Defective peroxisomal catabolism of branched fatty acyl coenzyme A in mice lacking the sterol carrier protein-2/sterol carrier protein-x gene function.
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Anaerobic toluene catabolism of Thauera aromatica: the bbs operon codes for enzymes of beta oxidation of the intermediate benzylsuccinateMetabolic Interplay between Peroxisomes and Other Subcellular Organelles Including Mitochondria and the Endoplasmic ReticulumPeroxisomes in brain development and functionRecognition of a Functional Peroxisome Type 1 Target by the Dynamic Import Receptor Pex5pThe structural determination of an insect sterol carrier protein-2 with a ligand-bound C16 fatty acid at 1.35-A resolutionThe crystal structure of sterol carrier protein 2 from Yarrowia lipolytica and the evolutionary conservation of a large, non-specific lipid-binding cavityStructure of human phytanoyl-CoA 2-hydroxylase identifies molecular mechanisms of Refsum diseaseA phytol-enriched diet induces changes in fatty acid metabolism in mice both via PPARalpha-dependent and -independent pathwaysLocalization of a portion of the liver isoform of fatty-acid-binding protein (L-FABP) to peroxisomesPrenatal and postnatal development of peroxisomal lipid-metabolizing pathways in the mouseAbsence of spontaneous peroxisome proliferation in enoyl-CoA Hydratase/L-3-hydroxyacyl-CoA dehydrogenase-deficient mouse liver. Further support for the role of fatty acyl CoA oxidase in PPARalpha ligand metabolismThe murine and human cholesterol 7alpha-hydroxylase gene promoters are differentially responsive to regulation by fatty acids mediated via peroxisome proliferator-activated receptor alphaConformational plasticity of the lipid transfer protein SCP2Loss of liver FA binding protein significantly alters hepatocyte plasma membrane microdomainsMutations in the gene encoding peroxisomal sterol carrier protein X (SCPx) cause leukencephalopathy with dystonia and motor neuropathy.The sterol carrier protein 2/3-oxoacyl-CoA thiolase (SCPx) is involved in cholesterol uptake in the midgut of Spodoptera litura: gene cloning, expression, localization and functional analyses.Probing lipid- and drug-binding domains with fluorescent dyes.Sterol carrier protein-2 localization in endoplasmic reticulum and role in phospholipid formation.FRET microscopy demonstrates molecular association of non-specific lipid transfer protein (nsL-TP) with fatty acid oxidation enzymes in peroxisomes.Phytol-induced hepatotoxicity in mice.Hepatic phenotype of liver fatty acid binding protein gene-ablated micePPARalpha: energy combustion, hypolipidemia, inflammation and cancerDifferences in the structure and dynamics of the apo- and palmitate-ligated forms of Aedes aegypti sterol carrier protein 2 (AeSCP-2).Effect of sterol carrier protein-2 gene ablation on HDL-mediated cholesterol efflux from cultured primary mouse hepatocytes.Effects of mutations in Aedes aegypti sterol carrier protein-2 on the biological function of the protein.Biochemistry and genetics of inherited disorders of peroxisomal fatty acid metabolismLiver fatty acid-binding protein and obesity.Glucose regulates fatty acid binding protein interaction with lipids and peroxisome proliferator-activated receptor α.Early steps in steroidogenesis: intracellular cholesterol trafficking.Overexpression of peroxisome proliferator-activated receptor-alpha (PPARalpha)-regulated genes in liver in the absence of peroxisome proliferation in mice deficient in both L- and D-forms of enoyl-CoA hydratase/dehydrogenase enzymes of peroxisomal bAcyl-CoA binding protein gene ablation induces pre-implantation embryonic lethality in mice.Nonalcoholic steatosis and steatohepatitis. III. Peroxisomal beta-oxidation, PPAR alpha, and steatohepatitis.Refsum disease, peroxisomes and phytanic acid oxidation: a review.Liver fatty acid binding protein gene ablation potentiates hepatic cholesterol accumulation in cholesterol-fed female mice.Regulation of bile acid biosynthesis by hepatocyte nuclear factor 4alpha.Ablating L-FABP in SCP-2/SCP-x null mice impairs bile acid metabolism and biliary HDL-cholesterol secretion.Acyl-CoA binding proteins interact with the acyl-CoA binding domain of mitochondrial carnitine palmitoyl transferase I.Minireview: translocator protein (TSPO) and steroidogenesis: a reappraisal.The mutant Moonwalker TRPC3 channel links calcium signaling to lipid metabolism in the developing cerebellum.Loss of L-FABP, SCP-2/SCP-x, or both induces hepatic lipid accumulation in female mice
P2860
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P2860
Defective peroxisomal catabolism of branched fatty acyl coenzyme A in mice lacking the sterol carrier protein-2/sterol carrier protein-x gene function.
description
1998 nî lūn-bûn
@nan
1998 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
1998 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
1998年の論文
@ja
1998年論文
@yue
1998年論文
@zh-hant
1998年論文
@zh-hk
1998年論文
@zh-mo
1998年論文
@zh-tw
1998年论文
@wuu
name
Defective peroxisomal cataboli ...... rrier protein-x gene function.
@ast
Defective peroxisomal cataboli ...... rrier protein-x gene function.
@en
type
label
Defective peroxisomal cataboli ...... rrier protein-x gene function.
@ast
Defective peroxisomal cataboli ...... rrier protein-x gene function.
@en
prefLabel
Defective peroxisomal cataboli ...... rrier protein-x gene function.
@ast
Defective peroxisomal cataboli ...... rrier protein-x gene function.
@en
P2093
P2860
P356
P1433
P1476
Defective peroxisomal cataboli ...... rrier protein-x gene function.
@en
P2093
F Kannenberg
P Ellinghaus
R J Wanders
P2860
P304
P356
10.1101/GAD.12.8.1189
P577
1998-04-01T00:00:00Z