about
Identification of LACTB2, a metallo-β-lactamase protein, as a human mitochondrial endoribonucleaseTRMT5 Mutations Cause a Defect in Post-transcriptional Modification of Mitochondrial tRNA Associated with Multiple Respiratory-Chain DeficienciesDeficient methylation and formylation of mt-tRNA(Met) wobble cytosine in a patient carrying mutations in NSUN3Deep sequencing of Danish Holstein dairy cattle for variant detection and insight into potential loss-of-function variants in protein coding genesTwo RNAs or DNAs May Artificially Fuse Together at a Short Homologous Sequence (SHS) during Reverse Transcription or Polymerase Chain Reactions, and Thus Reporting an SHS-Containing Chimeric RNA Requires Extra Caution.The Pseudouridine Synthase RPUSD4 Is an Essential Component of Mitochondrial RNA GranulesMaturation of selected human mitochondrial tRNAs requires deadenylation.Mitochondrial Mutations in Cardiac Disorders.Mouse models for mitochondrial diseases.Human mitochondrial nucleases.Dealing with an Unconventional Genetic Code in Mitochondria: The Biogenesis and Pathogenic Defects of the 5-Formylcytosine Modification in Mitochondrial tRNAMet.Regulation of Mammalian Mitochondrial Gene Expression: Recent Advances.Mitochondrial tRNA mutation with high-salt stimulation on cardiac damage: underlying mechanism associated with change of Bax and VDAC.rRNA processing in the mitochondrionrRNA modification in the mitochondriontRNA processingtRNA processing in the mitochondrionBiallelic C1QBP Mutations Cause Severe Neonatal-, Childhood-, or Later-Onset Cardiomyopathy Associated with Combined Respiratory-Chain Deficiencies.New insights into the phenotype of FARS2 deficiency.Defects in the mitochondrial-tRNA modification enzymes MTO1 and GTPBP3 promote different metabolic reprogramming through a HIF-PPARγ-UCP2-AMPK axis.Defective mitochondrial rRNA methyltransferase MRM2 causes MELAS-like clinical syndrome.Mitochondrial RNase P (mtRNase P) cleaves the 5' ends of pre-tRNAs and ELAC2 (RNase Z) cleaves the 3' ends of pre-tRNAs in the H strand transcriptMitochondrial RNase P (mtRNase P) cleaves the 5' ends of pre-tRNAs and ELAC2 (RNase Z) cleaves the 3' ends of pre-tRNAs in the L strand transcriptDedicated surveillance mechanism controls G-quadruplex forming non-coding RNAs in human mitochondria.RNA modification landscape of the human mitochondrial tRNA regulates protein synthesis
P2860
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P2860
description
2015 nî lūn-bûn
@nan
2015年の論文
@ja
2015年論文
@yue
2015年論文
@zh-hant
2015年論文
@zh-hk
2015年論文
@zh-mo
2015年論文
@zh-tw
2015年论文
@wuu
2015年论文
@zh
2015年论文
@zh-cn
name
Mitochondrial transcript maturation and its disorders
@ast
Mitochondrial transcript maturation and its disorders
@en
type
label
Mitochondrial transcript maturation and its disorders
@ast
Mitochondrial transcript maturation and its disorders
@en
prefLabel
Mitochondrial transcript maturation and its disorders
@ast
Mitochondrial transcript maturation and its disorders
@en
P2093
P2860
P50
P1476
Mitochondrial transcript maturation and its disorders
@en
P2093
Aaron R D'Souza
Lindsey Van Haute
Sarah F Pearce
P2860
P2888
P304
P356
10.1007/S10545-015-9859-Z
P5008
P577
2015-05-28T00:00:00Z
2015-07-01T00:00:00Z