Corrective effect on Fabry mice of yeast recombinant human alpha-galactosidase with N-linked sugar chains suitable for lysosomal delivery.
about
Structural Analysis of Saccharomyces cerevisiae -Galactosidase and Its Complexes with Natural Substrates Reveals New Insights into Substrate Specificity of GH27 GlycosidasesCrystallization and preliminary X-ray diffraction data of alpha-galactosidase from Saccharomyces cerevisiae.Carboxyl-terminal truncations alter the activity of the human α-galactosidase AEfficient uptake of recombinant α-galactosidase A produced with a gene-manipulated yeast by Fabry mice kidneysProduction of recombinant beta-hexosaminidase A, a potential enzyme for replacement therapy for Tay-Sachs and Sandhoff diseases, in the methylotrophic yeast Ogataea minutaUse of a modified alpha-N-acetylgalactosaminidase in the development of enzyme replacement therapy for Fabry disease.Lucerastat, an Iminosugar for Substrate Reduction Therapy: Tolerability, Pharmacodynamics, and Pharmacokinetics in Patients With Fabry Disease on Enzyme Replacement.Valuation of agro-industrial wastes as substrates for heterologous production of α-galactosidaseGlucosylceramide synthase inhibition with lucerastat lowers globotriaosylceramide and lysosome staining in cultured fibroblasts from Fabry patients with different mutation types
P2860
Q27662908-C51294BD-C180-4DA3-930F-AF779CB52511Q33522544-044EC233-DAB1-446B-857B-FD529800AEC8Q35125851-C1440A42-912F-4AE1-97E6-74DAEA9711B8Q35719001-388C028A-CAC8-4083-86EB-8DD5BDC32809Q35946763-69D85D50-6F17-41A6-8356-3678B3A63872Q37417886-8B119B88-BE21-4CA9-A35E-B61A6B38408DQ51842157-AB0E4687-22B4-4741-AAAD-0CDD483C40A1Q58768211-D161ACF2-6641-4FF2-86F2-E85798FADC14Q58794894-E67B32F6-F439-4E63-A977-2F37FEE0F9E0
P2860
Corrective effect on Fabry mice of yeast recombinant human alpha-galactosidase with N-linked sugar chains suitable for lysosomal delivery.
description
2006 nî lūn-bûn
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2006 թուականի Մարտին հրատարակուած գիտական յօդուած
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2006 թվականի մարտին հրատարակված գիտական հոդված
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2006年の論文
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2006年学术文章
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2006年学术文章
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2006年学术文章
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2006年学术文章
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2006年學術文章
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name
Corrective effect on Fabry mic ...... itable for lysosomal delivery.
@ast
Corrective effect on Fabry mic ...... itable for lysosomal delivery.
@en
type
label
Corrective effect on Fabry mic ...... itable for lysosomal delivery.
@ast
Corrective effect on Fabry mic ...... itable for lysosomal delivery.
@en
prefLabel
Corrective effect on Fabry mic ...... itable for lysosomal delivery.
@ast
Corrective effect on Fabry mic ...... itable for lysosomal delivery.
@en
P2093
P1476
Corrective effect on Fabry mic ...... itable for lysosomal delivery.
@en
P2093
Hiroshi Takahashi
Hitoshi Sakuraba
Ikuo Kawashima
Kumiko Ishii
Mai Ohsawa
Masaharu Kotani
Takashi Shimada
Tamotsu Kanzaki
Tomoko Fukushige
Toshihide Kobayashi
P2888
P304
P356
10.1007/S10038-006-0369-6
P577
2006-03-11T00:00:00Z