DNAJC19, a mitochondrial cochaperone associated with cardiomyopathy, forms a complex with prohibitins to regulate cardiolipin remodeling. - Wikidata - awgldk - TriplyDB

DNAJC19, a mitochondrial cochaperone associated with cardiomyopathy, forms a complex with prohibitins to regulate cardiolipin remodeling.

DNAJC19, a mitochondrial cochaperone associated with cardiomyopathy, forms a complex with prohibitins to regulate cardiolipin remodeling.

http://www.wikidata.org/entity/Q34421187

about

C11orf83, a mitochondrial cardiolipin-binding protein involved in bc1 complex assembly and supercomplex stabilization Barth Syndrome: From Mitochondrial Dysfunctions Associated with Aberrant Production of Reactive Oxygen Species to Pluripotent Stem Cell Studies The Role of Cardiolipin in Cardiovascular Health Defining functional classes of Barth syndrome mutation in humans Disorders of phospholipid metabolism: an emerging class of mitochondrial disease due to defects in nuclear genes Mitochondrial dysfunction in cardiac aging Biosynthesis, remodeling and turnover of mitochondrial cardiolipin Cardiolipin remodeling: a regulatory hub for modulating cardiolipin metabolism and function CLPB variants associated with autosomal-recessive mitochondrial disorder with cataract, neutropenia, epilepsy, and methylglutaconic aciduria Loss of OMA1 delays neurodegeneration by preventing stress-induced OPA1 processing in mitochondria Mitochondrial Diseases Part II: Mouse models of OXPHOS deficiencies caused by defects in regulatory factors and other components required for mitochondrial function.Spectrum of combined respiratory chain defects.Acyl-CoA synthetase 1 deficiency alters cardiolipin species and impairs mitochondrial function.Human Mitochondrial DNA-Protein Complexes Attach to a Cholesterol-Rich Membrane Structure Tafazzins from Drosophila and mammalian cells assemble in large protein complexes with a short half-life.Loss of CLPP alleviates mitochondrial cardiomyopathy without affecting the mammalian UPRmt.Cardiolipin or MTCH2 can serve as tBID receptors during apoptosis Genetic anticipation in a special form of hypertrophic cardiomyopathy with sudden cardiac death in a family with 74 members across 5 generations.Role of membrane contact sites in protein import into mitochondria.Expression of a mutant prohibitin from the aP2 gene promoter leads to obesity-linked tumor development in insulin resistance-dependent manner.How lipids modulate mitochondrial protein import.Cardiolipin and mitochondrial cristae organization.The antioxidant protein Oxr1 influences aspects of mitochondrial morphology CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.Analysis of the effect of the mitochondrial prohibitin complex, a context-dependent modulator of longevity, on the C. elegans metabolome.Unraveling the functions of type II-prohibitins in Arabidopsis mitochondria.Previously Unreported Biallelic Mutation in DNAJC19: Are Sensorineural Hearing Loss and Basal Ganglia Lesions Additional Features of Dilated Cardiomyopathy and Ataxia (DCMA) Syndrome?Role of Cardiolipin in Mitochondrial Signaling Pathways Deficiency of PHB complex impairs respiratory supercomplex formation and activates mitochondrial flashes.The membrane scaffold SLP2 anchors a proteolytic hub in mitochondria containing PARL and the i-AAA protease YME1L.Barth syndrome cardiomyopathy.Biological Implications of Differential Expression of Mitochondrial-Shaping Proteins in Parkinson's Disease.Oculomotor apraxia and dilated cardiomyopathy with ataxia syndrome: A case report.Regulation of mitochondrial protein import by the nucleotide exchange factors GrpEL1 and GrpEL2 in human cells.Mitochondrial epileptic encephalopathy, 3-methylglutaconic aciduria and variable complex V deficiency associated with TIMM50 mutations.CLPP deficiency protects against metabolic syndrome but hinders adaptive thermogenesis.Quantitative Analysis of Glycerophospholipids in Mitochondria by Mass Spectrometry.Prohibitin is a positive modulator of mitochondrial function in PC12 cells under oxidative stress

P2860

Q24315727-87D9945D-D935-4B19-8D2D-5F736A3E6BC3 Q26772690-73F9D455-D021-4DD3-AEB7-FBF825DF47D3 Q26798052-DB5062A9-9165-4250-A8E9-0C205E876020 Q28386747-23B82066-C599-4A5C-9156-BA97BD6017B6 Q28387241-5179697E-F890-4C11-B4E5-F6426E8F25AD Q28389063-8466E24E-BEED-4594-AE23-3AA9AB1F9422 Q28395064-A0459D82-2546-43BE-959D-93CEE79E01A9 Q28395178-ED7556F1-FB37-4767-9005-C72E9EA33C79 Q34458614-B2EFA719-05AC-43A3-BD45-F0503A618A44 Q34509729-B201333E-7656-451E-86CE-5105E30DCCC6 Q35660977-51CA5B39-327C-49E8-9D9D-976684F2B1E1 Q35825509-60D49068-B640-4FA1-81C3-58DB442E4254 Q35886303-C2F5D25A-D1D3-48CA-92FE-97FBACABB024 Q36174547-03907A26-513F-450E-9CB1-1D28F63A0C1F Q36409360-FC354B48-CC0F-4C03-87D0-FD01B2B1C74A Q37061723-CA0C9258-1392-45AC-A76D-E64261B513E6 Q37098808-F5A4ABB8-D285-413C-AAC4-C3DB9499AE81 Q37725295-79833276-1AFF-48B4-9C67-188DC3A58CE0 Q38290676-C798935E-C0B8-4C3F-B9B9-6981413341B3 Q38294405-B767FFD5-839E-47BD-AEE9-AA224F3742B5 Q38359266-0442C210-938E-4C9B-855E-2050295DE92F Q38881323-4BB828F6-9FB6-42BA-9EC2-C675BFF9C38F Q38887200-6CDF3261-0478-403F-8602-9EE86170549C Q39232101-37D0CCCA-F396-4781-8A07-4A41BE851A21 Q40819032-E17ADB32-D890-4373-A1BC-EA468C4C434F Q41036551-AF3A3229-184E-4004-B8DE-ECBC0A552799 Q41619233-B8102F60-B66D-4A72-B7CE-7981F7FA810E Q42369764-B0611A46-EAC2-45B6-80D0-14AF082C7A87 Q42511264-85C325CA-B8A5-4A60-806C-55907DB2FF66 Q45161551-15ED51B8-2D5E-4EE9-BAF6-373565F11675 Q46423521-B9617670-1517-45F3-983F-32ECB9FF4FA8 Q47265377-DE91CAB5-80F0-4D42-97E7-47EB97198144 Q47625652-E042E268-B5B0-4FB9-8EF8-E322C4E9DAF8 Q47894100-70A6C780-7887-4044-96CA-C5AF05126DDA Q48090122-2F48BD98-7FA8-4A10-81C0-6198070B79F7 Q51758932-5CA0A688-0DE6-4F08-B962-3CCC85DC7E66 Q51836778-C0AF756C-A122-4917-B5C0-C40D62A352D5 Q56394741-77E381A9-B1EE-407D-9DCC-D459E9DDC6AA

P2860

DNAJC19, a mitochondrial cochaperone associated with cardiomyopathy, forms a complex with prohibitins to regulate cardiolipin remodeling.

http://www.wikidata.org/entity/Q34421187

description

2014 nî lūn-bûn

@nan

2014 թուականի Մայիսին հրատարակուած գիտական յօդուած

@hyw

2014 թվականի մայիսին հրատարակված գիտական հոդված

@hy

2014年の論文

@ja

2014年論文

@yue

2014年論文

@zh-hant

2014年論文

@zh-hk

2014年論文

@zh-mo

2014年論文

@zh-tw

2014年论文

@wuu

name

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@ast

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@en

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@nl

type

label

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@ast

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@en

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@nl

prefLabel

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@ast

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@en

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@nl

P1433

Q34421187-E1AAC586-1B7C-4FDA-B234-2D2F39335DBE

P1476

Q34421187-48FE8FB0-2902-4150-B430-C8344C44ED6A

P2093

Q34421187-2795B78A-D56E-4033-87A6-B514124DCC30

Q34421187-50CCD0AB-8D00-44AA-8659-181842BDF453

Q34421187-56B53AD1-FB2B-445D-9AA3-DEBA99692AA8

Q34421187-6BE069ED-3A79-4B1C-BF4D-3972B8E060DE

Q34421187-82B2FED5-2377-4D10-A9C8-C2B9484A5B69

Q34421187-C5EE5D57-21EF-472B-A01E-9AAC9009AFA5

Q34421187-D6BC7759-280D-4161-BD41-BA09A783F03C

Q34421187-D87392E7-F956-40D6-AB13-DCFF35C9A966

Q34421187-E752478E-FBDB-4F8C-BCC7-0777E51A917B

P304

Q34421187-57D4FA93-BFF3-4C1B-B474-1C9C57782A2C

P31

Q34421187-4A6CC248-5E2D-4C54-B3C2-E731731B93B7

P356

Q34421187-A8C1AA56-2C14-4B01-B7DD-208CC259213F

P433

Q34421187-483B740C-C181-419E-95EF-FB1F4513E701

P478

Q34421187-61DBF90F-F3A1-498E-B13F-A7ED97BFCACA

P50

Q34421187-D29FF8D3-8BA8-458D-966C-F66CFDAEDEC6

P577

Q34421187-C400118D-A0F5-4B7D-8A0C-7E17DFE70936

P5875

Q34421187-324A51C6-17B4-44B4-BC2C-C9A71D37F76C

P698

Q34421187-86C037BD-D507-45AD-8A9B-0C6887A8D5C0

P921

Q34421187-531E75B3-1FC3-42C4-A0EF-62239F936EB8

Q34421187-5EEABEF2-6DDF-4E6F-80D5-3ED3C6188148

Q34421187-91F265F2-8008-43DA-A7B0-C4B91840E2FF

Q34421187-D2100119-332B-4BF1-9F0A-E62D9907E734

Q34421187-F9F73E01-465A-4838-BA90-48033E0C7089

P356

J.CMET.2014.04.016

P1433

Cell Metabolism

P1476

DNAJC19, a mitochondrial cocha ...... gulate cardiolipin remodeling.

@en

P2093

Anne Korwitz

http://www.w3.org/2001/XMLSchema#string

Mathias Haag

http://www.w3.org/2001/XMLSchema#string

Michael Baker

http://www.w3.org/2001/XMLSchema#string

Ricarda Richter-Dennerlein

http://www.w3.org/2001/XMLSchema#string

Sascha Dargazanli

http://www.w3.org/2001/XMLSchema#string

Takashi Tatsuta

http://www.w3.org/2001/XMLSchema#string

Thomas Langer

http://www.w3.org/2001/XMLSchema#string

Thorsten Decker

http://www.w3.org/2001/XMLSchema#string

Tobias Lamkemeyer

http://www.w3.org/2001/XMLSchema#string

P304

158-171

http://www.w3.org/2001/XMLSchema#string

P31

scholarly article

P356

10.1016/J.CMET.2014.04.016

http://www.w3.org/2001/XMLSchema#string

P433

1

http://www.w3.org/2001/XMLSchema#string

P478

20

http://www.w3.org/2001/XMLSchema#string

P50

Elena I Rugarli

P577

2014-05-22T00:00:00Z

http://www.w3.org/2001/XMLSchema#dateTime

P5875

262610798

http://www.w3.org/2001/XMLSchema#string

P698

24856930

http://www.w3.org/2001/XMLSchema#string

P921

AFG3-like AAA ATPase 2

Presequence translocase-asssociated motor 16 homolog (S. cerevisiae)

DnaJ heat shock protein family (Hsp40) member C19