Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.

Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.

Item
http://www.wikidata.org/entity/Q35057660
The effect of chloroquine on the metabolism of [35S]cystine in normal and cystinotic human skin fibroblastsRole of thiols in degradation of proteins by cathepsinsTime course of pathogenic and adaptation mechanisms in cystinotic mouse kidneysInhibitors of protein synthesis also inhibit lysosomal proteolysis. Studies using cystinotic fibroblasts.Effects of oral phosphocysteamine and rectal cysteamine in cystinosis.Pancytopenia in a patient with cystinosis secondary to myelosuppression from cystine crystal deposition: a case reportA cysteine-specific lysosomal transport system provides a major route for the delivery of thiol to human fibroblast lysosomes: possible role in supporting lysosomal proteolysis.Cystine accumulation and loss in normal, heterozygous, and cystinotic fibroblasts.The renal Fanconi syndrome in cystinosis: pathogenic insights and therapeutic perspectives.Role of thiols, pH and cathepsin D in the lysosomal catabolism of serum albumin.Cystine accumulation in cystinotic fibroblasts from free and protein-linked cystine but not cysteine.Disulphide reduction in lysosomes. The role of cysteine.Cysteine Metabolism in Neuronal Redox Homeostasis.
P2860

Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.

Item
http://www.wikidata.org/entity/Q35057660
description
1977 nî lūn-bûn
@nan
1977 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած
@hyw
1977 թվականի հոտեմբերին հրատարակված գիտական հոդված
@hy
1977年の論文
@ja
1977年論文
@yue
1977年論文
@zh-hant
1977年論文
@zh-hk
1977年論文
@zh-mo
1977年論文
@zh-tw
1977年论文
@wuu
name
Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.
@ast
Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.
@en
type
label
Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.
@ast
Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.
@en
prefLabel
Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.
@ast
Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.
@en
P1433
P1476
P2093
P2860
P304
P31
P356
P407
P433
P478
P577
P5875
P698
P932
P356
P1433
P1476
Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.
@en
P2093
P2860
P304
P31
P356
P407
P433
P478
P577
P5875
P698
P932