Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome. - Wikidata - awgldk - TriplyDB

Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

http://www.wikidata.org/entity/Q30543370

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Complement factor B mutations in atypical hemolytic uremic syndrome-disease-relevant or benign?Successful Remission of Hemolytic-Uremic Syndrome During the Third-line Weekly Gemcitabine for Metastatic Breast Cancer Class II human leucocyte antigen DRB1*11 in hairy cell leukaemia patients with and without haemolytic uraemic syndrome.Absolute immature platelet count dynamics in diagnosing and monitoring the clinical course of thrombotic thrombocytopenic purpura.Identification and management of atypical hemolytic uremic syndrome immediately post-heart transplantation.An international consensus approach to the management of atypical hemolytic uremic syndrome in children.Modified Ham test for atypical hemolytic uremic syndrome Role of the skin biopsy in the diagnosis of atypical hemolytic uremic syndrome.Variable Eculizumab Clearance Requires Pharmacodynamic Monitoring to Optimize Therapy for Thrombotic Microangiopathy after Hematopoietic Stem Cell Transplantation.The genetic fingerprint of susceptibility for transplant-associated thrombotic microangiopathy.von Willebrand factor is a cofactor in complement regulation.Turkish pediatric atypical hemolytic uremic syndrome registry: initial analysis of 146 patients Reincarnation of ancient links between coagulation and complement.Rationale for Adjunctive Therapies for Pediatric Sepsis Induced Multiple Organ Failure.Acquired thrombotic thrombocytopenic purpura and atypical hemolytic uremic syndrome successfully treated with eculizumab.Factors influencing treatment of atypical hemolytic uremic syndrome.ADAMTS13 missense variants associated with defective activity and secretion of ADAMTS13 in a patient with non-cirrhotic portal hypertension.Targeted exome sequencing in anti-factor H antibody negative HUS reveals multiple variations.The role of von Willebrand factor in thrombotic microangiopathy.Thrombocytopenia in the ICU: disseminated intravascular coagulation and thrombotic microangiopathies-what intensivists need to know.Thrombotic thrombocytopenic purpura Gemcitabine-induced haemolytic uremic syndrome, although infrequent, can it be prevented: A case report and review of literature TTP-like syndrome: novel concept and molecular pathogenesis of endotheliopathy-associated vascular microthrombotic disease

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P2860

Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

http://www.wikidata.org/entity/Q30543370

description

2013 nî lūn-bûn

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2013 թուականի Յուլիսին հրատարակուած գիտական յօդուած

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2013 թվականի հուլիսին հրատարակված գիտական հոդված

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2013年の論文

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2013年論文

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2013年論文

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2013年論文

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2013年論文

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2013年論文

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2013年论文

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name

Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

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Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

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type

label

Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

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Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

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Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

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Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

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Partial ADAMTS13 deficiency in atypical hemolytic uremic syndrome.

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P2093

Carla M Nester

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Michael H Kroll

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Richard J Smith

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Shuju Feng

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Stephen J Eyler

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Tara Maga

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Vahid Afshar-Kharghan

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Yuzhou Zhang

http://www.w3.org/2001/XMLSchema#string

P2860

Atypical hemolytic uremic syndrome

Mutations and common polymorphisms in ADAMTS13 gene responsible for von Willebrand factor-cleaving protease activity

von Willebrand factor cleaving protease (ADAMTS13) is deficient in recurrent and familial thrombotic thrombocytopenic purpura and hemolytic uremic syndrome.

Severe deficiency of the specific von Willebrand factor-cleaving protease (ADAMTS 13) activity in a subgroup of children with atypical hemolytic uremic syndrome.

Measurement of von Willebrand factor-cleaving protease (ADAMTS-13) activity in plasma: a multicenter comparison of different assay methods.

Mild to moderate reduction of a von Willebrand factor cleaving protease (ADAMTS-13) in pregnant women with HELLP microangiopathic syndrome.

Evaluation of ADAMTS-13 activity in plasma using recombinant von Willebrand Factor A2 domain polypeptide as substrate.

Measurement of von Willebrand factor cleaving protease (ADAMTS-13): results of an international collaborative study involving 11 methods testing the same set of coded plasmas.

Complement factor H mutation in familial thrombotic thrombocytopenic purpura with ADAMTS13 deficiency and renal involvement.

FRETS-VWF73, a first fluorogenic substrate for ADAMTS13 assay.

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1487-1493

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10.1182/BLOOD-2013-03-492421

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