PRKCSH/80K-H, the protein mutated in polycystic liver disease, protects polycystin-2/TRPP2 against HERP-mediated degradation
about
Transcriptomic analyses of sexual dimorphism of the zebrafish liver and the effect of sex hormonesInternational Union of Basic and Clinical Pharmacology. LXXVI. Current progress in the mammalian TRP ion channel familyA polycystin-centric view of cyst formation and disease: the polycystins revisitedThe delicate balance between secreted protein folding and endoplasmic reticulum-associated degradation in human physiologyWhole-exome sequencing reveals LRP5 mutations and canonical Wnt signaling associated with hepatic cystogenesisHDAC6 is overexpressed in cystic cholangiocytes and its inhibition reduces cystogenesisA genetic interaction network of five genes for human polycystic kidney and liver diseases defines polycystin-1 as the central determinant of cyst formationSecondary and tertiary structure modeling reveals effects of novel mutations in polycystic liver disease genes PRKCSH and SEC63.N-glycosylation determines the abundance of the transient receptor potential channel TRPP2Isolated polycystic liver disease.Mutations in GANAB, Encoding the Glucosidase IIα Subunit, Cause Autosomal-Dominant Polycystic Kidney and Liver DiseaseHerp regulates Hrd1-mediated ubiquitylation in a ubiquitin-like domain-dependent manner.Short-hairpin RNA library: identification of therapeutic partners for gefitinib-resistant non-small cell lung cancer.Polycystic diseases in visceral organs.Endoplasmic Reticulum-Targeted Subunit Toxins Provide a New Approach to Rescue Misfolded Mutant Proteins and Revert Cell Models of Genetic Diseases.Hepatocystin is Essential for TRPM7 Function During Early Embryogenesis.Zebrafish models of human liver development and diseaseThe zebrafish as a model to study polycystic liver disease.Polycystin-1 negatively regulates Polycystin-2 expression via the aggresome/autophagosome pathway.Systematic review: the pathophysiology and management of polycystic liver disease.TRP channels.Therapeutic Targets in Polycystic Liver Disease.Herp coordinates compartmentalization and recruitment of HRD1 and misfolded proteins for ERAD.Posttranslational regulation of polycystin-2 protein expression as a novel mechanism of cholangiocyte reaction and repair from biliary damage.Using zebrafish to model liver diseases-Where do we stand?
P2860
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P2860
PRKCSH/80K-H, the protein mutated in polycystic liver disease, protects polycystin-2/TRPP2 against HERP-mediated degradation
description
2010 nî lūn-bûn
@nan
2010 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@ast
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@en
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@en-gb
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@nl
type
label
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@ast
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@en
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@en-gb
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@nl
prefLabel
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@ast
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@en
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@en-gb
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@nl
P2093
P2860
P921
P356
P1476
PRKCSH/80K-H, the protein muta ...... inst HERP-mediated degradation
@en
P2093
Christina Engel
Christopher Boehlke
E Wolfgang Kuehn
Hongquan Peng
Hongyu Gao
Kassiani Skouloudaki
Michael Pütz
Tomasz Wegierski
P2860
P356
10.1093/HMG/DDP463
P407
P577
2010-01-01T00:00:00Z