Rabson–Mendenhall syndrome
Rabson–Mendenhall syndrome is a rare autosomal recessive disorder characterized by severe insulin resistance. The disorder is caused by mutations in the insulin receptor gene. Symptoms include growth abnormalities of the head, face and nails, along with the development of acanthosis nigricans. Treatment involves controlling blood glucose levels by using insulin and incorporating a strategically planned, controlled diet. Also, direct actions against other symptoms may be taken (e.g. surgery for facial abnormalities) This syndrome usually affects children and has a prognosis of 1–2 years.
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Rabson–Mendenhall syndrome
Rabson–Mendenhall syndrome is a rare autosomal recessive disorder characterized by severe insulin resistance. The disorder is caused by mutations in the insulin receptor gene. Symptoms include growth abnormalities of the head, face and nails, along with the development of acanthosis nigricans. Treatment involves controlling blood glucose levels by using insulin and incorporating a strategically planned, controlled diet. Also, direct actions against other symptoms may be taken (e.g. surgery for facial abnormalities) This syndrome usually affects children and has a prognosis of 1–2 years.
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A síndrome de Rabson-Mendenhal ...... rística autossômica recessiva.
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Das Rabson-Mendenhall-Syndrom ...... n Rabson und E. N. Mendenhall.
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La sindrome di Rabson-Mendenha ...... rattere autosomico recessivo..
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Rabson–Mendenhall syndrome is ...... has a prognosis of 1–2 years.
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Zespół Rabsona-Mendenhalla (an ...... bson i Mendenhall w 1956 roku.
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متلازمة رابسون ميندينهال هي اض ...... ولها مستقبل مرضي من 1-2 سنوات.
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1,025,391,816
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ICD
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E13.
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name
Rabson–Mendenhall syndrome
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OMIM
Orphanet
synonyms
Pineal hyperplasia, insulin-resistant diabetes mellitus, and somatic abnormalities
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A síndrome de Rabson-Mendenhal ...... rística autossômica recessiva.
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Das Rabson-Mendenhall-Syndrom ...... n Rabson und E. N. Mendenhall.
@de
La sindrome di Rabson-Mendenha ...... rattere autosomico recessivo..
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Rabson–Mendenhall syndrome is ...... has a prognosis of 1–2 years.
@en
Zespół Rabsona-Mendenhalla (an ...... bson i Mendenhall w 1956 roku.
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متلازمة رابسون ميندينهال هي اض ...... ولها مستقبل مرضي من 1-2 سنوات.
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label
Rabson-Mendenhall-Syndrom
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Rabson–Mendenhall syndrome
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Sindrome di Rabson-Mendenhall
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Síndrome de Rabson-Mendenhall
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Zespół Rabsona-Mendenhalla
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متلازمة رابسون ميندينهال
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Rabson–Mendenhall syndrome
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