Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit - Wikidata - awgldk - TriplyDB

Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit

Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit

http://www.wikidata.org/entity/Q24337773

about

MPV17L2 is required for ribosome assembly in mitochondria C7orf30 is necessary for biogenesis of the large subunit of the mitochondrial ribosome Human G-proteins, ObgH1 and Mtg1, associate with the large mitochondrial ribosome subunit and are involved in translation and assembly of respiratory complexes The human mitochondrial transcriptome and the RNA-binding proteins that regulate its expression The universally conserved prokaryotic GTPases Assignment of 2'-O-methyltransferases to modification sites on the mammalian mitochondrial large subunit 16 S ribosomal RNA (rRNA)Mitochondrial ribosomal RNA (rRNA) methyltransferase family members are positioned to modify nascent rRNA in foci near the mitochondrial DNA nucleoid Transcription-independent role for human mitochondrial RNA polymerase in mitochondrial ribosome biogenesis The role of the mitochondrial ribosome in human disease: searching for mutations in 12S mitochondrial rRNA with high disruptive potential.MRM2 and MRM3 are involved in biogenesis of the large subunit of the mitochondrial ribosome.Mitochondrial ribosomal protein L12 selectively associates with human mitochondrial RNA polymerase to activate transcription.Yeast as a system for modeling mitochondrial disease mechanisms and discovering therapies.A bioinformatic survey of RNA-binding proteins in Plasmodium Mechanism of protein biosynthesis in mammalian mitochondria.C7orf30 specifically associates with the large subunit of the mitochondrial ribosome and is involved in translation Mitochondrial nucleoid interacting proteins support mitochondrial protein synthesis.Mitochondrial ribosome assembly in health and disease Autophagy is induced through the ROS-TP53-DRAM1 pathway in response to mitochondrial protein synthesis inhibition.AFG3L2 supports mitochondrial protein synthesis and Purkinje cell survival.An RMND1 Mutation causes encephalopathy associated with multiple oxidative phosphorylation complex deficiencies and a mitochondrial translation defect.Two independent activities define Ccm1p as a moonlighting protein in Saccharomyces cerevisiae The Genomes of Three Uneven Siblings: Footprints of the Lifestyles of Three Trichoderma Species.Human Cytomegalovirus Infection Upregulates the Mitochondrial Transcription and Translation Machineries Identification and characterization of CHCHD1, AURKAIP1, and CRIF1 as new members of the mammalian mitochondrial ribosome.The Pseudouridine Synthase RPUSD4 Is an Essential Component of Mitochondrial RNA Granules Mitochondrial protein synthesis: figuring the fundamentals, complexities and complications, of mammalian mitochondrial translation.A homozygous missense mutation in ERAL1, encoding a mitochondrial rRNA chaperone, causes Perrault syndrome.The process of mammalian mitochondrial protein synthesis.Regulation of Mammalian Mitochondrial Gene Expression: Recent Advances.CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.MRPS27 is a pentatricopeptide repeat domain protein required for the translation of mitochondrially encoded proteins.Human C4orf14 interacts with the mitochondrial nucleoid and is involved in the biogenesis of the small mitochondrial ribosomal subunit.The nucleoid as a site of rRNA processing and ribosome assembly Drosophila protease ClpXP specifically degrades DmLRPPRC1 controlling mitochondrial mRNA and translation.The presence of highly disruptive 16S rRNA mutations in clinical samples indicates a wider role for mutations of the mitochondrial ribosome in human disease.Human mitochondrial leucyl tRNA synthetase can suppress non cognate pathogenic mt-tRNA mutations The human RNA-binding protein RBFA promotes the maturation of the mitochondrial ribosome.Down-regulation of MRPS23 inhibits rat breast cancer proliferation and metastasis.Mutations in mitochondrial ribosomal protein MRPL12 leads to growth retardation, neurological deterioration and mitochondrial translation deficiency.Proximity Biotinylation as a Method for Mapping Proteins Associated with mtDNA in Living Cells.

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P2860

Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit

http://www.wikidata.org/entity/Q24337773

description

2010 nî lūn-bûn

@nan

2010 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած

@hyw

2010 թվականի սեպտեմբերին հրատարակված գիտական հոդված

@hy

2010年の論文

@ja

2010年論文

@yue

2010年論文

@zh-hant

2010年論文

@zh-hk

2010年論文

@zh-mo

2010年論文

@zh-tw

2010年论文

@wuu

name

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@ast

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@en

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@en-gb

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@nl

type

label

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@ast

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@en

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@en-gb

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@nl

prefLabel

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@ast

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@en

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@en-gb

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

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P1433

Biochemical Journal

P1476

Human ERAL1 is a mitochondrial ...... itochondrial ribosomal subunit

@en

P2093

Agata Rozanska

http://www.w3.org/2001/XMLSchema#string

Mateusz Wydro

http://www.w3.org/2001/XMLSchema#string

Robert N Lightowlers

http://www.w3.org/2001/XMLSchema#string

Sven Dennerlein

http://www.w3.org/2001/XMLSchema#string

Zofia M A Chrzanowska-Lightowlers

http://www.w3.org/2001/XMLSchema#string

P2860

A functional peptidyl-tRNA hydrolase, ICT1, has been recruited into the human mitochondrial ribosome

Isolation of DAP3, a novel mediator of interferon-gamma-induced cell death

mtRF1a is a human mitochondrial translation release factor decoding the major termination codons UAA and UAG

Structure of ERA in complex with the 3' end of 16S rRNA: Implications for ribosome biogenesis

Sequence and organization of the human mitochondrial genome

The m-AAA protease defective in hereditary spastic paraplegia controls ribosome assembly in mitochondria.

Human mitochondrial transcription factor B1 methylates ribosomal RNA at a conserved stem-loop

A new face on apoptosis: death-associated protein 3 and PDCD9 are mitochondrial ribosomal proteins

CLIP: a method for identifying protein-RNA interaction sites in living cells

Interaction of Era with the 30S ribosomal subunit implications for 30S subunit assembly

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551-8

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scholarly article

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4556448

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10.1042/BJ20100757

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P407

P433

3

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430

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2010-09-15T00:00:00Z

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45095760

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P698

20604745

http://www.w3.org/2001/XMLSchema#string

P921

ribosomal small subunit binding

Era like 12S mitochondrial rRNA chaperone 1

molecular chaperones

P932

2995420

http://www.w3.org/2001/XMLSchema#string