Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS.
about
Effects of ALS-related SOD1 mutants on dynein- and KIF5-mediated retrograde and anterograde axonal transportA Case for Microtubule Vulnerability in Amyotrophic Lateral Sclerosis: Altered Dynamics During DiseaseALS as a distal axonopathy: molecular mechanisms affecting neuromuscular junction stability in the presymptomatic stages of the diseaseAbnormal mitochondrial transport and morphology are common pathological denominators in SOD1 and TDP43 ALS mouse models.Abnormalities of Mitochondrial Dynamics in Neurodegenerative Diseases.Misfolded SOD1 associated with motor neuron mitochondria alters mitochondrial shape and distribution prior to clinical onset.ALS-linked mutant SOD1 damages mitochondria by promoting conformational changes in Bcl-2.Mitochondrial dysfunction and intracellular calcium dysregulation in ALSSOD1 targeted to the mitochondrial intermembrane space prevents motor neuropathy in the Sod1 knockout mouse.Wild-type human TDP-43 expression causes TDP-43 phosphorylation, mitochondrial aggregation, motor deficits, and early mortality in transgenic mice.Rodent models of TDP-43 proteinopathy: investigating the mechanisms of TDP-43-mediated neurodegenerationActivation of the endoplasmic reticulum stress response in skeletal muscle of G93A*SOD1 amyotrophic lateral sclerosis mice.Fluoxetine increases plasticity and modulates the proteomic profile in the adult mouse visual cortex.Early and gender-specific differences in spinal cord mitochondrial function and oxidative stress markers in a mouse model of ALSMitochondrial dynamic abnormalities in amyotrophic lateral sclerosis.Elimination Rate of Serum Lactate is Correlated with Amyotrophic Lateral Sclerosis Progression.Mitochondrial dysfunction in amyotrophic lateral sclerosis.SOD1 and TDP-43 animal models of amyotrophic lateral sclerosis: recent advances in understanding disease toward the development of clinical treatments.Mitochondrial dysfunction in familial amyotrophic lateral sclerosis.Misfolded SOD1 and ALS: zeroing in on mitochondria.Human TDP-43 and FUS selectively affect motor neuron maturation and survival in a murine cell model of ALS by non-cell-autonomous mechanisms.Defining peripheral nervous system dysfunction in the SOD-1G93A transgenic rat model of amyotrophic lateral sclerosis.S-nitrosylated protein disulfide isomerase contributes to mutant SOD1 aggregates in amyotrophic lateral sclerosis.Amyotrophic lateral sclerosis: a dying motor unit?Implications of white matter damage in amyotrophic lateral sclerosis (Review).An antibody-based affinity chromatography tool to assess Cu, Zn superoxide dismutase (SOD) G93A structural complexity in vivo.Energy metabolism in ALS: an underappreciated opportunity?
P2860
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P2860
Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS.
description
2009 nî lūn-bûn
@nan
2009 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2009 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
2009年の論文
@ja
2009年論文
@yue
2009年論文
@zh-hant
2009年論文
@zh-hk
2009年論文
@zh-mo
2009年論文
@zh-tw
2009年论文
@wuu
name
Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS.
@ast
Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS.
@en
type
label
Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS.
@ast
Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS.
@en
prefLabel
Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS.
@ast
Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS.
@en
P2093
P2860
P356
P1476
Axonal mitochondrial clusters containing mutant SOD1 in transgenic models of ALS
@en
P2093
Florencia Palacios
Joseph S Beckman
Luis Barbeito
Monica Marin
Paola Lepanto
Sofia Horjales
Victoria Elizondo
P2860
P304
P356
10.1089/ARS.2009.2614
P577
2009-07-01T00:00:00Z