In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis.
about
Differential effects of Hsc70 and Hsp70 on the intracellular trafficking and functional expression of epithelial sodium channelsRescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus reportCorrection of chloride transport and mislocalization of CFTR protein by vardenafil in the gastrointestinal tract of cystic fibrosis miceLung infections associated with cystic fibrosis.Laser fluorescence bronchoscopy for detection of fluorescent reporter genes in airway epithelia.The CF-CIRC study: a French collaborative study to assess the accuracy of cystic fibrosis diagnosis in neonatal screening.In vitro prediction of stop-codon suppression by intravenous gentamicin in patients with cystic fibrosis: a pilot studyDifferential roles of NHERF1, NHERF2, and PDZK1 in regulating CFTR-mediated intestinal anion secretion in mice.Activation of the CFTR Cl- channel by trimethoxyflavone in vitro and in vivoInter-α-inhibitor blocks epithelial sodium channel activation and decreases nasal potential differences in ΔF508 mice.DeltaF508 CFTR processing correction and activity in polarized airway and non-airway cell monolayers.Current status of gene therapy for cystic fibrosis pulmonary disease.The K+ channel opener 1-EBIO potentiates residual function of mutant CFTR in rectal biopsies from cystic fibrosis patients.An international randomized multicenter comparison of nasal potential difference techniques.Intestinal current measurement versus nasal potential difference measurements for diagnosis of cystic fibrosis: a case-control study.CFTR regulates early pathogenesis of chronic obstructive lung disease in βENaC-overexpressing miceEstablishing a diagnosis of cystic fibrosis.Regulation of endogenous ENaC functional expression by CFTR and ΔF508-CFTR in airway epithelial cells.Towards the pharmacogenomics of cystic fibrosis.Nasal potential difference to detect Na+ channel dysfunction in acute lung injury.CFTR transcription defects in pancreatic sufficient cystic fibrosis patients with only one mutation in the coding region of CFTR.Optimizing nasal potential difference analysis for CFTR modulator development: assessment of ivacaftor in CF subjects with the G551D-CFTR mutation.Multicenter intestinal current measurements in rectal biopsies from CF and non-CF subjects to monitor CFTR function.Non-viral gene transfer therapy for cystic fibrosis.Nasal airway ion transport is linked to the cystic fibrosis phenotype in adult patients.Species-specific differences in mouse and human airway epithelial biology of recombinant adeno-associated virus transduction.Emerging drug treatments for cystic fibrosis.No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations.Cystic fibrosis transmembrane conductance regulator (CFTR) gene mutations in allergic bronchopulmonary aspergillosis.Chloride conductance and genetic background modulate the cystic fibrosis phenotype of Delta F508 homozygous twins and siblings.In vivo activation of the cystic fibrosis transmembrane conductance regulator mutant deltaF508 in murine nasal epitheliumCFTR is required for maximal transepithelial liquid transport in pig alveolar epithelia.Cystic fibrosis: terminology and diagnostic algorithmsTargeted therapy for cystic fibrosis: cystic fibrosis transmembrane conductance regulator mutation-specific pharmacologic strategies.Could a defective epithelial sodium channel lead to bronchiectasis.Detection of cystic fibrosis transmembrane conductance regulator activity in early-phase clinical trials.Gene therapy for the treatment of cystic fibrosis.Cystic fibrosis and estrogens: a perfect stormNasal potential difference measurements to assess CFTR ion channel activity.
P2860
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P2860
In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis.
description
1995 nî lūn-bûn
@nan
1995 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
1995 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
1995年の論文
@ja
1995年学术文章
@wuu
1995年学术文章
@zh-cn
1995年学术文章
@zh-hans
1995年学术文章
@zh-my
1995年学术文章
@zh-sg
1995年學術文章
@yue
name
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@ast
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@en
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@nl
type
label
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@ast
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@en
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@nl
prefLabel
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@ast
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@en
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@nl
P2093
P356
P1433
P1476
In vivo nasal potential differ ...... e transfer in cystic fibrosis.
@en
P2093
Boucher RC
Knowles MR
Paradiso AM
P304
P356
10.1089/HUM.1995.6.4-445
P577
1995-04-01T00:00:00Z