Primary biliary cholangitis
Primary biliary cholangitis (PBC), previously known as primary biliary cirrhosis, is an autoimmune disease of the liver. It results from a slow, progressive destruction of the small bile ducts of the liver, causing bile and other toxins to build up in the liver, a condition called cholestasis. Further slow damage to the liver tissue can lead to scarring, fibrosis, and eventually cirrhosis. Common symptoms are tiredness, itching, and in more advanced cases, jaundice. In early cases, the only changes may be in blood tests.
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A30-Cw5-B18-DR3-DQ2_(HLA_Haplotype)Adaptation (eye)Alagille syndromeAlbert GombaultAndrew Kenneth Burroughs1,2-dimethoxyethaanAnti-SSA/Ro autoantibodiesAnti-centromere antibodiesAnti-glycoprotein-210 antibodiesAnti-mitochondrial antibodyAnti-nuclear antibodyAnti-p62 antibodiesAnti-sp100 antibodiesAnti-thrombin antibodiesAntibodyAutoantibodyAutoimmune hepatitisBile acidBiliary cirrhosisBilirubinBranched-chain alpha-keto acid dehydrogenase complexCREST syndromeCTLA-4Canals of HeringChild–Pugh scoreCholangiocyteCholestasisCholestasis faciesCholestatic liver diseaseChronic liver diseaseCirrhosisClonorchis sinensisCoeliac_diseaseDihydrolipoyl transacetylaseDouglas_MacArthurDuctopeniaE3 binding proteinElevated alkaline phosphataseEpstein–Barr virus-associated lymphoproliferative diseasesErythema annulare centrifugum
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Primary biliary cholangitis
Primary biliary cholangitis (PBC), previously known as primary biliary cirrhosis, is an autoimmune disease of the liver. It results from a slow, progressive destruction of the small bile ducts of the liver, causing bile and other toxins to build up in the liver, a condition called cholestasis. Further slow damage to the liver tissue can lead to scarring, fibrosis, and eventually cirrhosis. Common symptoms are tiredness, itching, and in more advanced cases, jaundice. In early cases, the only changes may be in blood tests.
has abstract
Cirrose biliar primária (atual ...... em diretrizes de todo o mundo.
@pt
Die primär biliäre Cholangitis ...... r noch relativ unversehrt ist.
@de
La cholangite biliaire primiti ...... chez la majorité des malades.
@fr
La cirrosi biliar primària, so ...... s d'almenys 9:1 (dona a home).
@ca
La colangite biliare primitiva ...... dividui ogni 100.000 abitanti.
@it
La colangitis biliar primaria ...... 9 veces más común en mujeres.
@es
Pierwotne zapalenie dróg żółci ...... dzić do niewydolności wątroby.
@pl
Primary biliary cholangitis (P ...... tient advocacy groups in 2014.
@en
Primär biliär cirros (PBC) är ...... e även kallats Hanots sjukdom.
@sv
تشمع المرارة الأولي (بالإنجليز ...... حتى تشمعه وتصبح صعبة العلاج .
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complications
Cirrhosis,hepatic failure,portal hypertension
differential diagnosis
DiseasesDB
eMedicine subject
med
@en
eMedicine topic
223
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medical diagnosis
MedlinePlus
MeSH ID
OMIM id
symptoms
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1,025,145,627
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caption
Micrograph of PBC showing bile duct inflammation and injury, H&E stain
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causes
Autoimmune
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complications
differential
DiseasesDB
eMedicineSubj
med
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eMedicineTopic
frequency
ICD
MedlinePlus
MeshID
D008105
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name
Primary biliary cholangitis
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OMIM
onset
Usually middle-aged women
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risks
Female gender
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symptoms
synonyms
Primary biliary cirrhosis
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comment
Cirrose biliar primária (atual ...... em diretrizes de todo o mundo.
@pt
Die primär biliäre Cholangitis ...... r noch relativ unversehrt ist.
@de
La cholangite biliaire primiti ...... chez la majorité des malades.
@fr
La cirrosi biliar primària, so ...... s d'almenys 9:1 (dona a home).
@ca
La colangite biliare primitiva ...... dividui ogni 100.000 abitanti.
@it
La colangitis biliar primaria ...... ngitis esclerosante primaria.
@es
Pierwotne zapalenie dróg żółci ...... dzić do niewydolności wątroby.
@pl
Primary biliary cholangitis (P ...... changes may be in blood tests.
@en
Primär biliär cirros (PBC) är ...... e även kallats Hanots sjukdom.
@sv
تشمع المرارة الأولي (بالإنجليز ...... حتى تشمعه وتصبح صعبة العلاج .
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label
Cholangite biliaire primitive
@fr
Cirrose biliar primária
@pt
Cirrosi biliar primària
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Cirrosis biliar primaria
@es
Colangite biliare primitiva
@it
Pierwotna marskość żółciowa wątroby
@pl
Primary biliary cholangitis
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Primär biliär cirros
@sv
Primär biliäre Cholangitis
@de
التهاب الأقنية الصفراوية الأولي
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name
Primary biliary cholangitis
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