemangiectatic hypertrophyIndex of trauma and orthopaedics articlesKTKTSKTWKlippelKlippel-Trenaunay-WeberKlippel-Trenaunay-Weber SyndromeKlippel-Trenaunay-Weber syndromeKlippel-Trenaunay SyndromeKlippel-Trenaunay syndromeKlippel-Trénaunay-WeberKlippel-Trénaunay-Weber SyndromeKlippel-Trénaunay-Weber syndromeKlippel-Trénaunay syndromeKlippel-trenaunay-weber syndromeKlippel Trenaunay Weber syndromeKlippel Trenaunay syndromeKlippel–Trenaunay syndromeKlippel–Trenaunay–Weber syndromeKlippel–Trénaunay–Weber syndromeList of MeSH codes (C14)List of abbreviations for diseases and disordersList of diseases (K)List of fetal abnormalitiesList of orthopaedic eponymsList of skin conditionsList of syndromesLocal gigantism
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Klippel–Trénaunay syndrome
Klippel–Trénaunay syndrome, formerly Klippel–Trénaunay–Weber syndrome and sometimes angioosteohypertrophy syndrome and hemangiectatic hypertrophy, is a rare congenital medical condition in which blood vessels and/or lymph vessels fail to form properly. The three main features are nevus flammeus (port-wine stain), venous and lymphatic malformations, and soft-tissue hypertrophy of the affected limb. It is similar to, though distinctly separate from, the less common Parkes Weber syndrome. The classical triad of Klippel–Trenaunay syndrome consists of:
has abstract
El Síndrome de Klippel-Trenaun ...... os no se forman correctamente.
@es
Het syndroom van Klippel-Tréna ...... eohypertrofiesyndroom genoemd.
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Klippel-Trenaunays syndrom (KT ...... av ytliga blodkärl samt ödem.
@sv
Klippel–Trénaunay syndrome, fo ...... , usually the lower extremity.
@en
La sindrome angio-osteoipertro ...... tessuti molli e varici venose.
@it
Le syndrome de Klippel-Trenaun ...... férieurs de bas de contention.
@fr
Síndrome de Klippel–Trénaunay ...... om a Síndrome de Parkes Weber.
@pt
Zespół Klippla i Trénaunaya (z ...... o rozwoju zatorowości płucnej.
@pl
Синдром Кліппеля-Треноне (сино ...... и клапанній недостатності вен.
@uk
متلازمة كيبل ترينوني ويبر أو م ...... وعائية هو متلازمة ستيرج ويبر.
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DiseasesDB
eMedicine subject
derm
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eMedicine topic
213
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ICD10
ICD9
MedlinePlus
MeSH ID
OMIM id
Wikipage page ID
23,113,679
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Wikipage revision ID
1,013,730,349
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MRI
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DiseasesDB
eMedicineSubj
derm
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eMedicineTopic
ICD
MedlinePlus
MeshID
D007715
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name
Klippel–Trénaunay Syndrome
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OMIM
synonyms
KTS or KT
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hypernym
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El Síndrome de Klippel-Trenaun ...... os no se forman correctamente.
@es
Het syndroom van Klippel-Tréna ...... zijn in dezelfde extremiteit.
@nl
Klippel-Trenaunays syndrom (KT ...... g och lymfatiska abnormiteter.
@sv
Klippel–Trénaunay syndrome, fo ...... renaunay syndrome consists of:
@en
La sindrome angio-osteoipertro ...... tessuti molli e varici venose.
@it
Le syndrome de Klippel-Trenaun ...... anés et de veines variqueuses.
@fr
Síndrome de Klippel–Trénaunay ...... om a Síndrome de Parkes Weber.
@pt
Zespół Klippla i Trénaunaya (z ...... o rozwoju zatorowości płucnej.
@pl
Синдром Кліппеля-Треноне (сино ...... нцівки гіпертрофуються (як м'я
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متلازمة كيبل ترينوني ويبر أو م ...... وعائية هو متلازمة ستيرج ويبر.
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label
Klippel-Trénaunay-Weber-Syndrom
@de
Klippel-Trénaunays syndrom
@sv
Klippel–Trénaunay syndrome
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Sindrome angio-osteoipertrofica
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Syndrome de Klippel-Trenaunay
@fr
Syndroom van Klippel-Trénaunay
@nl
Síndrome de Klippel-Trenaunay
@pt
Síndrome de Klippel-Trenaunay-Weber
@es
Zespół Klippla-Trénaunaya
@pl
Синдром Кліппеля-Треноне
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name
Klippel–Trénaunay Syndrome
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