Altered sensitivity of cerebellar granule cells to glutamate receptor overactivation in the Cln3(Δex7/8)-knock-in mouse model of juvenile neuronal ceroid lipofuscinosis.
about
Diseases associated with leaky hemichannelsAbnormally increased surface expression of AMPA receptors in the cerebellum, cortex and striatum of Cln3(-/-) miceLarge-scale phenotyping of an accurate genetic mouse model of JNCL identifies novel early pathology outside the central nervous systemHemichannels in neurodegenerative diseases: is there a link to pathology?The juvenile Batten disease protein, CLN3, and its role in regulating anterograde and retrograde post-Golgi trafficking.Evidence for aberrant astrocyte hemichannel activity in Juvenile Neuronal Ceroid Lipofuscinosis (JNCL).Finding the most appropriate mouse model of juvenile CLN3 (Batten) disease for therapeutic studies: the importance of genetic background and gender.Neuroinflammatory paradigms in lysosomal storage diseases.Photoreceptor phagosome processing defects and disturbed autophagy in retinal pigment epithelium of Cln3Δex1-6 mice modelling juvenile neuronal ceroid lipofuscinosis (Batten disease).Efficacy of phosphodiesterase-4 inhibitors in juvenile Batten disease (CLN3).Detailed Clinical Phenotype and Molecular Genetic Findings in CLN3-Associated Isolated Retinal Degeneration.Glial cells are functionally impaired in juvenile neuronal ceroid lipofuscinosis and detrimental to neurons.Defective synaptic transmission causes disease signs in a mouse model of juvenile neuronal ceroid lipofuscinosis.Microglia in juvenile neuronal ceroid lipofuscinosis are primed toward a pro-inflammatory phenotype.Revisiting the neuronal localization and trafficking of CLN3 in juvenile neuronal ceroid lipofuscinosis.Decreased sensitivity of palmitoyl protein thioesterase 1-deficient neurons to chemical anoxia.Altered Cerebellar Short-Term Plasticity but No Change in Postsynaptic AMPA-Type Glutamate Receptors in a Mouse Model of Juvenile Batten Disease.
P2860
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P2860
Altered sensitivity of cerebellar granule cells to glutamate receptor overactivation in the Cln3(Δex7/8)-knock-in mouse model of juvenile neuronal ceroid lipofuscinosis.
description
2011 nî lūn-bûn
@nan
2011 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Altered sensitivity of cerebel ...... euronal ceroid lipofuscinosis.
@ast
Altered sensitivity of cerebel ...... euronal ceroid lipofuscinosis.
@en
type
label
Altered sensitivity of cerebel ...... euronal ceroid lipofuscinosis.
@ast
Altered sensitivity of cerebel ...... euronal ceroid lipofuscinosis.
@en
prefLabel
Altered sensitivity of cerebel ...... euronal ceroid lipofuscinosis.
@ast
Altered sensitivity of cerebel ...... euronal ceroid lipofuscinosis.
@en
P2093
P2860
P1476
Altered sensitivity of cerebel ...... euronal ceroid lipofuscinosis.
@en
P2093
Attila D Kovács
David A Pearce
Rozzy Finn
P2860
P304
P356
10.1016/J.NEUINT.2011.02.003
P577
2011-02-17T00:00:00Z