Physiological substrates for human lysosomal beta -hexosaminidase S.
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Human neutrophils secrete bioactive paucimannosidic proteins from azurophilic granules into pathogen-infected sputumCrystal structure of human beta-hexosaminidase B: understanding the molecular basis of Sandhoff and Tay-Sachs diseaseCrystallographic structure of human beta-hexosaminidase A: interpretation of Tay-Sachs mutations and loss of GM2 ganglioside hydrolysisNovel transmembrane receptor involved in phagosome transport of lysozymes and β-hexosaminidase in the enteric protozoan Entamoeba histolyticaMolecular and biochemical characterization of a novel β-N-acetyl-D-hexosaminidase with broad substrate-spectrum from the Aisan corn borer, Ostrinia furnacalis.Crystal structure of β-hexosaminidase B in complex with pyrimethamine, a potential pharmacological chaperoneBiosynthesis and degradation of mammalian glycosphingolipids.Ganglioside biochemistryA Second β-Hexosaminidase Encoded in the Streptococcus pneumoniae Genome Provides an Expanded Biochemical Ability to Degrade Host Glycans.Production of recombinant beta-hexosaminidase A, a potential enzyme for replacement therapy for Tay-Sachs and Sandhoff diseases, in the methylotrophic yeast Ogataea minutaGene expression and activity of cartilage degrading glycosidases in human rheumatoid arthritis and osteoarthritis synovial fibroblasts.My journey into the world of sphingolipids and sphingolipidoses.Enzymatic properties and subtle differences in the substrate specificity of phylogenetically distinct invertebrate N-glycan processing hexosaminidases.Membrane lipids regulate ganglioside GM2 catabolism and GM2 activator protein activityAbsence of metabolic cross-correction in Tay-Sachs cells: implications for gene therapy.Acid sphingomyelinase activity is regulated by membrane lipids and facilitates cholesterol transfer by NPC2.A novel role of the Batten disease gene CLN3: association with BMP synthesis.Kidney sulfatides in mouse models of inherited glycosphingolipid disorders: determination by nano-electrospray ionization tandem mass spectrometry.Reversion of the biochemical defects in murine embryonic Sandhoff neurons using a bicistronic lentiviral vector encoding hexosaminidase alpha and beta.Defective platelet beta-N-acetyl hexosaminidase content and release in chronic myeloproliferative disorders.Reduced rates of axonal and dendritic growth in embryonic hippocampal neurones cultured from a mouse model of Sandhoff disease.β-hexosaminidase from Xenopus laevis eggs and oocytes: from gene to immunochemical characterization.
P2860
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P2860
Physiological substrates for human lysosomal beta -hexosaminidase S.
description
2001 nî lūn-bûn
@nan
2001 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2001 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2001年の論文
@ja
2001年論文
@yue
2001年論文
@zh-hant
2001年論文
@zh-hk
2001年論文
@zh-mo
2001年論文
@zh-tw
2001年论文
@wuu
name
Physiological substrates for human lysosomal beta -hexosaminidase S.
@ast
Physiological substrates for human lysosomal beta -hexosaminidase S.
@en
type
label
Physiological substrates for human lysosomal beta -hexosaminidase S.
@ast
Physiological substrates for human lysosomal beta -hexosaminidase S.
@en
prefLabel
Physiological substrates for human lysosomal beta -hexosaminidase S.
@ast
Physiological substrates for human lysosomal beta -hexosaminidase S.
@en
P2093
P2860
P356
P1476
Physiological substrates for human lysosomal beta -hexosaminidase S.
@en
P2093
Konrad Sandhoff
Melanie Kolzer
Richard L Proia
Roger Sandhoff
Stefan T Hepbildikler
P2860
P304
P356
10.1074/JBC.M105457200
P407
P577
2001-11-13T00:00:00Z