Pathophysiology of gene-targeted mouse models for cystic fibrosis - Wikidata - awgldk - TriplyDB

Pathophysiology of gene-targeted mouse models for cystic fibrosis

Pathophysiology of gene-targeted mouse models for cystic fibrosis

http://www.wikidata.org/entity/Q28295602

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Multi-country estimate of different manifestations of aspergillosis in cystic fibrosis Bestrophin-1 enables Ca2+-activated Cl- conductance in epithelia Regulation of dental enamel shape and hardness Airway surface liquid volume regulation determines different airway phenotypes in liddle compared with betaENaC-overexpressing mice Acute regulation of the SLC26A3 congenital chloride diarrhoea anion exchanger (DRA) expressed in Xenopus oocytes Progress toward generating a ferret model of cystic fibrosis by somatic cell nuclear transfer Engineering large animal models of human disease Origins of cystic fibrosis lung disease Distribution of ClC-2 chloride channel in rat and human epithelial tissues Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer Polycystin 1 is required for the structural integrity of blood vessels STa and cGMP stimulate CFTR translocation to the surface of villus enterocytes in rat jejunum and is regulated by protein kinase G Noninvasive real-time measurement of nasal mucociliary clearance in mice by pinhole gamma scintigraphy.Bicarbonate and functional CFTR channel are required for proper mucin secretion and link cystic fibrosis with its mucus phenotype.High-resolution mucociliary transport measurement in live excised large animal trachea using synchrotron X-ray imaging.Reduced blood pressure of CFTR-F508del carriers correlates with diminished arterial reactivity rather than circulating blood volume in mice Molecular insights into the physiology of the 'thin film' of airway surface liquid.Pathology of gastrointestinal organs in a porcine model of cystic fibrosis.Transduction efficiencies of novel AAV vectors in mouse airway epithelium in vivo and human ciliated airway epithelium in vitro.Chemosensory functions for pulmonary neuroendocrine cells Cellular distribution and function of ion channels involved in transport processes in rat tracheal epithelium.Gel-forming mucins form distinct morphologic structures in airways Single HA2 mutation increases the infectivity and immunogenicity of a live attenuated H5N1 intranasal influenza vaccine candidate lacking NS1.The Mouse Lemur, a Genetic Model Organism for Primate Biology, Behavior, and Health.Alveolar inflammation in cystic fibrosis.Common gene therapy viral vectors do not efficiently penetrate sputum from cystic fibrosis patients.Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth.Pathophysiological preconditions promoting mixed "black" pigment plus cholesterol gallstones in a DeltaF508 mouse model of cystic fibrosis.Targeted ablation of the abcc6 gene results in ectopic mineralization of connective tissues Thiazolidinone CFTR inhibitor identified by high-throughput screening blocks cholera toxin-induced intestinal fluid secretion.Variation in MSRA modifies risk of neonatal intestinal obstruction in cystic fibrosis.Altered ion transport by thyroid epithelia from CFTR(-/-) pigs suggests mechanisms for hypothyroidism in cystic fibrosis.Completion of the swine genome will simplify the production of swine as a large animal biomedical model.Electrolyte transport in the mammalian colon: mechanisms and implications for disease.Hypersusceptibility of cystic fibrosis mice to chronic Pseudomonas aeruginosa oropharyngeal colonization and lung infection.Cystic fibrosis transmembrane conductance regulator with a shortened R domain rescues the intestinal phenotype of CFTR-/- mice.Use of genetically engineered mice in drug discovery and development: wielding Occam's razor to prune the product portfolio.Characterization of nasal potential difference in cftr knockout and F508del-CFTR mice.Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia.Abnormal surface liquid pH regulation by cultured cystic fibrosis bronchial epithelium.

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P2860

Pathophysiology of gene-targeted mouse models for cystic fibrosis

http://www.wikidata.org/entity/Q28295602

description

1999 nî lūn-bûn

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1999 թուականի Յունուարին հրատարակուած գիտական յօդուած

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1999 թվականի հունվարին հրատարակված գիտական հոդված

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1999年の論文

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1999年論文

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Pathophysiology of gene-targeted mouse models for cystic fibrosis

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Pathophysiology of gene-targeted mouse models for cystic fibrosis

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Pathophysiology of gene-targeted mouse models for cystic fibrosis

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Pathophysiology of gene-targeted mouse models for cystic fibrosis

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Pathophysiology of gene-targeted mouse models for cystic fibrosis

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Pathophysiology of gene-targeted mouse models for cystic fibrosis

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Pathophysiology of gene-targeted mouse models for cystic fibrosis

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Pathophysiology of gene-targeted mouse models for cystic fibrosis

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PHYSREV.1999.79.1.S193

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Physiological Reviews

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Pathophysiology of gene-targeted mouse models for cystic fibrosis

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B R Grubb

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R C Boucher

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P2860

Cystic fibrosis heterozygote resistance to cholera toxin in the cystic fibrosis mouse model

Identification of the cystic fibrosis gene: chromosome walking and jumping

CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP

The genetic advantage hypothesis in cystic fibrosis heterozygotes: a murine study

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

Correction of the ion transport defect in cystic fibrosis transgenic mice by gene therapy

Expression cloning and cDNA sequencing of the Na+/glucose co-transporter

Identification of the cystic fibrosis gene: genetic analysis

Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation.

Cloning the mouse homolog of the human cystic fibrosis transmembrane conductance regulator gene.

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pathophysiology

cystic fibrosis