Comparison of a new pmp22 transgenic mouse line with other mouse models and human patients with CMT1A.
about
Molecular regulators of nerve conduction - Lessons from inherited neuropathies and rodent genetic modelsShortened internodal length of dermal myelinated nerve fibres in Charcot-Marie-Tooth disease type 1A.The PMP22 gene and its related diseases.Proximal nerve magnetization transfer MRI relates to disability in Charcot-Marie-Tooth diseasesGenome editing-enabled HTS assays expand drug target pathways for Charcot-Marie-tooth disease.Regulation of the PMP22 gene through an intronic enhancer.Pharmacological induction of the heat shock response improves myelination in a neuropathic modelDistal enhancers upstream of the Charcot-Marie-Tooth type 1A disease gene PMP22Identification of drug modulators targeting gene-dosage disease CMT1A.Induction of heat shock protein 70 (Hsp70) prevents neuregulin-induced demyelination by enhancing the proteasomal clearance of c-Jun.Role of immune cells in animal models for inherited peripheral neuropathies.Animal models of Charcot-Marie-Tooth disease type 1A.Conduction block in PMP22 deficiency.Molecular mechanisms of inherited demyelinating neuropathies.Murine therapeutic models for Charcot-Marie-Tooth (CMT) disease.Therapeutic options in Charcot-Marie-Tooth diseases.Caveats in the Established Understanding of CMT1A.c-Jun activation in Schwann cells protects against loss of sensory axons in inherited neuropathy.Graded Elevation of c-Jun in Schwann Cells In Vivo: Gene Dosage Determines Effects on Development, Remyelination, Tumorigenesis, and Hypomyelination.Sustained MAPK/ERK Activation in Adult Schwann Cells Impairs Nerve Repair.Schwann cell-specific deletion of the endosomal PI 3-kinase Vps34 leads to delayed radial sorting of axons, arrested myelination, and abnormal ErbB2-ErbB3 tyrosine kinase signaling.Identification of the variant Ala335Val of MED25 as responsible for CMT2B2: molecular data, functional studies of the SH3 recognition motif and correlation between wild-type MED25 and PMP22 RNA levels in CMT1A animal modelsIn Vivo Electrophysiological Measurement of Compound Muscle Action Potential from the Forelimbs in Mouse Models of Motor Neuron DegenerationMyelin and Axon Pathology in a Long-Term Study ofPMP22-Overexpressing Mice
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P2860
Comparison of a new pmp22 transgenic mouse line with other mouse models and human patients with CMT1A.
description
2002 nî lūn-bûn
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2002 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
2002 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
2002年の論文
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2002年論文
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2002年論文
@zh-hant
2002年論文
@zh-hk
2002年論文
@zh-mo
2002年論文
@zh-tw
2002年论文
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name
Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@ast
Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@en
Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@nl
type
label
Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@ast
Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@en
Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@nl
prefLabel
Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@ast
Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@en
Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@nl
P2093
P2860
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Comparison of a new pmp22 tran ...... and human patients with CMT1A.
@en
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A A Gabreëls-Festen
A M Robertson
A McGuigan
J R Muddle
P K Thomas
R H M King
P2860
P304
P356
10.1046/J.1469-7580.2002.00039.X
P577
2002-04-01T00:00:00Z