4-Phenylbutyric acid treatment rescues trafficking and processing of a mutant surfactant protein-C.
about
Interstitial lung disease in childrenA non-BRICHOS SFTPC mutant (SP-CI73T) linked to interstitial lung disease promotes a late block in macroautophagy disrupting cellular proteostasis and mitophagyLost after translation: insights from pulmonary surfactant for understanding the role of alveolar epithelial dysfunction and cellular quality control in fibrotic lung disease.The unfolded protein response controls ER stress-induced apoptosis of lung epithelial cells through angiotensin generation.The genetic basis of idiopathic pulmonary fibrosisFolding and Intramembraneous BRICHOS Binding of the Prosurfactant Protein C Transmembrane SegmentSFTPC mutations cause SP-C degradation and aggregate formation without increasing ER stress.Idiopathic Pulmonary Fibrosis: Molecular Endotypes of Fibrosis Stratifying Existing and Emerging Therapies.A novel surfactant protein C mutation resulting in aberrant protein processing and altered subcellular localization causes infantile interstitial lung disease.
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P2860
4-Phenylbutyric acid treatment rescues trafficking and processing of a mutant surfactant protein-C.
description
2012 nî lūn-bûn
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2012年の論文
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2012年学术文章
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2012年学术文章
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2012年学术文章
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2012年学术文章
@zh-my
2012年学术文章
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2012年學術文章
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name
4-Phenylbutyric acid treatment ...... a mutant surfactant protein-C.
@ast
4-Phenylbutyric acid treatment ...... a mutant surfactant protein-C.
@en
type
label
4-Phenylbutyric acid treatment ...... a mutant surfactant protein-C.
@ast
4-Phenylbutyric acid treatment ...... a mutant surfactant protein-C.
@en
prefLabel
4-Phenylbutyric acid treatment ...... a mutant surfactant protein-C.
@ast
4-Phenylbutyric acid treatment ...... a mutant surfactant protein-C.
@en
P2093
P2860
P356
P1476
4-Phenylbutyric acid treatment ...... a mutant surfactant protein-C.
@en
P2093
Cheng-Lun Na
Emily P Martin
Gareth A Stewart
Karunyakanth Mandapaka
Ross Ridsdale
Timothy E Weaver
P2860
P304
P356
10.1165/RCMB.2012-0003OC
P577
2012-03-29T00:00:00Z