about
Acyl-CoA dehydrogenase short/branched chainBranched chain amino acid transaminase 2Branched chain amino acid transaminase 13-hydroxyisobutyryl-CoA hydrolaseProtein phosphatase, Mg2+/Mn2+ dependent 1KAU RNA binding methylglutaconyl-CoA hydrataseAcyl-CoA dehydrogenase family member 8Branched chain keto acid dehydrogenase kinaseHydroxysteroid 17-beta dehydrogenase 10Isovaleryl-CoA dehydrogenaseAldehyde dehydrogenase 6 family member A1Methylcrotonoyl-CoA carboxylase 1Methylcrotonoyl-CoA carboxylase 2Dihydrolipoamide branched chain transacylase E2Branched chain keto acid dehydrogenase E1 subunit alphaBranched chain keto acid dehydrogenase E1 subunit betaBranched chain ketoacid dehydrogenase kinase, isoform CRA_b3-hydroxyisobutyryl-CoA hydrolase, mitochondrial2-oxoisovalerate dehydrogenase subunit alpha/beta CT_340Acyl-Coenzyme A dehydrogenase family, member 8AU RNA binding protein/enoyl-coenzyme A hydrataseBranched chain ketoacid dehydrogenase kinase3-hydroxyisobutyrate dehydrogenase2-oxoisovalerate dehydrogenase, E1 component subunit alpha TTHA02292-oxoisovalerate dehydrogenase subunit alpha PA2247Pyruvate dehydrogenase E1 component subunit beta PA3416NAD-dependent L-serine dehydrogenase PA07433-hydroxyisobutyrate dehydrogenase PA35693-hydroxyisobutyryl-Coenzyme A hydrolaseBranched chain aminotransferase 2, mitochondrialBranched chain aminotransferase 1, cytosolicBranched chain ketoacid dehydrogenase E1, beta polypeptide2-oxoisovalerate dehydrogenase subunit alpha, mitochondrialBranched-chain alpha-keto acid dehydrogenase complex subunit alpha PP_44013-hydroxyisobutyrate dehydrogenase lpg01282-oxoisovalerate dehydrogenase subunit beta PA22483-hydroxyisobutyrate dehydrogenase PP_46663-hydroxyisobutyrate dehydrogenase RSP_01543-hydroxyisobutyrate dehydrogenase AHA_20833-hydroxyisobutyrate dehydrogenase VPA0625
P682
Molecular and biochemical basis of intermediate maple syrup urine disease. Occurrence of homozygous G245R and F364C mutations at the E1 alpha locus of Hispanic-Mexican patientsIdentification of the active site catalytic residue in human isovaleryl-CoA dehydrogenase.BCAA catabolism in brown fat controls energy homeostasis through SLC25A44
P921
Q21104908-2D68750A-B1B1-4859-ACF1-7E98BC1ADA99Q21109562-02CC5FDC-63E7-44D5-B60F-362038130158Q21109574-AE688026-C030-4F5B-A6F0-00078CDEA49DQ21111026-E717F39B-359E-472B-ACC4-A34DE62C8556Q21111719-28A6D373-126A-4B9D-ADE7-ACB2F260C7F8Q21112722-5FA4B1A7-DC05-4868-A9D1-09E4AE937D7EQ21113721-12ECE908-A960-4EBC-8F4A-0F529543F4EAQ21113873-C4362361-DE47-4775-B70F-4E0AD6410650Q21116211-A1853038-E6AB-4424-B39B-1298EE4A4BC6Q21118486-8D149A23-D1E2-49FC-8B96-82F1A540A501Q21118777-50419343-B783-48D5-B6D1-6232153B3BB4Q21119984-4DEB40E2-39B9-4E8E-897F-9915F7F69EFFQ21119986-03C74E87-EAED-41B3-8CC1-C950DFC1765EQ21121763-CD83C48D-0D31-40EC-862E-8AF9D7BA360EQ21121766-5230360D-6BFC-47ED-948F-559F4D931087Q21121766-9C72050E-7814-46D3-850D-55BB2EB2179BQ21121766-F79EC5A6-6646-440C-A3C8-C20B349E82D8Q21121767-842D206E-46D7-4730-933D-7D321553DA95Q21121767-ADFD733C-D0FC-4BB2-97E4-4152C4FCAD7AQ21121767-F5508F7D-E999-41D5-8015-F7D92041CE30Q21149603-3AB924D1-A7E6-44EE-B7DF-C422B1825BFAQ21150455-E2AF399C-D72E-457E-8AD7-203265859EEBQ21153952-3B58FAC5-07D1-4079-8C1E-C833B97B4769Q21495327-4A0949A8-CB19-493D-8B00-0B86B9C43410Q21496127-71B0CC6A-FAD0-4CA3-815A-DE3F6507235FQ21499171-104C1D49-EC68-48A3-9205-5BB797527E0DQ21499171-A39F4562-F21A-4686-97B1-73934389ADDEQ21499428-6C64C0D5-7126-4E2E-BD5C-08A59C080A6FQ21756314-CFF125ED-E132-49DD-917E-2F6DABDAF37CQ21758920-9DA51D88-E86E-4DF8-9109-D43D7FF54B6EQ21758920-DBB42607-4525-4F76-A350-6A86DB70940DQ21761234-9F22CC62-4186-45AF-A977-F8A905C1CD42Q21762155-6C36CDE7-DA0A-4848-8A1C-833083211617Q21762648-58700C75-4F49-4181-9775-5C3CC01E7D41Q21982276-7F5BA245-11BB-4A50-ACC9-E95183BE11AFQ21984732-3A1D636E-5890-408D-B0CE-4AD0B3E29650Q21984732-BB7DCEDB-CCB3-4399-B4EC-FB5B4C997880Q21984734-5BBCFD47-B1B9-4D43-9DD2-A2ED910D2908Q21985912-6725DE1D-94CC-4276-83E1-CFA15B52BF62Q21985912-9223DAB1-1D28-4E57-9142-AF1913C48315
P682
description
The chemical reactions and pat ...... soleucine, leucine and valine.
@en
biologisch proces
@nl
name
branched-chain amino acid catabolic process
@en
type
label
branched-chain amino acid catabolic process
@en
altLabel
GO:0009083
@en
branched chain family amino acid breakdown
@en
branched chain family amino acid catabolic process
@en
branched chain family amino acid catabolism
@en
branched chain family amino acid degradation
@en
prefLabel
branched-chain amino acid catabolic process
@en
P2888
P686
GO:0009083