Peroxisome biogenesis and peroxisome biogenesis disorders.
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Phenotype-genotype relationships in peroxisome biogenesis disorders of PEX1-defective complementation group 1 are defined by Pex1p-Pex6p interactionMutations in the peroxin Pex26p responsible for peroxisome biogenesis disorders of complementation group 8 impair its stability, peroxisomal localization, and interaction with the Pex1p x Pex6p complexFunctional studies on human Pex7p: subcellular localization and interaction with proteins containing a peroxisome-targeting signal type 2 and other peroxinsIn vitro transport of membrane proteins to peroxisomes by shuttling receptor Pex19pRequirement for microtubules and dynein motors in the earliest stages of peroxisome biogenesisCharacterization of the interaction between recombinant human peroxin Pex3p and Pex19p: identification of TRP-104 IN Pex3p as a critical residue for the interactionThe membrane biogenesis peroxin Pex16p. Topogenesis and functional roles in peroxisomal membrane assemblyInteraction of a farnesylated protein with renal type IIa Na/Pi co-transporter in response to parathyroid hormone and dietary phosphateMutations in novel peroxin gene PEX26 that cause peroxisome-biogenesis disorders of complementation group 8 provide a genotype-phenotype correlationHsp70 regulates the interaction between the peroxisome targeting signal type 1 (PTS1)-receptor Pex5p and PTS1PEX3 is the causal gene responsible for peroxisome membrane assembly-defective Zellweger syndrome of complementation group G.Peroxisomal targeting signal receptor Pex5p interacts with cargoes and import machinery components in a spatiotemporally differentiated manner: conserved Pex5p WXXXF/Y motifs are critical for matrix protein import.Human pex19p binds peroxisomal integral membrane proteins at regions distinct from their sorting sequencesPeroxisome biogenesis in mammalian cellsYHR150w and YDR479c encode peroxisomal integral membrane proteins involved in the regulation of peroxisome number, size, and distribution in Saccharomyces cerevisiaePex15p of Saccharomyces cerevisiae provides a molecular basis for recruitment of the AAA peroxin Pex6p to peroxisomal membranesPex7p translocates in and out of peroxisomes in Saccharomyces cerevisiaePex11-related proteins in peroxisome dynamics: a role for the novel peroxin Pex27p in controlling peroxisome size and number in Saccharomyces cerevisiae.Pex19p dampens the p19ARF-p53-p21WAF1 tumor suppressor pathwayMolecular mechanism of a temperature-sensitive phenotype in peroxisomal biogenesis disorderDomain architecture and activity of human Pex19p, a chaperone-like protein for intracellular trafficking of peroxisomal membrane proteinsIdentification of a substrate-binding site in a peroxisomal beta-oxidation enzyme by photoaffinity labeling with a novel palmitoyl derivativeYarrowia lipolytica cells mutant for the PEX24 gene encoding a peroxisomal membrane peroxin mislocalize peroxisomal proteins and accumulate membrane structures containing both peroxisomal matrix and membrane proteins.Yarrowia lipolytica cells mutant for the peroxisomal peroxin Pex19p contain structures resembling wild-type peroxisomesShuttling mechanism of peroxisome targeting signal type 1 receptor Pex5: ATP-independent import and ATP-dependent export.The life cycle of the peroxisome.The membrane peroxin PEX3 induces peroxisome-ubiquitination-linked pexophagy.Pexophagy: the selective degradation of peroxisomesShuttles and cycles: transport of proteins into the peroxisome matrix (review).Identification and characterization of the peroxin 1 gene MoPEX1 required for infection-related morphogenesis and pathogenicity in Magnaporthe oryzae.Peroxisome biogenesis and human peroxisome-deficiency disorders.AAA peroxins and their recruiter Pex26p modulate the interactions of peroxins involved in peroxisomal protein import.Defective lipid remodeling of GPI anchors in peroxisomal disorders, Zellweger syndrome, and rhizomelic chondrodysplasia punctata.Interactions of Pex7p and Pex18p/Pex21p with the peroxisomal docking machinery: implications for the first steps in PTS2 protein import.Intracellular localization, function, and dysfunction of the peroxisome-targeting signal type 2 receptor, Pex7p, in mammalian cells.Domain mapping of human PEX5 reveals functional and structural similarities to Saccharomyces cerevisiae Pex18p and Pex21p.Identification of a cysteine residue important for the ATPase activity of C. elegans fidgetin homologue.Arabidopsis ABERRANT PEROXISOME MORPHOLOGY9 is a peroxin that recruits the PEX1-PEX6 complex to peroxisomes.RNA interference of peroxisome-related genes in C. elegans: a new model for human peroxisomal disorders.Hydrophobic regions adjacent to transmembrane domains 1 and 5 are important for the targeting of the 70-kDa peroxisomal membrane protein.
P2860
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P2860
Peroxisome biogenesis and peroxisome biogenesis disorders.
description
2000 nî lūn-bûn
@nan
2000 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2000 թվականի հունիսին հրատարակված գիտական հոդված
@hy
2000年の論文
@ja
2000年学术文章
@wuu
2000年学术文章
@zh-cn
2000年学术文章
@zh-hans
2000年学术文章
@zh-my
2000年学术文章
@zh-sg
2000年學術文章
@yue
name
Peroxisome biogenesis and peroxisome biogenesis disorders.
@ast
Peroxisome biogenesis and peroxisome biogenesis disorders.
@en
type
label
Peroxisome biogenesis and peroxisome biogenesis disorders.
@ast
Peroxisome biogenesis and peroxisome biogenesis disorders.
@en
prefLabel
Peroxisome biogenesis and peroxisome biogenesis disorders.
@ast
Peroxisome biogenesis and peroxisome biogenesis disorders.
@en
P2860
P1433
P1476
Peroxisome biogenesis and peroxisome biogenesis disorders.
@en
P2093
P2860
P356
10.1016/S0014-5793(00)01667-7
P407
P577
2000-06-01T00:00:00Z