Primary lateral sclerosis
Primary lateral sclerosis (PLS) is a very rare neuromuscular disease characterized by progressive muscle weakness in the voluntary muscles. PLS belongs to a group of disorders known as motor neuron diseases. Motor neuron diseases develop when the nerve cells that control voluntary muscle movement degenerate and die, causing weakness in the muscles they control. PLS only affects upper motor neurons. There is no evidence of the degeneration of spinal motor neurons or muscle wasting (amyotrophy) that occurs in amyotrophic lateral sclerosis (ALS).
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Amyotrophic lateral sclerosisCarolyn GeorgeDavid Hart (political activist)Jeffrey MacklisList of abbreviations for diseases and disordersList of diseases (P)List of neurological conditions and disordersLou_GehrigMotor neuron diseasePLSPrimary Lateral SclerosisProgressive muscular atrophyRalph GombergSclerosis (medicine)Stiff-person syndrome
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Primary lateral sclerosis
Primary lateral sclerosis (PLS) is a very rare neuromuscular disease characterized by progressive muscle weakness in the voluntary muscles. PLS belongs to a group of disorders known as motor neuron diseases. Motor neuron diseases develop when the nerve cells that control voluntary muscle movement degenerate and die, causing weakness in the muscles they control. PLS only affects upper motor neurons. There is no evidence of the degeneration of spinal motor neurons or muscle wasting (amyotrophy) that occurs in amyotrophic lateral sclerosis (ALS).
has abstract
Die Primäre Lateralsklerose (P ...... imäre Lateralsklerose handeln.
@de
La sclérose latérale primitive ...... e détérioration intellectuelle
@fr
Per Sclerosi laterale primaria ...... rone, ma lascia intatto il 2°.
@it
Primaire laterale sclerose (af ...... s geen vaste behandeling voor.
@nl
Primary lateral sclerosis (PLS ...... ophic lateral sclerosis (ALS).
@en
Se trata de una forma de prese ...... er de mama.
* Datos: Q2881413
@es
DiseasesDB
eMedicine subject
neuro
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eMedicine topic
324
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ICD10
ICD9
MeSH ID
OMIM id
ORPHA
Wikipage page ID
page length (characters) of wiki page
Wikipage revision ID
997,002,810
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caption
This condition is inherited via an autosomal dominant manner
@en
DiseasesDB
eMedicineSubj
neuro
@en
eMedicineTopic
ICD
MeshID
D016472
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name
Primary lateral sclerosis
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OMIM
Orphanet
synonyms
Adult-onset primary lateral sclerosis
@en
wikiPageUsesTemplate
wordnet_type
subject
hypernym
comment
Die Primäre Lateralsklerose (P ...... imäre Lateralsklerose handeln.
@de
La sclérose latérale primitive ...... e détérioration intellectuelle
@fr
Per Sclerosi laterale primaria ...... rone, ma lascia intatto il 2°.
@it
Primaire laterale sclerose (af ...... s geen vaste behandeling voor.
@nl
Primary lateral sclerosis (PLS ...... ophic lateral sclerosis (ALS).
@en
Se trata de una forma de prese ...... er de mama.
* Datos: Q2881413
@es
label
Esclerosis lateral primaria
@es
Primaire laterale sclerose
@nl
Primary lateral sclerosis
@en
Primäre Lateralsklerose
@de
Sclerosi laterale primaria
@it
Sclérose latérale primitive
@fr
sameAs
wasDerivedFrom
isPrimaryTopicOf
name
Primary lateral sclerosis
@en