Targeting of nuclear-encoded proteins to the mitochondrial matrix: implications for human genetic defects
about
Identification of RNA splicing errors resulting in human ornithine transcarbamylase deficiencyTwo mitochondrial matrix proteases act sequentially in the processing of mammalian matrix enzymesRat liver mitochondrial intermediate peptidase (MIP): purification and initial characterizationChanges in brain mitochondrial bioenergetics in protein-deficient ratsImport of rat ornithine transcarbamylase precursor into mitochondria: two-step processing of the leader peptide.An enzyme trafficking defect in two patients with primary hyperoxaluria type 1: peroxisomal alanine/glyoxylate aminotransferase rerouted to mitochondria.Cleavage of precursors by the mitochondrial processing peptidase requires a compatible mature protein or an intermediate octapeptideMitochondrial import and processing of mutant human ornithine transcarbamylase precursors in cultured cells
P2860
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P2860
Targeting of nuclear-encoded proteins to the mitochondrial matrix: implications for human genetic defects
description
1986 nî lūn-bûn
@nan
1986 թուականին հրատարակուած գիտական յօդուած
@hyw
1986 թվականին հրատարակված գիտական հոդված
@hy
1986年の論文
@ja
1986年論文
@yue
1986年論文
@zh-hant
1986年論文
@zh-hk
1986年論文
@zh-mo
1986年論文
@zh-tw
1986年论文
@wuu
name
Targeting of nuclear-encoded p ...... ions for human genetic defects
@ast
Targeting of nuclear-encoded p ...... ions for human genetic defects
@en
Targeting of nuclear-encoded p ...... ions for human genetic defects
@en-gb
Targeting of nuclear-encoded p ...... ions for human genetic defects
@nl
type
label
Targeting of nuclear-encoded p ...... ions for human genetic defects
@ast
Targeting of nuclear-encoded p ...... ions for human genetic defects
@en
Targeting of nuclear-encoded p ...... ions for human genetic defects
@en-gb
Targeting of nuclear-encoded p ...... ions for human genetic defects
@nl
prefLabel
Targeting of nuclear-encoded p ...... ions for human genetic defects
@ast
Targeting of nuclear-encoded p ...... ions for human genetic defects
@en
Targeting of nuclear-encoded p ...... ions for human genetic defects
@en-gb
Targeting of nuclear-encoded p ...... ions for human genetic defects
@nl
P2093
P2860
P1476
Targeting of nuclear-encoded p ...... ions for human genetic defects
@en
P2093
F Kalousek
L E Rosenberg
W A Fenton
P2860
P304
P356
10.1111/J.1749-6632.1986.TB46550.X
P407
P577
1986-01-01T00:00:00Z