Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats - Wikidata - awgldk - TriplyDB

Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats

Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats

http://www.wikidata.org/entity/Q27316635

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Epithelial Anion Transport as Modulator of Chemokine Signaling Origins of cystic fibrosis lung disease Airway Gland Structure and Function Barriers to inhaled gene therapy of obstructive lung diseases: A review Impact of the F508del mutation on ovine CFTR, a Cl- channel with enhanced conductance and ATP-dependent gating.Improved Growth Patterns in Cystic Fibrosis Mice after Loss of Histone Deacetylase 6.Cellular distribution and function of ion channels involved in transport processes in rat tracheal epithelium.Longevity and plasticity of CFTR provide an argument for noncanonical SNP organization in hominid DNA A functional anatomic defect of the cystic fibrosis airway.Animal models of gastrointestinal and liver diseases. Animal models of cystic fibrosis: gastrointestinal, pancreatic, and hepatobiliary disease and pathophysiology.Composition of mineralizing incisor enamel in cystic fibrosis transmembrane conductance regulator-deficient mice.Sonographic evidence of abnormal tracheal cartilage ring structure in cystic fibrosis.Growth deficits in cystic fibrosis mice begin in utero prior to IGF-1 reduction.Pancreatic pathophysiology in cystic fibrosis.Cellular chloride and bicarbonate retention alters intracellular pH regulation in Cftr KO crypt epithelium.The innate immune function of airway epithelial cells in inflammatory lung disease Lessons learned from the cystic fibrosis pig.Combination therapy with cystic fibrosis transmembrane conductance regulator modulators augment the airway functional microanatomy.In vivo imaging of airway cilia and mucus clearance with micro-optical coherence tomography.Cystic fibrosis genetics: from molecular understanding to clinical application.Tailored Pig Models for Preclinical Efficacy and Safety Testing of Targeted Therapies.Postnatal airway growth in cystic fibrosis piglets.Genetic medicines for CF: Hype versus reality.Impact of gene editing on the study of cystic fibrosis.rAAV-CFTRΔR Rescues the Cystic Fibrosis Phenotype in Human Intestinal Organoids and Cystic Fibrosis Mice.Characterization of primary rat nasal epithelial cultures in CFTR knockout rats as a model for CF sinus disease.Sinus hypoplasia in the cystic fibrosis rat resolves in the absence of chronic infection.A novel translational model for fetoscopic intratracheal delivery of nanoparticles in piglets.Stem cell-derived organoids to model gastrointestinal facets of cystic fibrosis.PATHOPHYSIOLOGIC EVALUATION OF THE TRANSGENIC CFTR "GUT-CORRECTED" PORCINE MODEL OF CYSTIC FIBROSIS.Roadmap for an early gene therapy for cystic fibrosis airway disease.Use of ferrets for electrophysiologic monitoring of ion transport.Klotho Inhibits Interleukin-8 Secretion from Cystic Fibrosis Airway Epithelia.Reduced bone length, growth plate thickness, bone content, and IGF-I as a model for poor growth in the CFTR-deficient rat.AJRCCM: 100-Year Anniversary. Progress along the Pathway of Discovery Leading to Treatment and Cure of Cystic Fibrosis.Development of an airway mucus defect in the cystic fibrosis rat.Medical and Surgical Advancements in the Management of Cystic Fibrosis Chronic Rhinosinusitis.Therapeutic attenuation of the epithelial sodium channel with a SPLUNC1-derived peptide in airway diseases.Lack of cystic fibrosis transmembrane conductance regulator disrupts fetal airway development in pigs.Airway disease phenotypes in animal models of cystic fibrosis.

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P2860

Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats

http://www.wikidata.org/entity/Q27316635

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2014 nî lūn-bûn

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Andre Chambers

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David M Bedwell

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Katherine L Tuggle

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P2860

Method for quantitative study of airway functional microanatomy using micro-optical coherence tomography

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer

Genome editing with engineered zinc finger nucleases

Targeted integration in rat and mouse embryos with zinc-finger nucleases

Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation.

Enamel pathology resulting from loss of function in the cystic fibrosis transmembrane conductance regulator in a porcine animal model

New features in the development of the submucosal gland of the respiratory tract.

Disease phenotype of a ferret CFTR-knockout model of cystic fibrosis.

An international randomized multicenter comparison of nasal potential difference techniques.

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