about
The cell biology of disease: lysosomal storage disorders: the cellular impact of lysosomal dysfunctionIntracellular trafficking of ceramide by ceramide transfer proteinApoptosis and signalling in acid sphingomyelinase deficient cellsA fluorescent glycolipid-binding peptide probe traces cholesterol dependent microdomain-derived trafficking pathwaysMutagenesis of the putative sterol-sensing domain of yeast Niemann Pick C-related protein reveals a primordial role in subcellular sphingolipid distribution.Yeast cells lacking the ARV1 gene harbor defects in sphingolipid metabolism. Complementation by human ARV1.Generation of stable lipid raft microdomains in the enterocyte brush border by selective endocytic removal of non-raft membraneDynamic partitioning of a glycosyl-phosphatidylinositol-anchored protein in glycosphingolipid-rich microdomains imaged by single-quantum dot tracking.Traffic jam: a compendium of human diseases that affect intracellular transport processes.Metabolic cytometry: capillary electrophoresis with two-color fluorescence detection for the simultaneous study of two glycosphingolipid metabolic pathways in single primary neuronsNonesterified cholesterol content of lysosomes modulates susceptibility to oxidant-induced permeabilization.Sphingolipid trafficking and protein sorting in epithelial cells.Glycosphingolipid lysosomal storage diseases: therapy and pathogenesis.Early axonal loss accompanied by impaired endocytosis, abnormal axonal transport, and decreased microtubule stability occur in the model of Krabbe's disease.Neurobiology and cellular pathogenesis of glycolipid storage diseases.A historical perspective of the glycosphingolipids and sphingolipidoses.Structure-dependent pseudoreceptor intracellular traffic of adamantyl globotriaosyl ceramide mimicsLipid regulation of the synaptic vesicle cycle.Storage solutions: treating lysosomal disorders of the brain.New developments in treating glycosphingolipid storage diseases.Anomalous surface distribution of glycosyl phosphatidyl inositol-anchored proteins in neurons lacking acid sphingomyelinase.The mucopolysaccharidoses: a success of molecular medicine.Functional interactions between sphingolipids and sterols in biological membranes regulating cell physiologyCeramidase regulates synaptic vesicle exocytosis and traffickingSterols and sphingolipids: dynamic duo or partners in crime?Trafficking of Acetyl-C16-Ceramide-NBD with Long-Term Stability and No Cytotoxicity into the Golgi Complex.Rab proteins mediate Golgi transport of caveola-internalized glycosphingolipids and correct lipid trafficking in Niemann-Pick C cells.Polarized membrane traffic and cell polarity development is dependent on dihydroceramide synthase-regulated sphinganine turnoverEndocytosis of NBD-sphingolipids in neurons: exclusion from degradative compartments and transport to the Golgi complex.pH-dependent formation of membranous cytoplasmic body-like structure of ganglioside G(M1)/bis(monoacylglycero)phosphate mixed membranes.Enhanced delivery of α-glucosidase for Pompe disease by ICAM-1-targeted nanocarriers: comparative performance of a strategy for three distinct lysosomal storage disorders.The equilibria of sphingolipid-cholesterol and sphingolipid-sphingolipid in monolayers at the air-water interface.A soluble sulfogalactosyl ceramide mimic promotes Delta F508 CFTR escape from endoplasmic reticulum associated degradationInternalized Pseudomonas exotoxin A can exploit multiple pathways to reach the endoplasmic reticulum.Absence of metabolic cross-correction in Tay-Sachs cells: implications for gene therapy.Sterol-dependent regulation of sphingolipid metabolism in Saccharomyces cerevisiae.Glucosylceramide modulates membrane traffic along the endocytic pathway.Sphingolipid storage induces accumulation of intracellular cholesterol by stimulating SREBP-1 cleavage.Fluorescent analogues of plasma membrane sphingolipids are sorted to different intracellular compartments in astrocytes; Harmful effects of chronic ethanol exposure on sphingolipid trafficking and metabolism.
P2860
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P2860
description
2000 nî lūn-bûn
@nan
2000 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2000 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2000年の論文
@ja
2000年論文
@yue
2000年論文
@zh-hant
2000年論文
@zh-hk
2000年論文
@zh-mo
2000年論文
@zh-tw
2000年论文
@wuu
name
Membrane traffic in sphingolipid storage diseases.
@ast
Membrane traffic in sphingolipid storage diseases.
@en
Membrane traffic in sphingolipid storage diseases.
@nl
type
label
Membrane traffic in sphingolipid storage diseases.
@ast
Membrane traffic in sphingolipid storage diseases.
@en
Membrane traffic in sphingolipid storage diseases.
@nl
prefLabel
Membrane traffic in sphingolipid storage diseases.
@ast
Membrane traffic in sphingolipid storage diseases.
@en
Membrane traffic in sphingolipid storage diseases.
@nl
P2093
P2860
P1433
P1476
Membrane traffic in sphingolipid storage diseases.
@en
P2093
P2860
P304
P356
10.1034/J.1600-0854.2000.011101.X
P577
2000-11-01T00:00:00Z