Unusually large plasma factor VIII:von Willebrand factor multimers in chronic relapsing thrombotic thrombocytopenic purpura.
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Structure of von Willebrand factor-cleaving protease (ADAMTS13), a metalloprotease involved in thrombotic thrombocytopenic purpuraADAMTS-13 metalloprotease interacts with the endothelial cell-derived ultra-large von Willebrand factorAntibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpuraVon Willebrand factor, ADAMTS13, and thrombotic thrombocytopenic purpuraCurrent concepts in thrombotic thrombocytopenic purpuraPathogenesis of thrombotic microangiopathiesADAM and ADAMTS Family Proteins and Snake Venom Metalloproteinases: A Structural OverviewProteolytic processing of von Willebrand factor by adamts13 and leukocyte proteasesAnimal models for thrombotic thrombocytopenic purpuraThe unfolded von Willebrand factor response in bloodstream: the self-association perspectiveCalcium modulates force sensing by the von Willebrand factor A2 domainADAMTS13 and von Willebrand factor in thrombotic thrombocytopenic purpuraLateral clustering of platelet GP Ib-IX complexes leads to up-regulation of the adhesive function of integrin alpha IIbbeta 3Increased ADAMTS-13 proteolytic activity in rat hepatic stellate cells upon activation in vitro and in vivoIdentification of strain-specific variants of mouse Adamts13 gene encoding von Willebrand factor-cleaving proteaseShigatoxin triggers thrombotic thrombocytopenic purpura in genetically susceptible ADAMTS13-deficient mice.Size regulation of von Willebrand factor-mediated platelet thrombi by ADAMTS13 in flowing bloodN-acetylcysteine reduces the size and activity of von Willebrand factor in human plasma and miceThe rate of hemolysis in sickle cell disease correlates with the quantity of active von Willebrand factor in the plasma.In vitro microvessels for the study of angiogenesis and thrombosis.Cocaine and specific cocaine metabolites induce von Willebrand factor release from endothelial cells in a tissue-specific manner.Single particle tracking of ADAMTS13 (a disintegrin and metalloprotease with thrombospondin type-1 repeats) molecules on endothelial von Willebrand factor stringsPernicious Anemia Associated Cobalamin Deficiency and Thrombotic Microangiopathy: Case Report and Review of the LiteratureSolvent/detergent fresh frozen plasma as primary treatment of acute thrombotic thrombocytopenic purpura.Thrombotic thrombocytopenic purpura today.Antibody inhibitors to von Willebrand factor metalloproteinase and increased binding of von Willebrand factor to platelets in ticlopidine-associated thrombotic thrombocytopenic purpura.Management of thrombotic thrombocytopenic purpura.In vitro bleeding time test can diagnose thrombotic thrombocytopenia purpura and can possibly monitor therapeutic plasma apheresis.Impact of thrombotic thrombocytopenic purpura on leukemic children undergoing bone marrow transplantation.Design of the prospective randomized study for the treatment of patients with thrombotic microangiopathy. PRODROMI Study Group.Elevated endothelial microparticles in thrombotic thrombocytopenic purpura: findings from brain and renal microvascular cell culture and patients with active disease.Ten years of prophylactic treatment with fresh-frozen plasma in a child with chronic relapsing thrombotic thrombocytopenic purpura as a result of a congenital deficiency of von Willebrand factor-cleaving protease.Cryoprecipitate-reduced plasma:rationale for use and efficacy in the treatment of thrombotic thrombocytopenic purpura.Porcine hematopoietic cell xenotransplantation in nonhuman primates is complicated by thrombotic microangiopathy.Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura.New aspects in the pathogenesis and treatment of thrombotic thrombocytopenic purpura and hemolytic uremic syndrome.Consanguineous hemolytic uremic syndrome secondary to Escherichia coli O157:H7 infection treated with aggressive therapeutic plasma exchange.Plasma of patients with Upshaw-Schulman syndrome, a congenital deficiency of von Willebrand factor-cleaving protease activity, enhances the aggregation of normal platelets under high shear stress.von Willebrand factor-cleaving protease inhibitor in a patient with human immunodeficiency syndrome-associated thrombotic thrombocytopenic purpura.Thrombotic thrombocytopenic purpura and hemolytic uremic syndrome following allogeneic bone marrow transplantation.
P2860
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P2860
Unusually large plasma factor VIII:von Willebrand factor multimers in chronic relapsing thrombotic thrombocytopenic purpura.
description
1982 nî lūn-bûn
@nan
1982 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
1982 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
1982年の論文
@ja
1982年論文
@yue
1982年論文
@zh-hant
1982年論文
@zh-hk
1982年論文
@zh-mo
1982年論文
@zh-tw
1982年论文
@wuu
name
Unusually large plasma factor ...... otic thrombocytopenic purpura.
@ast
Unusually large plasma factor ...... otic thrombocytopenic purpura.
@en
type
label
Unusually large plasma factor ...... otic thrombocytopenic purpura.
@ast
Unusually large plasma factor ...... otic thrombocytopenic purpura.
@en
prefLabel
Unusually large plasma factor ...... otic thrombocytopenic purpura.
@ast
Unusually large plasma factor ...... otic thrombocytopenic purpura.
@en
P2093
P1476
Unusually large plasma factor ...... otic thrombocytopenic purpura.
@en
P2093
Colannino NM
Weinstein MJ
P304
P356
10.1056/NEJM198212023072306
P407
P577
1982-12-01T00:00:00Z