Cellular defenses against unfolded proteins: a cell biologist thinks about neurodegenerative diseases.
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Ubiquitin-proteasome system involvement in Huntington's diseaseAmyloid-mediated sequestration of essential proteins contributes to mutant huntingtin toxicity in yeastHook2 contributes to aggresome formationMuscle atrophy and motor neuron degeneration in human NEDL1 transgenic miceERp44, a novel endoplasmic reticulum folding assistant of the thioredoxin familyCoupling endoplasmic reticulum stress to the cell death program: role of the ER chaperone GRP78ASK1 is essential for endoplasmic reticulum stress-induced neuronal cell death triggered by expanded polyglutamine repeatsAberrant accumulation of EFEMP1 underlies drusen formation in Malattia Leventinese and age-related macular degenerationCystamine and cysteamine increase brain levels of BDNF in Huntington disease via HSJ1b and transglutaminase.Misfolded proteins partition between two distinct quality control compartmentsGene expression during ER stress-induced apoptosis in neurons: induction of the BH3-only protein Bbc3/PUMA and activation of the mitochondrial apoptosis pathwayMisfolding diverts CFTR from recycling to degradation: quality control at early endosomesThe molecular chaperone Hsp90 plays a role in the assembly and maintenance of the 26S proteasomeMisfolded CuZnSOD and amyotrophic lateral sclerosisNatural Phytochemicals in the Treatment and Prevention of Dementia: An OverviewThe P42 peptide and Peptide-based therapies for Huntington's diseaseDiametrical diseases reflect evolutionary-genetic tradeoffs: Evidence from psychiatry, neurology, rheumatology, oncology and immunologyTargeting heat shock proteins to modulate α-synuclein toxicityTargeting Hsp90/Hsp70-based protein quality control for treatment of adult onset neurodegenerative diseasesGraded Proteasome Dysfunction in Caenorhabditis elegans Activates an Adaptive Response Involving the Conserved SKN-1 and ELT-2 Transcription Factors and the Autophagy-Lysosome PathwayPostnatal proteasome inhibition induces neurodegeneration and cognitive deficiencies in adult mice: a new model of neurodevelopment syndromeThe polyglutamine-expanded androgen receptor responsible for spinal and bulbar muscular atrophy inhibits the APC/C(Cdh1) ubiquitin ligase complex.The 1.1-A resolution crystal structure of DJ-1, the protein mutated in autosomal recessive early onset Parkinson's diseaseCrystal structures of human DJ-1 and Escherichia coli Hsp31, which share an evolutionarily conserved domainStructural basis for the selection of glycosylated substrates by SCFFbs1 ubiquitin ligaseStructural Basis of E2-25K/UBB+1 Interaction Leading to Proteasome Inhibition and NeurotoxicityAn inducible chaperone adapts proteasome assembly to stress.HDAC6 controls major cell response pathways to cytotoxic accumulation of protein aggregatesDown-regulation of heat shock protein 27 in neuronal cells and non-neuronal cells expressing mutant ataxin-3HnRNP A1 and A/B interaction with PABPN1 in oculopharyngeal muscular dystrophyMammalian, yeast, bacterial, and chemical chaperones reduce aggregate formation and death in a cell model of oculopharyngeal muscular dystrophyProtein carbonylation, cellular dysfunction, and disease progressionAggresome formation and neurodegenerative diseases: therapeutic implicationsCell death in the nervous systemRuvbL1 and RuvbL2 enhance aggresome formation and disaggregate amyloid fibrils.Heat shock protein responses to aging and proteotoxicity in the olfactory bulb.Heat shock proteins in neurodegenerative disorders and agingNeuronal circuitry regulates the response of Caenorhabditis elegans to misfolded proteinsExpression of progerin in aging mouse brains reveals structural nuclear abnormalities without detectible significant alterations in gene expression, hippocampal stem cells or behavior.Distinct partitioning of ALS associated TDP-43, FUS and SOD1 mutants into cellular inclusions
P2860
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P2860
Cellular defenses against unfolded proteins: a cell biologist thinks about neurodegenerative diseases.
description
2001 nî lūn-bûn
@nan
2001 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2001 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2001年の論文
@ja
2001年論文
@yue
2001年論文
@zh-hant
2001年論文
@zh-hk
2001年論文
@zh-mo
2001年論文
@zh-tw
2001年论文
@wuu
name
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@ast
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@en
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@nl
type
label
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@ast
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@en
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@nl
prefLabel
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@ast
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@en
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@nl
P1433
P1476
Cellular defenses against unfo ...... ut neurodegenerative diseases.
@en
P2093
Goldberg AL
Sherman MY
P356
10.1016/S0896-6273(01)00177-5
P407
P577
2001-01-01T00:00:00Z