Olfactory stem cells, a new cellular model for studying molecular mechanisms underlying familial dysautonomia
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DERP6 (ELP5) and C3ORF75 (ELP6) regulate tumorigenicity and migration of melanoma cells as subunits of ElongatorFamilial Dysautonomia (FD) Human Embryonic Stem Cell Derived PNS Neurons Reveal that Synaptic Vesicular and Neuronal Transport Genes Are Directly or Indirectly Affected by IKBKAP DownregulationIKAP/Elp1 is required in vivo for neurogenesis and neuronal survival, but not for neural crest migration.Kinetin inhibits apoptosis of aging spleen cells induced by D-galactose in rats.Concise review: Patient-derived olfactory stem cells: new models for brain diseases.Translational potential of olfactory mucosa for the study of neuropsychiatric illness.Specific correction of a splice defect in brain by nutritional supplementation.Kinetin improves IKBKAP mRNA splicing in patients with familial dysautonomiaIKAP expression levels modulate disease severity in a mouse model of familial dysautonomia.Patient-derived stem cells: pathways to drug discovery for brain diseases.Olfactory stem cells reveal MOCOS as a new player in autism spectrum disorders.Familial Dysautonomia: Mechanisms and ModelsRole of mesenchymal stem cells in cell life and their signaling.Cardiac glycosides correct aberrant splicing of IKBKAP-encoded mRNA in familial dysautonomia derived cells by suppressing expression of SRSF3.Isolating nasal olfactory stem cells from rodents or humans.Faulty RNA splicing: consequences and therapeutic opportunities in brain and muscle disorders.Animal and cellular models of familial dysautonomia.MicroRNA screening identifies a link between NOVA1 expression and a low level of IKAP in familial dysautonomia.Role of matrix metalloproteinases in migration and neurotrophic properties of nasal olfactory stem and ensheathing cells.Elongator complex is required for long-term olfactory memory formation in Drosophila.A Patient-Specific Stem Cell Model to Investigate the Neurological Phenotype Observed in Ataxia-Telangiectasia.Genome-wide analysis of familial dysautonomia and kinetin target genes with patient olfactory ecto-mesenchymal stem cells.Antisense oligonucleotides correct the familial dysautonomia splicing defect in IKBKAP transgenic mice.Patient-Derived Stem Cell Models in HSP: Disease Modelling and Drug DiscoveryNeurogenesis in the Adult Olfactory Epithelium
P2860
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P2860
Olfactory stem cells, a new cellular model for studying molecular mechanisms underlying familial dysautonomia
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2010 nî lūn-bûn
@nan
2010 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
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name
Olfactory stem cells, a new ce ...... derlying familial dysautonomia
@ast
Olfactory stem cells, a new ce ...... derlying familial dysautonomia
@en
type
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Olfactory stem cells, a new ce ...... derlying familial dysautonomia
@ast
Olfactory stem cells, a new ce ...... derlying familial dysautonomia
@en
prefLabel
Olfactory stem cells, a new ce ...... derlying familial dysautonomia
@ast
Olfactory stem cells, a new ce ...... derlying familial dysautonomia
@en
P2093
P2860
P1433
P1476
Olfactory stem cells, a new ce ...... derlying familial dysautonomia
@en
P2093
Aurélie Bergon
Béatrice Loriod
Catherine Nguyen
Christine Formisano-Tréziny
Felicia B Axelrod
François Féron
Jean Gabert
Michel Khrestchatisky
Nathalie Boone
Oualid Sbai
P2860
P304
P356
10.1371/JOURNAL.PONE.0015590
P407
P50
P577
2010-12-20T00:00:00Z