Monolysocardiolipin in cultured fibroblasts is a sensitive and specific marker for Barth Syndrome
about
Role of calcium-independent phospholipase A2 in the pathogenesis of Barth syndromeSuccessful management of Barth syndrome: a systematic review highlighting the importance of a flexible and multidisciplinary approachBarth syndrome.Cardiolipin fingerprinting of leukocytes by MALDI-TOF/MS as a screening tool for Barth syndromeDisorders of phospholipid metabolism: an emerging class of mitochondrial disease due to defects in nuclear genesDistinct effects of tafazzin deletion in differentiated and undifferentiated mitochondria.Age-related decline in mitochondrial bioenergetics: does supercomplex destabilization determine lower oxidative capacity and higher superoxide production?Comprehensive approach to the quantitative analysis of mitochondrial phospholipids by HPLC-MS.Mitochondria-targeted antioxidant prevents cardiac dysfunction induced by tafazzin gene knockdown in cardiac myocytes.New clinical and molecular insights on Barth syndromeA role for peroxisome proliferator-activated receptor γ coactivator 1 (PGC-1) in the regulation of cardiac mitochondrial phospholipid biosynthesis.Lipidomics profiling by high-resolution LC-MS and high-energy collisional dissociation fragmentation: focus on characterization of mitochondrial cardiolipins and monolysocardiolipins.Expression of human monolysocardiolipin acyltransferase-1 improves mitochondrial function in Barth Syndrome lymphoblasts.Cardiolipin content in mitochondria from cultured skin fibroblasts harboring mutations in the mitochondrial ATP6 geneOmega-3 and omega-6 fatty acid differentially impact cardiolipin remodeling in activated macrophage
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Monolysocardiolipin in cultured fibroblasts is a sensitive and specific marker for Barth Syndrome
description
2006 nî lūn-bûn
@nan
2006 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի հոտեմբերին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@ast
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@en
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@en-gb
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@nl
type
label
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@ast
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@en
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@en-gb
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@nl
prefLabel
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@ast
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@en
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@en-gb
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@nl
P2093
P2860
P1476
Monolysocardiolipin in culture ...... ific marker for Barth Syndrome
@en
P2093
Agi Kyra Gedeon
David Ross Thorburn
James Jonathon Pitt
Michiel Adriaan van Werkhoven
P2860
P304
P356
10.1194/JLR.D600024-JLR200
P407
P577
2006-10-01T00:00:00Z