Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties.
about
Distinct origins of dura mater graft-associated Creutzfeldt-Jakob disease: past and future problemsEvidence that bank vole PrP is a universal acceptor for prionsSmall ruminant nor98 prions share biochemical features with human gerstmann-sträussler-scheinker disease and variably protease-sensitive prionopathyAnalysis of Conformational Stability of Abnormal Prion Protein Aggregates across the Spectrum of Creutzfeldt-Jakob Disease PrionsHuman prion diseases in the Netherlands (1998-2009): clinical, genetic and molecular aspects.Prionic diseases.Detection of prion seeding activity in the olfactory mucosa of patients with Fatal Familial InsomniaTypes and Strains: Their Essential Role in Understanding Protein Aggregation in Neurodegenerative Diseases.Mouse models for studying the formation and propagation of prions.Protease-sensitive conformers in broad spectrum of distinct PrPSc structures in sporadic Creutzfeldt-Jakob disease are indicator of progression rate.Strain specific resistance to murine scrapie associated with a naturally occurring human prion protein polymorphism at residue 171.Small protease sensitive oligomers of PrPSc in distinct human prions determine conversion rate of PrP(C).Variant CJD. 18 years of research and surveillance.Review: contribution of transgenic models to understanding human prion disease.Increased susceptibility of human-PrP transgenic mice to bovine spongiform encephalopathy infection following passage in sheep.Comparative Study of Prions in Iatrogenic and Sporadic Creutzfeldt-Jakob Disease.Variably protease-sensitive prionopathy, a unique prion variant with inefficient transmission properties.Molecular biology and pathology of prion strains in sporadic human prion diseases.Characteristic CSF prion seeding efficiency in humans with prion diseasesIn vivo comparison of chronic wasting disease infectivity from deer with variation at prion protein residue 96.Structural determinants of phenotypic diversity and replication rate of human prions.Transmission properties of atypical Creutzfeldt-Jakob disease: a clue to disease etiology?The glycosylation status of PrPC is a key factor in determining transmissible spongiform encephalopathy transmission between speciesDistinct pathological phenotypes of Creutzfeldt-Jakob disease in recipients of prion-contaminated growth hormone.The Distribution of Prion Protein Allotypes Differs Between Sporadic and Iatrogenic Creutzfeldt-Jakob Disease PatientsSensitive and specific detection of sporadic Creutzfeldt-Jakob disease brain prion protein using real-time quaking-induced conversion.Molecular pathogenesis of sporadic prion diseases in man.Identification of I137M and other mutations that modulate incubation periods for two human prion strains.Iatrogenic CJD due to pituitary-derived growth hormone with genetically determined incubation times of up to 40 years.The prion protein preference of sporadic Creutzfeldt-Jakob disease subtypes.Modulation of Creutzfeldt-Jakob disease prion propagation by the A224V mutationEmergence of two prion subtypes in ovine PrP transgenic mice infected with human MM2-cortical Creutzfeldt-Jakob disease prions.Sporadic Creutzfeldt-Jakob disease subtype-specific alterations of the brain proteome: impact on Rab3a recyclingPost-translational changes to PrP alter transmissible spongiform encephalopathy strain properties.Consensus classification of human prion disease histotypes allows reliable identification of molecular subtypes: an inter-rater study among surveillance centres in Europe and USARevisiting the Heidenhain Variant of Creutzfeldt-Jakob Disease: Evidence for Prion Type Variability Influencing Clinical Course and Laboratory FindingsLack of prion infectivity in fixed heart tissue from patients with Creutzfeldt-Jakob disease or amyloid heart disease.Prions: Beyond a Single Protein.Analyses of protease resistance and aggregation state of abnormal prion protein across the spectrum of human prionsCo-existence of distinct prion types enables conformational evolution of human PrPSc by competitive selection
P2860
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P2860
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties.
description
2010 nî lūn-bûn
@nan
2010 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի հունիսին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties.
@ast
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties.
@en
type
label
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties.
@ast
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties.
@en
prefLabel
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties.
@ast
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties.
@en
P2093
P2860
P356
P1476
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties.
@en
P2093
Jean C Manson
Matthew T Bishop
Robert G Will
P2860
P304
12005-12010
P356
10.1073/PNAS.1004688107
P407
P577
2010-06-14T00:00:00Z