The CCN family member Wisp3, mutant in progressive pseudorheumatoid dysplasia, modulates BMP and Wnt signaling
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WISP-1/CCN4 regulates osteogenesis by enhancing BMP-2 activityFunctions and mechanisms of action of CCN matricellular proteinsNormal growth and development in mice over-expressing the CCN family member WISP3Matricellular proteins of the Cyr61/CTGF/NOV (CCN) family and the nervous systemTaking aim at the extracellular matrix: CCN proteins as emerging therapeutic targetsNovel and recurrent mutations of WISP3 in two Chinese families with progressive pseudorheumatoid dysplasiaO-fucosylation of thrombospondin type 1 repeats restricts epithelial to mesenchymal transition (EMT) and maintains epiblast pluripotency during mouse gastrulationA Wisp3 Cre-knockin allele produces efficient recombination in spermatocytes during early prophase of meiosis I.Chondrocyte-specific microRNA-140 regulates endochondral bone development and targets Dnpep to modulate bone morphogenetic protein signaling.Temporal and spatial expression of CCN genes in zebrafish.Dual regulation of metalloproteinase expression in chondrocytes by Wnt-1-inducible signaling pathway protein 3/CCN6.CCN6 modulates BMP signaling via the Smad-independent TAK1/p38 pathway, acting to suppress metastasis of breast cancer.Whole Exome Screening Identifies Novel and Recurrent WISP3 Mutations Causing Progressive Pseudorheumatoid Dysplasia in Jammu and Kashmir-India.Clec11a/osteolectin is an osteogenic growth factor that promotes the maintenance of the adult skeleton.Disorders of the growth plate.The diagnostic challenge of progressive pseudorheumatoid dysplasia (PPRD): a review of clinical features, radiographic features, and WISP3 mutations in 63 affected individuals.A homozygous deletion of exon 1 in WISP3 causes progressive pseudorheumatoid dysplasia in two siblings.Signaling pathways regulating cartilage growth plate formation and activity.Matrilysin (MMP-7) catalytic activity regulates β-catenin localization and signaling activation in lung epithelial cells.Identification and functional analysis of Zranb2 as a novel Smad-binding protein that suppresses BMP signaling.The matricellular protein CCN6 (WISP3) decreases Notch1 and suppresses breast cancer initiating cells.A homozygous recurring mutation in WISP3 causing progressive pseudorheumatoid arthropathy.Temporal and spatial expression patterns of bone morphogenetic protein 3 in developing zebrafish.SAP30L (Sin3A-associated protein 30-like) is involved in regulation of cardiac development and hematopoiesis in zebrafish embryos.Genes uniquely expressed in human growth plate chondrocytes uncover a distinct regulatory network.WISP3 mutation associated with Pseudorheumatoid Dysplasia.Structural analyses of von Willebrand factor C domains of collagen 2A and CCN3 reveal an alternative mode of binding to bone morphogenetic protein-2.Transgenic Expression of A Venous Malformation Related Mutation, TIE2-R849W, Significantly Induces Multiple Malformations of Zebrafish.Temporal and spatial expression of CCN3 during retina development.Novel and recurrent mutations in WISP3 and an atypical phenotype.
P2860
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P2860
The CCN family member Wisp3, mutant in progressive pseudorheumatoid dysplasia, modulates BMP and Wnt signaling
description
2007 nî lūn-bûn
@nan
2007年の論文
@ja
2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
2007年论文
@zh
2007年论文
@zh-cn
name
The CCN family member Wisp3, m ...... odulates BMP and Wnt signaling
@ast
The CCN family member Wisp3, m ...... odulates BMP and Wnt signaling
@en
type
label
The CCN family member Wisp3, m ...... odulates BMP and Wnt signaling
@ast
The CCN family member Wisp3, m ...... odulates BMP and Wnt signaling
@en
prefLabel
The CCN family member Wisp3, m ...... odulates BMP and Wnt signaling
@ast
The CCN family member Wisp3, m ...... odulates BMP and Wnt signaling
@en
P2093
P2860
P356
P1476
The CCN family member Wisp3, m ...... odulates BMP and Wnt signaling
@en
P2093
Allisan Aquilina-Beck
Gilbert Weidinger
Jennifer O Liang
Keiko Tamai
Matthew L Warman
Randall T Moon
Yukio Nakamura
P2860
P304
P356
10.1172/JCI32001
P407
P577
2007-10-01T00:00:00Z