Clinical and molecular predictors of thrombocytopenia and risk of bleeding in patients with von Willebrand disease type 2B: a cohort study of 67 patients.
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Human von Willebrand factor/factor VIII concentrates in the management of pediatric patients with von Willebrand disease/hemophilia ALinkage between the mechanisms of thrombocytopenia and thrombopoiesisPhenotyping bleedingvon Willebrand disease: clinical and laboratory lessons learned from the large von Willebrand disease studiesThe molecular characterization of von Willebrand disease: good in partsTerminal platelet production is regulated by von Willebrand factorPlatelet adhesion involves a novel interaction between vimentin and von Willebrand factor under high shear stressLIM kinase/cofilin dysregulation promotes macrothrombocytopenia in severe von Willebrand disease-type 2B.Reduced survival of type 2B von Willebrand factor, irrespective of large multimer representation or thrombocytopeniaPlatelet reactive conformation and multimeric pattern of von Willebrand factor in acquired thrombotic thrombocytopenic purpura during acute disease and remission.Inherited platelet disorders: a clinical approach to diagnosis and management.Pregnancy in type 2B VWD: a case series.von Willebrand factor mutation promotes thrombocytopathy by inhibiting integrin αIIbβ3.Misfolding of vWF to pathologically disordered conformations impacts the severity of von Willebrand diseaseDiagnosis and treatment of inherited thrombocytopenias.Higher and lower active circulating VWF levels: different facets of von Willebrand disease.Apoptotic Platelet Events Are Not Observed in Severe von Willebrand Disease-Type 2B Mutation p.V1316M.Differential diagnosis of neonatal alloimmune thrombocytopenia: Type 2B von Willebrand disease.Diagnosis of inherited platelet disorders on a blood smear: a tool to facilitate worldwide diagnosis of platelet disorders.Type 2B von Willebrand disease with or without large multimers: A distinction of the two sides of the disorder is long overdueDiagnosis and Treatment of von Willebrand Disease and Rare Bleeding DisordersDestabilization of the A1 domain in von Willebrand factor dissociates the A1A2A3 tri-domain and provokes spontaneous binding to glycoprotein Ibalpha and platelet activation under shear stressImpact of sex, age, race, ethnicity and aspirin use on bleeding symptoms in healthy adults.Gain-of-function GPIb ELISA assay for VWF activity in the Zimmerman Program for the Molecular and Clinical Biology of VWD.The diagnosis and management of von Willebrand disease: a United Kingdom Haemophilia Centre Doctors Organization guideline approved by the British Committee for Standards in Haematology.Diagnostic approach to von Willebrand diseaseVariable content of von Willebrand factor mutant monomer drives the phenotypic variability in a family with von Willebrand diseaseN-terminal flanking region of A1 domain in von Willebrand factor stabilizes structure of A1A2A3 complex and modulates platelet activation under shear stress.New insights into genotype and phenotype of VWD.Differential surface activation of the A1 domain of von Willebrand factor.Principles of care for the diagnosis and treatment of von Willebrand disease.Rapid discrimination of the phenotypic variants of von Willebrand disease.A genetically-engineered von Willebrand disease type 2B mouse model displays defects in hemostasis and inflammation.Von Willebrand Factor Abnormalities Studied in the Mouse Model: What We Learned about VWF Functions.Changes of von Willebrand Factor during Pregnancy in Women with and without von Willebrand Disease.The molecular genetics of von Willebrand diseaseVon Willebrand disease in the United States: a perspective from Wisconsin.Changes in thermodynamic stability of von Willebrand factor differentially affect the force-dependent binding to platelet GPIbalpha.Platelet clearance via shear-induced unfolding of a membrane mechanoreceptor.Translational medicine advances in von Willebrand disease.
P2860
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P2860
Clinical and molecular predictors of thrombocytopenia and risk of bleeding in patients with von Willebrand disease type 2B: a cohort study of 67 patients.
description
2008 nî lūn-bûn
@nan
2008 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
name
Clinical and molecular predict ...... a cohort study of 67 patients.
@ast
Clinical and molecular predict ...... a cohort study of 67 patients.
@en
type
label
Clinical and molecular predict ...... a cohort study of 67 patients.
@ast
Clinical and molecular predict ...... a cohort study of 67 patients.
@en
prefLabel
Clinical and molecular predict ...... a cohort study of 67 patients.
@ast
Clinical and molecular predict ...... a cohort study of 67 patients.
@en
P2093
P50
P1433
P1476
Clinical and molecular predict ...... a cohort study of 67 patients.
@en
P2093
Augusto B Federici
Giancarlo Castaman
Luciano Baronciani
Maria T Canciani
Philip G De Groot
P304
P356
10.1182/BLOOD-2008-04-152280
P407
P577
2008-09-19T00:00:00Z