Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
about
Combined defects in oxidative phosphorylation and fatty acid β-oxidation in mitochondrial diseaseBarth Syndrome: From Mitochondrial Dysfunctions Associated with Aberrant Production of Reactive Oxygen Species to Pluripotent Stem Cell StudiesALCAT1 controls mitochondrial etiology of fatty liver diseases, linking defective mitophagy to steatosisDisorders of phospholipid metabolism: an emerging class of mitochondrial disease due to defects in nuclear genesKnown unknowns of cardiolipin signaling: the best is yet to comeElimination of the unnecessary: intra- and extracellular signaling by anionic phospholipidsImaging mass spectrometry reveals loss of polyunsaturated cardiolipins in the cortical contusion, hippocampus, and thalamus after traumatic brain injuryDysregulation of cardiolipin biosynthesis in pediatric heart failure.Cardiac metabolic pathways affected in the mouse model of barth syndrome.Lipid metabolism in mitochondrial membranes.Impaired Cardiolipin Biosynthesis Prevents Hepatic Steatosis and Diet-Induced Obesity.Emerging roles for SIRT5 in metabolism and cancer.Influence of tissue, diet, and enzymatic remodeling on cardiolipin fatty acyl profile.Mitochondrial Trifunctional Protein Deficiency: Severe Cardiomyopathy and Cardiac Transplantation.Identifying off-target effects of etomoxir reveals that carnitine palmitoyltransferase I is essential for cancer cell proliferation independent of β-oxidation.Expression of human monolysocardiolipin acyltransferase-1 improves mitochondrial function in Barth Syndrome lymphoblasts.Estrogen receptor beta modulates permeability transition in brain mitochondria.
P2860
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P2860
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
description
2012 nî lūn-bûn
@nan
2012 թուականին հրատարակուած գիտական յօդուած
@hyw
2012 թվականին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@ast
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@en
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@en-gb
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@nl
type
label
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@ast
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@en
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@en-gb
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@nl
altLabel
Human Trifunctional Protein Alpha Links Cardiolipin Remodeling to Beta-Oxidation
@en
prefLabel
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@ast
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@en
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@en-gb
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@nl
P2093
P2860
P1433
P1476
Human trifunctional protein alpha links cardiolipin remodeling to beta-oxidation
@en
P2093
Edgard M Mejia
Genevieve C Sparagna
Grant M Hatch
Patrick C Choy
Ryan W Mitchell
William A Taylor
P2860
P304
P356
10.1371/JOURNAL.PONE.0048628
P407
P577
2012-01-01T00:00:00Z