Unraveling of the E-helices and disruption of 4-fold pores are associated with iron mishandling in a mutant ferritin causing neurodegeneration

Unraveling of the E-helices and disruption of 4-fold pores are associated with iron mishandling in a mutant ferritin causing neurodegeneration

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http://www.wikidata.org/entity/Q24318488
Neurodegeneration with brain iron accumulation: update on pathogenic mechanismsMutant ferritin L-chains that cause neurodegeneration act in a dominant-negative manner to reduce ferritin iron incorporationNeuroferritinopathy: From ferritin structure modification to pathogenetic mechanismA novel ferritin light chain mutation in neuroferritinopathy with an atypical presentationBrain, blood, and iron: perspectives on the roles of erythrocytes and iron in neurodegeneration.Abnormal iron metabolism in fibroblasts from a patient with the neurodegenerative disease hereditary ferritinopathy.Iron loading-induced aggregation and reduction of iron incorporation in heteropolymeric ferritin containing a mutant light chain that causes neurodegeneration.Systemic and cerebral iron homeostasis in ferritin knock-out mice.A mutant light-chain ferritin that causes neurodegeneration has enhanced propensity toward oxidative damage.Effect of Systemic Iron Overload and a Chelation Therapy in a Mouse Model of the Neurodegenerative Disease Hereditary FerritinopathyAbnormal iron homeostasis and neurodegeneration.Brain iron homeostasis: from molecular mechanisms to clinical significance and therapeutic opportunitiesThe neuropathology of neurodegeneration with brain iron accumulation.Regulation of quinolinic acid neosynthesis in mouse, rat and human brain by iron and iron chelators in vitro.Detergent Insoluble Proteins and Inclusion Body-Like Structures Immunoreactive for PRKDC/DNA-PK/DNA-PKcs, FTL, NNT, and AIFM1 in the Amygdala of Cognitively Impaired Elderly Persons.Computational approaches for deciphering the equilibrium and kinetic properties of iron transport proteins.
P2860

Unraveling of the E-helices and disruption of 4-fold pores are associated with iron mishandling in a mutant ferritin causing neurodegeneration

Item
http://www.wikidata.org/entity/Q24318488
description
2010 nî lūn-bûn
@nan
2010 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի հունվարին հրատարակված գիտական հոդված
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2010年の論文
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2010年論文
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2010年論文
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2010年論文
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2010年論文
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2010年論文
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2010年论文
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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Unraveling of the E-helices an ...... itin causing neurodegeneration
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P407
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P577
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P921
P932