Homeostatic expansion of autoreactive immunoglobulin-secreting cells in the Rag2 mouse model of Omenn syndrome - Wikidata - awgldk - TriplyDB

Homeostatic expansion of autoreactive immunoglobulin-secreting cells in the Rag2 mouse model of Omenn syndrome

Homeostatic expansion of autoreactive immunoglobulin-secreting cells in the Rag2 mouse model of Omenn syndrome

http://www.wikidata.org/entity/Q33979830

about

The pre-B cell receptor; selecting for or against autoreactivity Human RAG mutations: biochemistry and clinical implications Rag defects and thymic stroma: lessons from animal models.Expansion of immunoglobulin-secreting cells and defects in B cell tolerance in Rag-dependent immunodeficiency.Transient lymphopenia breaks costimulatory blockade-based peripheral tolerance and initiates cardiac allograft rejection B-cell development and functions and therapeutic options in adenosine deaminase-deficient patients.Intestinal microbiota sustains inflammation and autoimmunity induced by hypomorphic RAG defects.Defective B cell tolerance in adenosine deaminase deficiency is corrected by gene therapy Epigenetic Regulation of Antibody Responses by the Histone H2A Deubiquitinase MYSM1 Autoimmunity in wiskott-Aldrich syndrome: an unsolved enigma.Alterations in the adenosine metabolism and CD39/CD73 adenosinergic machinery cause loss of Treg cell function and autoimmunity in ADA-deficient SCID Broad-spectrum antibodies against self-antigens and cytokines in RAG deficiency Correction of murine Rag2 severe combined immunodeficiency by lentiviral gene therapy using a codon-optimized RAG2 therapeutic transgene.Omenn syndrome associated with a functional reversion due to a somatic second-site mutation in CARD11 deficiency.γδ T Cells Shape Preimmune Peripheral B Cell Populations Genetic regulation of immunoglobulin E level in different pathological states: integration of mouse and human genetics.Hypomorphic mutation in the RAG2 gene affects dendritic cell distribution and migration.Characterization of T and B cell repertoire diversity in patients with RAG deficiency BLyS levels correlate with vaccine-induced antibody titers in patients with glioblastoma lymphodepleted by therapeutic temozolomide.Anti-CD3ε mAb improves thymic architecture and prevents autoimmune manifestations in a mouse model of Omenn syndrome: therapeutic implications.Clonal and constricted T cell repertoire in Common Variable Immune Deficiency.RAGs and BUGS: An alliance for autoimmunity.Pathogenesis of autoimmunity in common variable immunodeficiency.Efficacy of lentiviral mediated gene therapy in an Omenn syndrome Rag2 mouse model is not hindered by inflammation and immune dysregulation.Omenn Syndrome: inflammation and autoimmunity.Spontaneous T Cell Proliferation: A Physiologic Process to Create and Maintain Homeostatic Balance and Diversity of the Immune System.Hypomorphic Rag1 mutations alter the pre-immune repertoire at early stages of lymphoid development.

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P2860

Homeostatic expansion of autoreactive immunoglobulin-secreting cells in the Rag2 mouse model of Omenn syndrome

http://www.wikidata.org/entity/Q33979830

description

2010 nî lūn-bûn

@nan

2010 թուականի Յունիսին հրատարակուած գիտական յօդուած

@hyw

2010 թվականի հունիսին հրատարակված գիտական հոդված

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2010年の論文

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2010年論文

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2010年論文

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2010年論文

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2010年論文

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2010年論文

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2010年论文

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name

Homeostatic expansion of autor ...... mouse model of Omenn syndrome

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Homeostatic expansion of autor ...... mouse model of Omenn syndrome

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type

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Homeostatic expansion of autor ...... mouse model of Omenn syndrome

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Homeostatic expansion of autor ...... mouse model of Omenn syndrome

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Homeostatic expansion of autor ...... mouse model of Omenn syndrome

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Homeostatic expansion of autor ...... mouse model of Omenn syndrome

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P1433

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P1433

Journal of Experimental Medicine

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Homeostatic expansion of autor ...... mouse model of Omenn syndrome

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P2093

Aisha V Sauer

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Alberto Martini

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Antonius G Rolink

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Dario Strina

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Elisabetta Traggiai

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Hedda Wardemann

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Maria Ravanini

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Mirjam van der Burg

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Paolo Vezzoni

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Stephan Regenass

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P2860

Plasma cell differentiation requires the transcription factor XBP-1

Partial V(D)J recombination activity leads to Omenn syndrome

The costimulatory molecule ICOS regulates the expression of c-Maf and IL-21 in the development of follicular T helper cells and TH-17 cells

Commitment of B lymphocytes to a plasma cell fate is associated with Blimp-1 expression in vivo

Involvement of inducible costimulator-B7 homologous protein costimulatory pathway in murine lupus nephritis

Blimp-1 orchestrates plasma cell differentiation by extinguishing the mature B cell gene expression program

Bcl6 mediates the development of T follicular helper cells

The role of the BAFF/APRIL system on T cell function

T follicular helper cells express a distinctive transcriptional profile, reflecting their role as non-Th1/Th2 effector cells that provide help for B cells

Regulation and functions of Blimp-1 in T and B lymphocytes

P304

1525-1540

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scholarly article

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10.1084/JEM.20091928

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P433

7

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207

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Christian E Busse

Pietro Luigi Poliani

Fabio Facchetti

Barbara Cassani

Francesca Schena

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2010-06-14T00:00:00Z

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44673008

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20547828

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2901059

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