Accumulation of protein-bound epidermal glucosylceramides in beta-glucocerebrosidase deficient type 2 Gaucher mice.
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The epidermal barrier function is dependent on the serine protease CAP1/Prss8The role of epidermal sphingolipids in dermatologic diseasesABCA12 maintains the epidermal lipid permeability barrier by facilitating formation of ceramide linoleic estersMice with targeted disruption of the fatty acid transport protein 4 (Fatp 4, Slc27a4) gene show features of lethal restrictive dermopathyA new covalently bound ceramide from human stratum corneum -omega-hydroxyacylphytosphingosine.The glycosphingolipidoses-from disease to basic principles of metabolism.The organizing potential of sphingolipids in intracellular membrane transport.Epithelial barrier function: assembly and structural features of the cornified cell envelope.Biosynthesis and degradation of mammalian glycosphingolipids.Sphingolipid and glycosphingolipid metabolic pathways in the era of sphingolipidomics.A novel function for transglutaminase 1: attachment of long-chain omega-hydroxyceramides to involucrin by ester bond formationEpidermal sphingolipids: metabolism, function, and roles in skin disorders.Glycosphingolipids--nature, function, and pharmacological modulation.Very long chain sphingolipids: tissue expression, function and synthesis.Animal models for Gaucher disease research.Gaucher disease paradigm: from ERAD to comorbidity.The stratum corneum: the rampart of the mammalian body.Formation and functions of the corneocyte lipid envelope (CLE).Dissecting the formation, structure and barrier function of the stratum corneum.Permeability Barrier and Microstructure of Skin Lipid Membrane Models of Impaired Glucosylceramide Processing.Sphingolipid metabolism during epidermal barrier development in mice.Carbohydrate expression and modification during keratinocyte differentiation in normal human and reconstructed epidermis.Site-specific cleavage--a model system for the identification of lipid-modified glutamate residues in proteins.Postnatal requirement of the epithelial sodium channel for maintenance of epidermal barrier function.Abnormal Sphingolipid World in Inflammation Specific for Lysosomal Storage Diseases and Skin Disorders.Integrity and barrier function of the epidermis critically depend on glucosylceramide synthesis.
P2860
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P2860
Accumulation of protein-bound epidermal glucosylceramides in beta-glucocerebrosidase deficient type 2 Gaucher mice.
description
1999 nî lūn-bûn
@nan
1999 թուականի Մարտին հրատարակուած գիտական յօդուած
@hyw
1999 թվականի մարտին հրատարակված գիտական հոդված
@hy
1999年の論文
@ja
1999年論文
@yue
1999年論文
@zh-hant
1999年論文
@zh-hk
1999年論文
@zh-mo
1999年論文
@zh-tw
1999年论文
@wuu
name
Accumulation of protein-bound ...... deficient type 2 Gaucher mice.
@ast
Accumulation of protein-bound ...... deficient type 2 Gaucher mice.
@en
type
label
Accumulation of protein-bound ...... deficient type 2 Gaucher mice.
@ast
Accumulation of protein-bound ...... deficient type 2 Gaucher mice.
@en
prefLabel
Accumulation of protein-bound ...... deficient type 2 Gaucher mice.
@ast
Accumulation of protein-bound ...... deficient type 2 Gaucher mice.
@en
P2860
P1433
P1476
Accumulation of protein-bound ...... deficient type 2 Gaucher mice
@en
P2093
P2860
P304
P356
10.1016/S0014-5793(99)00274-4
P407
P577
1999-03-01T00:00:00Z