Characterization of dysferlin deficient SJL/J mice to assess preclinical drug efficacy: fasudil exacerbates muscle disease phenotype
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The effects of MyD88 deficiency on disease phenotype in dysferlin-deficient A/J mice: role of endogenous TLR ligands.Activation of the ubiquitin proteasome pathway in a mouse model of inflammatory myopathy: a potential therapeutic targetThe proton pump inhibitor lansoprazole improves the skeletal phenotype in dystrophin deficient mdx miceEffects of Dantrolene Therapy on Disease Phenotype in Dystrophin Deficient mdx Mice.Inhibition of inflammation with celastrol fails to improve muscle function in dysferlin-deficient A/J miceEnhanced Muscular Dystrophy from Loss of Dysferlin Is Accompanied by Impaired Annexin A6 Translocation after Sarcolemmal Disruption.Behavioral and locomotor measurements using an open field activity monitoring system for skeletal muscle diseases.The molecular basis of skeletal muscle weakness in a mouse model of inflammatory myopathyDeletion of galectin-3 exacerbates microglial activation and accelerates disease progression and demise in a SOD1(G93A) mouse model of amyotrophic lateral sclerosisAssessment of disease activity in muscular dystrophies by noninvasive imagingPhosphatidylinositol 4-kinase III beta is essential for replication of human rhinovirus and its inhibition causes a lethal phenotype in vivo.Role of Toll-like receptors in the pathogenesis of dystrophin-deficient skeletal and heart muscleHip region muscular dystrophy and emergence of motor deficits in dysferlin-deficient Bla/J mice.Translational research and therapeutic perspectives in dysferlinopathies.Valproate and sodium butyrate attenuate manganese-decreased locomotor activity and astrocytic glutamate transporters expression in mice.Genetic disruption of Smad7 impairs skeletal muscle growth and regeneration.
P2860
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P2860
Characterization of dysferlin deficient SJL/J mice to assess preclinical drug efficacy: fasudil exacerbates muscle disease phenotype
description
2010 nî lūn-bûn
@nan
2010 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
Characterization of dysferlin ...... bates muscle disease phenotype
@ast
Characterization of dysferlin ...... bates muscle disease phenotype
@en
Characterization of dysferlin ...... bates muscle disease phenotype
@nl
type
label
Characterization of dysferlin ...... bates muscle disease phenotype
@ast
Characterization of dysferlin ...... bates muscle disease phenotype
@en
Characterization of dysferlin ...... bates muscle disease phenotype
@nl
prefLabel
Characterization of dysferlin ...... bates muscle disease phenotype
@ast
Characterization of dysferlin ...... bates muscle disease phenotype
@en
Characterization of dysferlin ...... bates muscle disease phenotype
@nl
P2093
P2860
P50
P1433
P1476
Characterization of dysferlin ...... bates muscle disease phenotype
@en
P2093
Eric P Hoffman
Jack H Van der Meulen
Susan M Knoblach
P2860
P304
P356
10.1371/JOURNAL.PONE.0012981
P407
P577
2010-09-24T00:00:00Z