Crystal Structure of Human -Galactosidase: STRUCTURAL BASIS OF GM1 GANGLIOSIDOSIS AND MORQUIO B DISEASES
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Emerging novel concept of chaperone therapies for protein misfolding diseasesPharmacological chaperones for human -N-acetylgalactosaminidaseStructural Insights into the Substrate Specificity of Streptococcus pneumoniae β(1,3)-Galactosidase BgaCInduced Structural Disorder as a Molecular Mechanism for Enzyme Dysfunction in Phosphoglucomutase 1 DeficiencyCrystallization and preliminary X-ray diffraction data of β-galactosidase from Aspergillus niger.Evaluation of N-nonyl-deoxygalactonojirimycin as a pharmacological chaperone for human GM1 gangliosidosis leads to identification of a feline model suitable for testing enzyme enhancement therapy.Candidate molecules for chemical chaperone therapy of GM1-gangliosidosis.Pharmacological chaperone therapy for lysosomal storage diseases.Ganglioside biochemistryInteraction between the elastin peptide VGVAPG and human elastin binding proteinVaProS: a database-integration approach for protein/genome information retrieval.Structural features of Aspergillus niger β-galactosidase define its activity against glycoside linkages.Glycomimetic-based pharmacological chaperones for lysosomal storage disorders: lessons from Gaucher, GM1-gangliosidosis and Fabry diseases.N-acetylgalatosamine-Mediated Regulation of the aga Operon by AgaR in Streptococcus pneumoniae.Structural basis of pharmacological chaperoning for human β-galactosidase.Enzyme replacement for GM1-gangliosidosis: Uptake, lysosomal activation, and cellular disease correction using a novel β-galactosidase:RTB lectin fusion.Expression, purification, crystallization and preliminary X-ray crystallographic analysis of tomato β-galactosidase 4.A bicyclic 1-deoxygalactonojirimycin derivative as a novel pharmacological chaperone for GM1 gangliosidosis.β-Galactosidosis in Patient with Intermediate GM1 and MBD Phenotype.A Specific Activity-Based Probe to Monitor Family GH59 Galactosylceramidase, the Enzyme Deficient in Krabbe Disease.Age-related modulation of plasmatic beta-Galactosidase activity in healthy subjects and in patients affected by T2DM.Polyethylene glycol-b-poly(lactic acid) polymersomes as vehicles for enzyme replacement therapy.SAAMP 2.0: an algorithm to predict genotype-phenotype correlation of lysosomal storage diseases.The Structure of an Archaeal β-Glucosaminidase Provides Insight into Glycoside Hydrolase Evolution.Structural and functional analysis of tomato β-galactosidase 4: insight into the substrate specificity of the fruit softening-related enzyme.Tuning protein folding in lysosomal storage diseases: the chemistry behind pharmacological chaperones.Aggrecan catabolism during mesenchymal stromal cellin vitrochondrogenesis
P2860
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P2860
Crystal Structure of Human -Galactosidase: STRUCTURAL BASIS OF GM1 GANGLIOSIDOSIS AND MORQUIO B DISEASES
description
2012 nî lūn-bûn
@nan
2012 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@ast
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@en
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@nl
type
label
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@ast
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@en
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@nl
prefLabel
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@ast
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@en
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@nl
P2093
P2860
P921
P3181
P356
P1476
Crystal Structure of Human -G ...... SIDOSIS AND MORQUIO B DISEASES
@en
P2093
Kenjiro Yuki
Kimihito Usui
Toshinari Ochi
Toshiyuki Shimizu
Umeharu Ohto
Yoshinori Satow
P2860
P304
P3181
P356
10.1074/JBC.M111.293795
P407
P577
2012-01-13T00:00:00Z