Defects in energy homeostasis in Leigh syndrome French Canadian variant through PGC-1alpha/LRP130 complex
about
LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAsMolecular dissection of the eukaryotic initiation factor 4E (eIF4E) export-competent RNPThe biology of IQGAP proteins: beyond the cytoskeletonLRPPRC mutation suppresses cytochrome oxidase activity by altering mitochondrial RNA transcript stability in a mouse modelPrimary respiratory chain disease causes tissue-specific dysregulation of the global transcriptome and nutrient-sensing signaling networkTwist-1 is a PPARdelta-inducible, negative-feedback regulator of PGC-1alpha in brown fat metabolismUnmasking activation of the zygotic genome using chromosomal deletions in the Drosophila embryoA human functional protein interaction network and its application to cancer data analysisDNA methylation status of nuclear-encoded mitochondrial genes underlies the tissue-dependent mitochondrial functionsLRPPRC and SLIRP interact in a ribonucleoprotein complex that regulates posttranscriptional gene expression in mitochondria.Mitochondrial and nuclear genomic responses to loss of LRPPRC expression.A compendium of human mitochondrial gene expression machinery with links to disease.Complex I deficiency due to loss of Ndufs4 in the brain results in progressive encephalopathy resembling Leigh syndrome.The bicoid stability factor controls polyadenylation and expression of specific mitochondrial mRNAs in Drosophila melanogaster.Leucine-rich pentatricopeptide-repeat containing protein regulates mitochondrial transcription.TLR signalling augments macrophage bactericidal activity through mitochondrial ROS.ABCB1 regulation through LRPPRC is influenced by the methylation status of the GC -100 box in its promoter.Knockdown of the cellular protein LRPPRC attenuates HIV-1 infection.Association of genes with physiological functions by comparative analysis of pooled expression microarray data.Nutrient sensing by the mitochondrial transcription machinery dictates oxidative phosphorylation.Cyclin D1 represses gluconeogenesis via inhibition of the transcriptional coactivator PGC1αRole of peroxisome proliferator-activated receptor gamma coactivator 1alpha in AKT/PKB-mediated inhibition of hepatitis B virus biosynthesis.OXPHOS-Mediated Induction of NAD+ Promotes Complete Oxidation of Fatty Acids and Interdicts Non-Alcoholic Fatty Liver Disease.Mitochondrial Diseases Part II: Mouse models of OXPHOS deficiencies caused by defects in regulatory factors and other components required for mitochondrial function.IQGAP1 and its binding proteins control diverse biological functions.LRP130 protein remodels mitochondria and stimulates fatty acid oxidation.Dual localized mitochondrial and nuclear proteins as gene expression regulators in plants?Metabolic adaptations through the PGC-1 alpha and SIRT1 pathways.The leucine-rich pentatricopeptide repeat-containing protein (LRPPRC) does not activate transcription in mammalian mitochondria.Modulation of PGC-1 coactivator pathways in brown fat differentiation through LRP130.Minireview: the PGC-1 coactivator networks: chromatin-remodeling and mitochondrial energy metabolismMitochondrion-associated protein LRPPRC suppresses the initiation of basal levels of autophagy via enhancing Bcl-2 stability.Integrative toxicoproteomics implicates impaired mitochondrial glutathione import as an off-target effect of troglitazoneThe effect of acute and chronic sprint-interval training on LRP130, SIRT3, and PGC-1α expression in human skeletal muscle.Proteomic profiling of lung adenocarcinoma indicates heightened DNA repair, antioxidant mechanisms and identifies LASP1 as a potential negative predictor of survival.PGC-1alpha, SIRT1 and AMPK, an energy sensing network that controls energy expenditure.The significance of LRPPRC overexpression in gastric cancer.White to beige conversion in PDE3B KO adipose tissue through activation of AMPK signaling and mitochondrial function.Mitochondrial DNA transcription regulation and nucleoid organization.Mitochondrial transcription: lessons from mouse models.
P2860
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P2860
Defects in energy homeostasis in Leigh syndrome French Canadian variant through PGC-1alpha/LRP130 complex
description
2006 nî lūn-bûn
@nan
2006 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@ast
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@en
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@en-gb
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@nl
type
label
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@ast
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@en
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@en-gb
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@nl
prefLabel
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@ast
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@en
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@en-gb
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@nl
P2093
P2860
P50
P921
P3181
P356
P1433
P1476
Defects in energy homeostasis ...... ough PGC-1alpha/LRP130 complex
@en
P2093
Jiandie Lin
Lindsay M Rohas
Marcus P Cooper
Wenli Yang
P2860
P304
P3181
P356
10.1101/GAD.1483906
P407
P577
2006-11-01T00:00:00Z