Defective C-propeptides of the proalpha2(I) chain of type I procollagen impede molecular assembly and result in osteogenesis imperfecta
about
Structural basis of homo- and heterotrimerization of collagen IA novel role of RNA helicase A in regulation of translation of type I collagen mRNAs.Segregation of type I collagen homo- and heterotrimers in fibrilsMolecular mechanism of type I collagen homotrimer resistance to mammalian collagenases.Role of LARP6 and nonmuscle myosin in partitioning of collagen mRNAs to the ER membrane.COL1 C-propeptide cleavage site mutations cause high bone mass osteogenesis imperfecta.Deficient degradation of homotrimeric type I collagen, α1(I)3 glomerulopathy in oim mice.The interface between catalytic and hemopexin domains in matrix metalloproteinase-1 conceals a collagen binding exosite.Collagen I and the fibroblast: high protein expression requires a new paradigm of post-transcriptional, feedback regulation.An unusual presentation of osteogenesis imperfecta type INonmuscle myosin-dependent synthesis of type I collagen.Osteogenesis imperfecta: recent findings shed new light on this once well-understood condition.New perspectives on osteogenesis imperfectaType I procollagen C-propeptide defects: study of genotype-phenotype correlation and predictive role of crystal structure.The unfolded protein response in skeletal development and homeostasis.Characterization of binding of LARP6 to the 5' stem-loop of collagen mRNAs: implications for synthesis of type I collagen
P2860
Q30842022-5EAD1F25-56F7-418E-ADC9-D0253F37179DQ33292421-A2D01B97-3886-48B5-9D82-51FEC57620CEQ33730397-701A508E-F3F6-4C9F-A39B-3DA40DEB9B07Q33991179-53EE9B55-69BF-4C5B-AB46-FD3E13CD7393Q34278273-76F2E508-A3E6-41A6-A858-E0DFCCD15741Q35012002-B51FDA76-0029-4FF9-9959-9E170F083FF9Q35489554-83DD4DCC-5509-4CF3-A2D9-752416988FA1Q35639806-04F61216-8196-4ABE-8E59-3B1635CEB692Q36593439-800868B7-49BC-44DC-9984-88817BF44488Q36856574-2548A37C-6D01-43AD-BE6D-4B6C8D64CBC0Q36907433-25CBF421-8D84-4172-8978-5074F4AE2A34Q37522199-0438CF4D-C638-41A6-954C-5FC1A09E2E82Q37889113-5CED4DDB-DBC3-4FC4-B9F4-0AC56D096804Q38242108-3B02B687-0BE9-4D37-A808-B70494D1743CQ38784676-BDCC59E0-3D29-4EBA-BCEE-C6137ED8873AQ41404805-3FD5E390-512A-4C09-9886-5B08036AA18D
P2860
Defective C-propeptides of the proalpha2(I) chain of type I procollagen impede molecular assembly and result in osteogenesis imperfecta
description
2008 nî lūn-bûn
@nan
2008 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի հունիսին հրատարակված գիտական հոդված
@hy
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
name
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@ast
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@en
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@en-gb
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@nl
type
label
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@ast
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@en
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@en-gb
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@nl
prefLabel
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@ast
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@en
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@en-gb
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@nl
P2093
P2860
P50
P921
P356
P1476
Defective C-propeptides of the ...... ult in osteogenesis imperfecta
@en
P2093
Andrea S Drenguis
Diana Chen
James M Pace
Mary Wiese
Natalia Kuznetsova
Suzanne H Mooney
Ulrike Schwarze
P2860
P304
P356
10.1074/JBC.M801982200
P407
P577
2008-06-06T00:00:00Z